541-15-1 | (3R)-3-hydroxy-4-(trimethylazaniumyl)butanoate

Packsize	Purity	Availability	Price	Discounted Price
1g	97%	in stock	$15.00	$10.00
5g	97%	in stock	$16.00	$11.00
25g	97%	in stock	$30.00	$21.00
100g	97%	in stock	$90.00	$63.00
500g	97%	in stock	$251.00	$176.00

Description

• Catalog Number: AI52126
• Chemical Name: (3R)-3-hydroxy-4-(trimethylazaniumyl)butanoate
• CAS Number: 541-15-1
• Molecular Formula: C7H15NO3
• Molecular Weight: 161.19890000000004
• MDL Number: MFCD00038747
• SMILES: OC(C[N+](C)(C)C)CC(=O)[O-]

Computed Properties

• Complexity: 134
• Covalently-Bonded Unit Count: 1
• Defined Atom Stereocenter Count: 1
• Heavy Atom Count: 11
• Hydrogen Bond Acceptor Count: 3
• Hydrogen Bond Donor Count: 1
• Rotatable Bond Count: 3
• XLogP3: -0.2

Literature

• The roles of bone morphogenetic protein 2 in perfluorooctanoic acid induced developmental cardiotoxicity and l-carnitine mediated protection.

  Toxicology and applied pharmacology 20180801

• Insights into myalgic encephalomyelitis/chronic fatigue syndrome phenotypes through comprehensive metabolomics.

  Scientific reports 20180101

• From the Cover: l-Carnitine via PPARγ- and Sirt1-Dependent Mechanisms Attenuates Epithelial-Mesenchymal Transition and Renal Fibrosis Caused by Perfluorooctanesulfonate.

  Toxicological sciences : an official journal of the Society of Toxicology 20171201

• L-Carnitine Attenuates Cardiac Dysfunction by Ischemic Insults Through Akt Signaling Pathway.

  Toxicological sciences : an official journal of the Society of Toxicology 20171201

• Experimental evidence of oxidative stress in patients with l-2-hydroxyglutaric aciduria and that l-carnitine attenuates in vitro DNA damage caused by d-2-hydroxyglutaric and l-2-hydroxyglutaric acids.

  Toxicology in vitro : an international journal published in association with BIBRA 20170801

• [ACTION OF L-CARNITINE, CORVITIN AND THEIR COMBINATION ON FUNCTIONAL STATE OF LIVER IN EXPERIMENTAL MODEL OF REYE SYNDROME IN RATS].

  Georgian medical news 20170201

• Plasma 2-hydroxyglutarate and hexanoylcarnitine levels are potential biomarkers for skeletal muscle toxicity in male Fischer 344 rats.

  The Journal of toxicological sciences 20170101

• Regression of fibrosis/cirrhosis by Glycine propionyl-l-carnitine treatment in d-Galactosamine induced chronic liver damage.

  Chemico-biological interactions 20161225

• Inflammatory and fibrotic processes are involved in the cardiotoxic effect of sunitinib: Protective role of L-carnitine.

  Toxicology letters 20160122

• A small molecule inhibitor of mutant IDH2 rescues cardiomyopathy in a D-2-hydroxyglutaric aciduria type II mouse model.

  Journal of inherited metabolic disease 20160101

• Triptolide disrupts fatty acids and peroxisome proliferator-activated receptor (PPAR) levels in male mice testes followed by testicular injury: A GC-MS based metabolomics study.

  Toxicology 20151002

• Metabolomic analysis of biochemical changes in the plasma and urine of collagen-induced arthritis in rats after treatment with Huang-Lian-Jie-Du-Tang.

  Journal of ethnopharmacology 20140528

• Glycine propionyl l-carnitine attenuates d-Galactosamine induced fulminant hepatic failure in wistar rats.

  Chemico-biological interactions 20140505

• Inhibition of mitochondrial carnitine/acylcarnitine transporter by H(2)O(2): molecular mechanism and possible implication in pathophysiology.

  Chemico-biological interactions 20130425

• Role of organic cation/carnitine transporter 1 in uptake of phenformin and inhibitory effect on complex I respiration in mitochondria.

  Toxicological sciences : an official journal of the Society of Toxicology 20130301

• Nutritional pork meat compounds as affected by ham dry-curing.

  Meat science 20130101

• Changes in mitochondrial carriers exhibit stress-specific signatures in INS-1Eβ-cells exposed to glucose versus fatty acids.

  PloS one 20130101

• Extraction and analysis of carnitine and acylcarnitines by electrospray ionization tandem mass spectrometry directly from dried blood and plasma spots using a novel autosampler.

  Rapid communications in mass spectrometry : RCM 20121115

• Decreased serum carnitine is independently correlated with increased tissue accumulation levels of advanced glycation end products in haemodialysis patients.

  Nephrology (Carlton, Vic.) 20121101

• Signal peptide-CUB-EGF domain-containing protein 1 (SCUBE1) level in hemodialysis patients and parameters affecting that level.

  Clinical biochemistry 20121101

• The carnitine biosynthetic pathway in Arabidopsis thaliana shares similar features with the pathway of mammals and fungi.

  Plant physiology and biochemistry : PPB 20121101

• L-carnitine supplementation for the management of fatigue in patients with cancer: an eastern cooperative oncology group phase III, randomized, double-blind, placebo-controlled trial.

  Journal of clinical oncology : official journal of the American Society of Clinical Oncology 20121101

• The mdx mouse as a model for carnitine deficiency in the pathogenesis of Duchenne muscular dystrophy.

  Muscle & nerve 20121101

• Perioperative perturbations in carnitine metabolism are attenuated by preoperative carbohydrate treatment: Another mechanism by which preoperative feeding may attenuate development of postoperative insulin resistance.

  Clinical nutrition (Edinburgh, Scotland) 20121001

• Functional redundancy of mitochondrial enoyl-CoA isomerases in the oxidation of unsaturated fatty acids.

  FASEB journal : official publication of the Federation of American Societies for Experimental Biology 20121001

• Cannabinoid receptor antagonist-induced striated muscle toxicity and ethylmalonic-adipic aciduria in beagle dogs.

  Toxicological sciences : an official journal of the Society of Toxicology 20121001

• Propionyl-L-carnitine improves endothelial function, microcirculation and pain management in critical limb ischemia.

  Cardiovascular drugs and therapy 20121001

• Determination of trimethylamine in spinach, cabbage, and lettuce at alkaline pH by headspace solid-phase microextraction.

  Journal of food science 20121001

• Feasibility of electroextraction as versatile sample preconcentration for fast and sensitive analysis of urine metabolites, demonstrated on acylcarnitines.

  Electrophoresis 20121001

• Antioxidant and oligonutrient status, distribution of amino acids, muscle damage, inflammation, and evaluation of renal function in elite rugby players.

  Clinical chemistry and laboratory medicine 20121001

• Propionyl-L-carnitine hydrochloride for treatment of mild to moderate colonic inflammatory bowel diseases.

  World journal of gastroenterology 20120928

• Modulatory effects of vitamin E, acetyl-L-carnitine and α-lipoic acid on new potential biomarkers for Alzheimer's disease in rat model.

  Experimental and toxicologic pathology : official journal of the Gesellschaft fur Toxikologische Pathologie 20120901

• Methylmalonic acidemia mimicking diabetic ketoacidosis in an infant.

  Pediatric diabetes 20120901

• Dietary supplementation of herring roe and milt enhances hepatic fatty acid catabolism in female mice transgenic for hTNFα.

  European journal of nutrition 20120901

• Postmortem tandem mass spectrometry profiling for detection of infection in unexpected infant death.

  Forensic science, medicine, and pathology 20120901

• Metabolic decompensation in methylmalonic aciduria: which biochemical parameters are discriminative?

  Journal of inherited metabolic disease 20120901

• Analysis of serum metabolic profiles in women with endometrial cancer and controls in a population-based case-control study.

  The Journal of clinical endocrinology and metabolism 20120901

• Rapid and weight-independent improvement of glucose tolerance induced by a peptide designed to elicit apoptosis in adipose tissue endothelium.

  Diabetes 20120901

• L-Carnitine prevents the development of ventricular fibrosis and heart failure with preserved ejection fraction in hypertensive heart disease.

  Journal of hypertension 20120901

• Carnitine and acylcarnitines: pharmacokinetic, pharmacological and clinical aspects.

  Clinical pharmacokinetics 20120901

• Bezafibrate can be a new treatment option for mitochondrial fatty acid oxidation disorders: evaluation by in vitro probe acylcarnitine assay.

  Molecular genetics and metabolism 20120901

• Promoting lipid utilization with l-carnitine to improve oocyte quality.

  Animal reproduction science 20120901

• [Evaluation of serum total carnitine values in persons with severe motor and intellectual disabilities with enteral (tube) feeding].

  No to hattatsu = Brain and development 20120901

• Cardiac-specific deletion of acetyl CoA carboxylase 2 prevents metabolic remodeling during pressure-overload hypertrophy.

  Circulation research 20120831

• [Effects of carnitine on respiratory chain and metabolism of oxygen radical in mitochondria of liver after exhaustive running in training rat].

  Sheng li xue bao : [Acta physiologica Sinica] 20120825

• Genetic ablation of calcium-independent phospholipase A(2)γ (iPLA(2)γ) attenuates calcium-induced opening of the mitochondrial permeability transition pore and resultant cytochrome c release.

  The Journal of biological chemistry 20120824

• Thirty-year follow-up of carnitine supplementation in two siblings with hypertrophic cardiomyopathy caused by primary systemic carnitine deficiency.

  International journal of cardiology 20120809

• Carnitine supplementation improves cardiac strain rate in children on chronic hemodialysis.

  Pediatric nephrology (Berlin, Germany) 20120801

• Serum metabolite concentrations and decreased GFR in the general population.

  American journal of kidney diseases : the official journal of the National Kidney Foundation 20120801

• Disruption of redox homeostasis in cerebral cortex of developing rats by acylcarnitines accumulating in medium-chain acyl-CoA dehydrogenase deficiency.

  International journal of developmental neuroscience : the official journal of the International Society for Developmental Neuroscience 20120801

• Changing metabolic signatures of amino acids and lipids during the prediabetic period in a pig model with impaired incretin function and reduced β-cell mass.

  Diabetes 20120801

• Coenzyme depletion by members of the aerolysin family of pore-forming toxins leads to diminished ATP levels and cell death.

  Molecular bioSystems 20120801

• A.S.P.E.N. position paper: recommendations for changes in commercially available parenteral multivitamin and multi-trace element products.

  Nutrition in clinical practice : official publication of the American Society for Parenteral and Enteral Nutrition 20120801

• Effect of short- and long-term treatment with valproate on carnitine homeostasis in humans.

  Therapeutic drug monitoring 20120801

• Malonyl coenzyme A decarboxylase deficiency: early dietary restriction and time course of cardiomyopathy.

  Pediatrics 20120801

• Effect of lysine, vitamin B(6), and carnitine supplementation on the lipid profile of male patients with hypertriglyceridemia: a 12-week, open-label, randomized, placebo-controlled trial.

  Clinical therapeutics 20120801

• The first Korean case of lysinuric protein intolerance: presented with short stature and increased somnolence.

  Journal of Korean medical science 20120801

• L-carnitine treatment during oocyte maturation improves in vitro development of cloned pig embryos by influencing intracellular glutathione synthesis and embryonic gene expression.

  Theriogenology 20120715

• Decreased expression of adipose CD36 and FATP1 are associated with increased plasma non-esterified fatty acids during prolonged fasting in northern elephant seal pups (Mirounga angustirostris).

  The Journal of experimental biology 20120715

• Thyroid hormone stimulates hepatic lipid catabolism via activation of autophagy.

  The Journal of clinical investigation 20120702

• Changes in the expression of HSL and OCTN2 in the female reproductive tract of the bat, Scotophilus heathii in relation to sperm storage.

  Acta histochemica 20120701

• Characterization of D-3-hydroxybutyrylcarnitine (ketocarnitine): an identified ketosis-induced metabolite.

  Metabolism: clinical and experimental 20120701

• SLC22A5/OCTN2 expression in breast cancer is induced by estrogen via a novel intronic estrogen-response element (ERE).

  Breast cancer research and treatment 20120701

• The metabolic effects of two different lipid emulsions used in parenterally fed premature infants--a randomized comparative study.

  Early human development 20120701

• Fatty emaciation: a case report of suspected fat overload syndrome in oral refeeding.

  JPEN. Journal of parenteral and enteral nutrition 20120701

• L carnitine in hemodialysis patients.

  Hemodialysis international. International Symposium on Home Hemodialysis 20120701

• Evaluation of asymmetric dimethylarginine, arginine, and carnitine metabolism in pediatric sepsis.

  Pediatric critical care medicine : a journal of the Society of Critical Care Medicine and the World Federation of Pediatric Intensive and Critical Care Societies 20120701

• Reduction in sperm aneuploidy levels in severe oligoasthenoteratospermic patients after medical therapy: a preliminary report.

  Asian journal of andrology 20120701

• L-carnitine and cancer cachexia. I. L-carnitine distribution and metabolic disorders in cancer cachexia.

  Oncology reports 20120701

• L-carnitine and cancer cachexia. II. Effects of lipid emulsion used in total parenteral nutrition on parameters of hemostasis and inflammatory state in L-carnitine deficiency in myocytes.

  Oncology reports 20120701

• Diagnosis of a patient with a kinetic variant of medium and short-chain 3-hydroxyacyl-CoA dehydrogenase deficiency by newborn screening.

  Molecular genetics and metabolism 20120701

• Carnitine, nutritional supplementation and discontinuation of ketogenic diet therapies.

  Epilepsy research 20120701

• Influence of dietary supplementation with (L)-carnitine on metabolic rate, fatty acid oxidation, body condition, and weight loss in overweight cats.

  American journal of veterinary research 20120701

• Intravenous lipid administration for drug-induced toxicity: a critical review of the existing data.

  Expert review of clinical pharmacology 20120701

• Urinary acylcarnitines are altered in human kidney cancer.

  International journal of cancer 20120615

• Analysis of multiple quaternary ammonium compounds in the brain using tandem capillary column separation and high resolution mass spectrometric detection.

  Journal of chromatography. A 20120608

• A musician's dystonia.

  Lancet (London, England) 20120602

• Carnitine supplementation effects on nonenzymatic antioxidants in young rats submitted to exhaustive exercise stress.

  Journal of strength and conditioning research 20120601

• Long-term correction of very long-chain acyl-coA dehydrogenase deficiency in mice using AAV9 gene therapy.

  Molecular therapy : the journal of the American Society of Gene Therapy 20120601

• Intrahepatic diacylglycerol content is associated with hepatic insulin resistance in obese subjects.

  Gastroenterology 20120601

• The dynamic range of the human metabolome revealed by challenges.

  FASEB journal : official publication of the Federation of American Societies for Experimental Biology 20120601

• Transport of the fluorescent organic cation 4-(4-(dimethylamino)styryl)-N-methylpyridinium iodide (ASP+) in human respiratory epithelial cells.

  European journal of pharmaceutics and biopharmaceutics : official journal of Arbeitsgemeinschaft fur Pharmazeutische Verfahrenstechnik e.V 20120601

• A carnitine-acylcarnitine carrier protein, MoCrc1, is essential for pathogenicity in Magnaporthe oryzae.

  Current genetics 20120601

• Analysis of acylcarnitine profiles in umbilical cord blood and during the early neonatal period by electrospray ionization tandem mass spectrometry.

  Brazilian journal of medical and biological research = Revista brasileira de pesquisas medicas e biologicas 20120601

• MCAD deficiency in Denmark.

  Molecular genetics and metabolism 20120601

• L-Carnitine plus cilostazol versus cilostazol alone for the treatment of claudication in patients with peripheral artery disease: a multicenter, randomized, double-blind, placebo-controlled trial.

  Vascular medicine (London, England) 20120601

• [Primary carnitine deficiency in 17 patients: diagnosis, treatment and follow up].

  Zhonghua er ke za zhi = Chinese journal of pediatrics 20120601

• [Abnormal findings during newborn period of 160 patients with early-onset methylmalonic aciduria].

  Zhonghua er ke za zhi = Chinese journal of pediatrics 20120601

• Over-expression in Escherichia coli, purification and reconstitution in liposomes of the third member of the OCTN sub-family: the mouse carnitine transporter OCTN3.

  Biochemical and biophysical research communications 20120525

• p-Sulfonated calix[6]arene modified graphene as a 'turn on' fluorescent probe for L-carnitine in living cells.

  Chemical communications (Cambridge, England) 20120518

• Muscle-specific deletion of carnitine acetyltransferase compromises glucose tolerance and metabolic flexibility.

  Cell metabolism 20120502

• L-Carnitine induces recovery of liver lipid metabolism in cancer cachexia.

  Amino acids 20120501

• Human sperm DNA oxidation, motility and viability in the presence of L-carnitine during in vitro incubation and centrifugation.

  Andrologia 20120501

• Propionyl-L-carnitine, L-arginine and niacin in sexual medicine: a nutraceutical approach to erectile dysfunction.

  Andrologia 20120501

• An improved LC-MS/MS method for the detection of classic and low excretor glutaric acidemia type 1.

  Journal of inherited metabolic disease 20120501

• Living-donor liver transplantation for propionic acidemia.

  Pediatric transplantation 20120501

• The mouse gene encoding the carnitine biosynthetic enzyme 4-N-trimethylaminobutyraldehyde dehydrogenase is regulated by peroxisome proliferator-activated receptor α.

  Biochimica et biophysica acta 20120501

• Utilization of endogenous fatty acid stores for energy production in bovine preimplantation embryos.

  Theriogenology 20120501

• Biochemical, molecular, and clinical characteristics of children with short chain acyl-CoA dehydrogenase deficiency detected by newborn screening in California.

  Molecular genetics and metabolism 20120501

• Oral carnitine supplementation for dyslipidemia in chronic hemodialysis patients.

  Saudi journal of kidney diseases and transplantation : an official publication of the Saudi Center for Organ Transplantation, Saudi Arabia 20120501

• High L-carnitine concentrations do not prevent late diabetic complications in type 1 and 2 diabetic patients.

  Nutrition research (New York, N.Y.) 20120501

• [Efficacy of natural vitamin E on oligospermia and asthenospermia: a prospective multi-centered randomized controlled study of 106 cases].

  Zhonghua nan ke xue = National journal of andrology 20120501

• Toward personalized hemodialysis by low molecular weight amino-containing compounds: future perspective of patient metabolic fingerprint.

  Blood transfusion = Trasfusione del sangue 20120501

• Comparing the effect between oral and injection form of carnitine on skin flap survival in rats.

  Journal of the Medical Association of Thailand = Chotmaihet thangphaet 20120501

• [Carnitine transporter deficiency is a hereditary disease with a high incidence in the Faroe Islands].

  Ugeskrift for laeger 20120430

• Serum metabolomic profiles from patients with acute kidney injury: a pilot study.

  Journal of chromatography. B, Analytical technologies in the biomedical and life sciences 20120415

• L-Carnitine rescues ketamine-induced attenuated heart rate and MAPK (ERK) activity in zebrafish embryos.

  Reproductive toxicology (Elmsford, N.Y.) 20120401

• Randomized phase III clinical trial of a combined treatment with carnitine + celecoxib ± megestrol acetate for patients with cancer-related anorexia/cachexia syndrome.

  Clinical nutrition (Edinburgh, Scotland) 20120401

• A single mutation in MCCC1 or MCCC2 as a potential cause of positive screening for 3-methylcrotonyl-CoA carboxylase deficiency.

  Molecular genetics and metabolism 20120401

• Metabolic profiles predict adverse events after coronary artery bypass grafting.

  The Journal of thoracic and cardiovascular surgery 20120401

• Serum metabolomics reveals the deregulation of fatty acids metabolism in hepatocellular carcinoma and chronic liver diseases.

  Analytical and bioanalytical chemistry 20120401

• Inhibition of OCTN2-mediated transport of carnitine by etoposide.

  Molecular cancer therapeutics 20120401

• [A primary study of L-carnitine protective effect on corneal and conjunctival epithelium of mouse dry eye model induced by hyperosmolar saline].

  [Zhonghua yan ke za zhi] Chinese journal of ophthalmology 20120401

• Plasma betaine concentrations correlate with plasma cortisol but not with C-reactive protein in an elderly population.

  Clinical chemistry and laboratory medicine 20120318

• Developmental evolution in a patient with multiple acyl-coenzymeA dehydrogenase deficiency under pharmacological treatment.

  European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology Society 20120301

• Metabolic conditioning to attenuate the adverse effects of perioperative fasting and improve patient outcomes.

  Current opinion in clinical nutrition and metabolic care 20120301

• Ergogenic dietary aids for the elderly.

  Nutrition (Burbank, Los Angeles County, Calif.) 20120301

• Combined extraction of acyl carnitines and 26:0 lysophosphatidylcholine from dried blood spots: prospective newborn screening for X-linked adrenoleukodystrophy.

  Molecular genetics and metabolism 20120301

• A randomized phase III clinical trial of a combined treatment for cachexia in patients with gynecological cancers: evaluating the impact on metabolic and inflammatory profiles and quality of life.

  Gynecologic oncology 20120301

• The human OCTN1 (SLC22A4) reconstituted in liposomes catalyzes acetylcholine transport which is defective in the mutant L503F associated to the Crohn's disease.

  Biochimica et biophysica acta 20120301

• Brown adipose tissue mitochondria oxidizing fatty acids generate high levels of reactive oxygen species irrespective of the uncoupling protein-1 activity state.

  Biochimica et biophysica acta 20120301

• Metabolomic profiling of fatty acid and amino acid metabolism in youth with obesity and type 2 diabetes: evidence for enhanced mitochondrial oxidation.

  Diabetes care 20120301

• Expression and functional analysis of intestinal organic cation/L-carnitine transporter (OCTN) in Crohn's disease.

  Journal of Crohn's & colitis 20120301

• Carnitine derivatives: clinical usefulness.

  Current opinion in gastroenterology 20120301

• Topically applied L-carnitine effectively reduces sebum secretion in human skin.

  Journal of cosmetic dermatology 20120301

• Muscle contraction increases carnitine uptake via translocation of OCTN2.

  Biochemical and biophysical research communications 20120224

• Carnitine supplementation for inborn errors of metabolism.

  The Cochrane database of systematic reviews 20120215

• Postprandial changes in plasma acylcarnitine concentrations as markers of fatty acid flux in overweight and obesity.

  Metabolism: clinical and experimental 20120201

• Analysis of plasma ghrelin in patients with medium-chain acyl-CoA dehydrogenase deficiency and glutaric aciduria type II.

  European journal of endocrinology 20120201

• Role of carnitine in the regulation of glucose homeostasis and insulin sensitivity: evidence from in vivo and in vitro studies with carnitine supplementation and carnitine deficiency.

  European journal of nutrition 20120201

• New perspectives on nutritional interventions to augment lipid utilisation during exercise.

  The British journal of nutrition 20120201

• Value of carnitine therapy in kidney dialysis patients and effects on cardiac function from human and animal studies.

  Current drug targets 20120201

• A case of acute valproic acid poisoning treated successfully with L-carnitine.

  European journal of emergency medicine : official journal of the European Society for Emergency Medicine 20120201

• Deletion of CaMKK2 from the liver lowers blood glucose and improves whole-body glucose tolerance in the mouse.

  Molecular endocrinology (Baltimore, Md.) 20120201

• Methacholine delays pulmonary absorption of inhaled β(2)-agonists due to competition for organic cation/carnitine transporters.

  Pulmonary pharmacology & therapeutics 20120201

• Can we treat ulcerative colitis with nutritional supplements?

  Alimentary pharmacology & therapeutics 20120201

• [The function of mitochondrion, carnitine, coenzyme-A, fat acids, glucose, the Randle cycle and insulin: a lecture].

  Klinicheskaia laboratornaia diagnostika 20120201

• [Hepatotoxicity of perfluorooctanoic acid in human hepatocytes using metabonomics].

  Se pu = Chinese journal of chromatography 20120201

• Quantification of acylglycines in human urine by HPLC electrospray ionization-tandem mass spectrometry and the establishment of pediatric reference interval in local Chinese.

  Talanta 20120115

• Atypical antipsychotics rapidly and inappropriately switch peripheral fuel utilization to lipids, impairing metabolic flexibility in rodents.

  Schizophrenia bulletin 20120101

• Endothelial antioxidant compound prolonged the endothelial antiapoptotic effects registered after tadalafil treatment in patients with arterial erectile dysfunction.

  Journal of andrology 20120101

• Variability in the clinical management of fatty acid oxidation disorders: results of a survey of Canadian metabolic physicians.

  Journal of inherited metabolic disease 20120101

• Altered carnitine metabolism in dialysis patients with reduced physical function may be due to dysfunctional fatty acid oxidation.

  Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20120101

• Oxidative stress parameters in urine from patients with disorders of propionate metabolism: a beneficial effect of L:-carnitine supplementation.

  Cellular and molecular neurobiology 20120101

• Post-treatment with the combination of 5-aminoimidazole-4-carboxyamide ribonucleoside and carnitine improves renal function after ischemia/reperfusion injury.

  Shock (Augusta, Ga.) 20120101

• The effect of carnitine on Arabidopsis development and recovery in salt stress conditions.

  Planta 20120101

• Genotype-phenotype correlation in primary carnitine deficiency.

  Human mutation 20120101

• A comparison of the efficacy of 5-fluorouracil/triamcinolone, carnitine and dexamethasone therapy on wound healing in tracheal injury: potential for preventing tracheal stenosis?

  European archives of oto-rhino-laryngology : official journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck Surgery 20120101

• Semen quality in patients with Chlamydia trachomatis genital infection treated concurrently with prulifloxacin and a phytotherapeutic agent.

  Journal of andrology 20120101

• Delineating the role of alterations in lipid metabolism to the pathogenesis of inherited skeletal and cardiac muscle disorders: Thematic Review Series: Genetics of Human Lipid Diseases.

  Journal of lipid research 20120101

• Reduction of butyrylcholinesterase activity in plasma from patients with disorders of propionate metabolism is prevented by treatment with L-carnitine and protein restriction.

  Clinical biochemistry 20120101

• Is propionyl-L-carnitine therapy effective in ulcerative colitis?

  Alimentary pharmacology & therapeutics 20120101

• Levocarnitine for valproic-acid-induced hyperammonemic encephalopathy.

  American journal of health-system pharmacy : AJHP : official journal of the American Society of Health-System Pharmacists 20120101

• Randomized, phase III study comparing osmoprotective carboxymethylcellulose with sodium hyaluronate in dry eye disease.

  European journal of ophthalmology 20120101

• Acetyl-L-carnitine supplementation reverses the age-related decline in carnitine palmitoyltransferase 1 (CPT1) activity in interfibrillar mitochondria without changing the L-carnitine content in the rat heart.

  Mechanisms of ageing and development 20120101

• The protection role of heat shock protein 70 (HSP-70) in the testes of cadmium-exposed rats.

  Bioinformation 20120101

• Carnitine deficiency.

  Romanian journal of morphology and embryology = Revue roumaine de morphologie et embryologie 20120101

• Neuroprotective effects of pre-treatment with l-carnitine and acetyl-L-carnitine on ischemic injury in vivo and in vitro.

  International journal of molecular sciences 20120101

• Expression of genes involved in hepatic carnitine synthesis and uptake in dairy cows in the transition period and at different stages of lactation.

  BMC veterinary research 20120101

• Dramatic decrease of carnitine esters after interruption of exogenous carnitine supply in hemodialysis patients.

  Renal failure 20120101

• Effects of L-carnitine against oxidative stress in human hepatocytes: involvement of peroxisome proliferator-activated receptor alpha.

  Journal of biomedical science 20120101

• Supplementation with l-carnitine downregulates genes of the ubiquitin proteasome system in the skeletal muscle and liver of piglets.

  Animal : an international journal of animal bioscience 20120101

• Levocarnitine-induced hypophosphatemia in a hemodialysis patient with acute valproic acid toxicity.

  The Journal of neuropsychiatry and clinical neurosciences 20120101

• Propionyl-L-carnitine corrects metabolic and cardiovascular alterations in diet-induced obese mice and improves liver respiratory chain activity.

  PloS one 20120101

• Metabolomic changes and protective effect of (L)-carnitine in rat kidney ischemia/reperfusion injury.

  Kidney & blood pressure research 20120101

• Modelling and analysis of central metabolism operating regulatory interactions in salt stress conditions in a L-carnitine overproducing E. coli strain.

  PloS one 20120101

• Caloric restriction alters the metabolic response to a mixed-meal: results from a randomized, controlled trial.

  PloS one 20120101

• Cyclic Vomiting Syndrome (CVS): is there a difference based on onset of symptoms--pediatric versus adult?

  BMC gastroenterology 20120101

• Muscle or liver-specific Sirt3 deficiency induces hyperacetylation of mitochondrial proteins without affecting global metabolic homeostasis.

  Scientific reports 20120101

• [Effects of L-carnitine on ejaculate parameters in males from infertile couples].

  Urologiia (Moscow, Russia : 1999) 20120101

•  Hepatotoxicity associated with dietary energy supplements: use and abuse by young athletes.

  Annals of hepatology 20120101

• Inhibition of gene expression of organic cation/carnitine transporter and antioxidant enzymes in oxazaphosphorines-induced acute cardiomyopathic rat models.

  Oxidative medicine and cellular longevity 20120101

• Metabolomic profiling reveals mitochondrial-derived lipid biomarkers that drive obesity-associated inflammation.

  PloS one 20120101

• Hypoxia-induced lipid peroxidation in the brain during postnatal ontogenesis.

  Physiological research 20120101

• The histopathological comparison of L-carnitine with amifostine for protective efficacy on radiation-induced acute small intestinal toxicity.

  Journal of cancer research and therapeutics 20120101

• Long-chain acylcarnitines regulate the hERG channel.

  PloS one 20120101

• Metabolomics of dietary fatty acid restriction in patients with phenylketonuria.

  PloS one 20120101

• PPAR-γ regulates carnitine homeostasis and mitochondrial function in a lamb model of increased pulmonary blood flow.

  PloS one 20120101

• Oxygen glucose deprivation in rat hippocampal slice cultures results in alterations in carnitine homeostasis and mitochondrial dysfunction.

  PloS one 20120101

• L-carnosine affects the growth of Saccharomyces cerevisiae in a metabolism-dependent manner.

  PloS one 20120101

• Functional effects of different medium-chain acyl-CoA dehydrogenase genotypes and identification of asymptomatic variants.

  PloS one 20120101

• Role of supplementary L-carnitine in exercise and exercise recovery.

  Medicine and sport science 20120101

• SLC22A5 mutations in a patient with systemic primary carnitine deficiency: the first Korean case confirmed by biochemical and molecular investigation.

  Annals of clinical and laboratory science 20120101

• Carnitine deficiency in OCTN2-/- newborn mice leads to a severe gut and immune phenotype with widespread atrophy, apoptosis and a pro-inflammatory response.

  PloS one 20120101

• Downregulation of oxidative and nitrosative apoptotic signaling by L-carnitine in Ifosfamide-induced Fanconi syndrome rat model.

  Oxidative medicine and cellular longevity 20120101

• Human Pompe disease-induced pluripotent stem cells for pathogenesis modeling, drug testing and disease marker identification.

  Human molecular genetics 20111215

• Carnitine and carnitine orotate affect the expression of the prolactin-releasing peptide gene.

  Genetics and molecular research : GMR 20111206

• Protective effect of L-carnitine on experimental lead toxicity in rats: a clinical, histopathological and immunohistochemical study.

  Biotechnic & histochemistry : official publication of the Biological Stain Commission 20111201

• Protective effect of L-carnitine versus amifostine against cisplatin-induced nephrotoxicity in rats.

  Medical oncology (Northwood, London, England) 20111201

• Selenium and L-carnitine reduce oxidative stress in the heart of rat induced by 2.45-GHz radiation from wireless devices.

  Biological trace element research 20111201

• A combination of grape extract, green tea extract and L-carnitine improves high-fat diet-induced obesity, hyperlipidemia and non-alcoholic fatty liver disease in mice.

  Phytotherapy research : PTR 20111201

• Evaluation of the efficacy of a topical cosmetic slimming product combining tetrahydroxypropyl ethylenediamine, caffeine, carnitine, forskolin and retinol, In vitro, ex vivo and in vivo studies.

  International journal of cosmetic science 20111201

• Carnitine supplementation modulates high dietary copper-induced oxidative toxicity and reduced performance in laying hens.

  Biological trace element research 20111201

• Functional analysis of pharmacogenetic variants of human organic cation/carnitine transporter 2 (hOCTN2) identified in Singaporean populations.

  Biochemical pharmacology 20111201

• Subacute bilateral visual loss in methylmalonic acidemia.

  Journal of neuro-ophthalmology : the official journal of the North American Neuro-Ophthalmology Society 20111201

• Severe dysfunction of respiratory chain and cholesterol metabolism in Atp7b(-/-) mice as a model for Wilson disease.

  Biochimica et biophysica acta 20111201

• The stability of markers in dried-blood spots for recommended newborn screening disorders in the United States.

  Clinical biochemistry 20111201

• Hepatic and muscular effects of different dietary fat content in VLCAD deficient mice.

  Molecular genetics and metabolism 20111201

• Effect of L-carnitine on the synthesis of nitric oxide in RAW 264·7 murine macrophage cell line.

  Cell biochemistry and function 20111201

• The effects of exercise training on γ-butyrobetaine hydroxylase and novel organic cation transporter-2 gene expression in the rat.

  Applied physiology, nutrition, and metabolism = Physiologie appliquee, nutrition et metabolisme 20111201

• Carnitine administration reduces cytokine levels, improves food intake, and ameliorates body composition in tumor-bearing rats.

  Cancer investigation 20111201

• [The impact of L-carnitine administration on the serum level of myocardium injury markers in patients with acute carbon monoxide poisoning].

  Zhongguo wei zhong bing ji jiu yi xue = Chinese critical care medicine = Zhongguo weizhongbing jijiuyixue 20111201

• Analysis of acylcarnitine levels by tandem mass spectrometry in epileptic children receiving valproate and oxcarbazepine.

  Epileptic disorders : international epilepsy journal with videotape 20111201

• Derivatives of R-aminocarnitine without ammonium moiety as liver carnitine palmitoyltransferase I (L-CPT I) inhibitors.

  ChemMedChem 20111104

• PKA/AKAP1 and PP2A/Bβ2 regulate neuronal morphogenesis via Drp1 phosphorylation and mitochondrial bioenergetics.

  The Journal of neuroscience : the official journal of the Society for Neuroscience 20111102

• Evaluation of valproate effects on acylcarnitine in epileptic children by LC-MS/MS.

  Brain & development 20111101

• Bioactives from bitter melon enhance insulin signaling and modulate acyl carnitine content in skeletal muscle in high-fat diet-fed mice.

  The Journal of nutritional biochemistry 20111101

• Normal atmospheric oxygen tension and the use of antioxidants improve hepatocyte spheroid viability and function.

  Journal of cellular physiology 20111101

• Effects of l-carnitine supplement on serum amyloid A and vascular inflammation markers in hemodialysis patients: a randomized controlled trial.

  Journal of renal nutrition : the official journal of the Council on Renal Nutrition of the National Kidney Foundation 20111101

• Profiling of acylcarnitines and sterols from dried blood or plasma spot by atmospheric pressure thermal desorption chemical ionization (APTDCI) tandem mass spectrometry.

  Biochimica et biophysica acta 20111101

• Impaired fasting tolerance among Alaska native children with a common carnitine palmitoyltransferase 1A sequence variant.

  Molecular genetics and metabolism 20111101

• Plasma pharmacokinetics and gastrointestinal transit of a new propionyl-L-carnitine controlled release formulation.

  Xenobiotica; the fate of foreign compounds in biological systems 20111101

• Bezafibrate upregulates carnitine palmitoyltransferase II expression and promotes mitochondrial energy crisis dissipation in fibroblasts of patients with influenza-associated encephalopathy.

  Molecular genetics and metabolism 20111101

• A review of the logistic role of L-carnitine in the management of radiation toxicity and radiotherapy side effects.

  Journal of applied toxicology : JAT 20111101

• Tandem mass spectrometry findings at autopsy for detection of metabolic disease in infant deaths: postmortem changes and confounding factors.

  Journal of clinical pathology 20111101

• Randomised clinical trial: the efficacy and safety of propionyl-L-carnitine therapy in patients with ulcerative colitis receiving stable oral treatment.

  Alimentary pharmacology & therapeutics 20111101

• Re: Gurocak et al.: Inflammation and oxidative stress in testicular torsion: do they deserve intensive treatment to save both guilty and innocent testes? (Urology 2011;78:164-169).

  Urology 20111101

• The effect of L-carnitine supplementation on lipid parameters, inflammatory and nutritional markers in maintenance hemodialysis patients.

  Saudi journal of kidney diseases and transplantation : an official publication of the Saudi Center for Organ Transplantation, Saudi Arabia 20111101

• L-carnitine increases survival in a murine model of severe verapamil toxicity.

  Academic emergency medicine : official journal of the Society for Academic Emergency Medicine 20111101

• [Effects of combined administration of ripronat and rotavit royal on the working capacity of the young football players].

  Georgian medical news 20111101

• L-carnitine supplementation improves hematological pattern in patients affected by HCV treated with Peg interferon-α 2b plus ribavirin.

  World journal of gastroenterology 20111021

• Protective role of L-carnitine supplementation against exhaustive exercise induced oxidative stress in rats.

  European journal of pharmacology 20111015

• [Carnitine: function, metabolism and value in hepatic failure during chronic alcohol intoxication].

  Postepy higieny i medycyny doswiadczalnej (Online) 20111007

• Synthesis, transport and mechanism of a type I prodrug: L-carnitine ester of prednisolone.

  Molecular pharmaceutics 20111003

• Comparison between orlistat plus l-carnitine and orlistat alone on inflammation parameters in obese diabetic patients.

  Fundamental & clinical pharmacology 20111001

• Beta-ketothiolase deficiency brought with lethargy: case report.

  Human & experimental toxicology 20111001

• Labial salivary gland biopsy in the investigation of neonatal hemochromatosis.

  Journal of oral and maxillofacial surgery : official journal of the American Association of Oral and Maxillofacial Surgeons 20111001

• Unexpected awakening from comatose thyroid storm after a single intravenous injection of L-carnitine.

  Intensive care medicine 20111001

• First-trimester prediction of preeclampsia using metabolomic biomarkers: a discovery phase study.

  Prenatal diagnosis 20111001

• [Acute valproic acid intoxication: interest of a treatment by extracoporeal elimination combined with L-carnitine].

  Annales francaises d'anesthesie et de reanimation 20111001

• Bladder cancer determination via two urinary metabolites: a biomarker pattern approach.

  Molecular & cellular proteomics : MCP 20111001

• Effects of exercise intensity and altered substrate availability on cardiovascular and metabolic responses to exercise after oral carnitine supplementation in athletes.

  International journal of sport nutrition and exercise metabolism 20111001

• Carnitine supplementation for valproate-related hyperammonemia to maintain therapeutic valproate level.

  Journal of clinical psychopharmacology 20111001

• Fat burners: nutrition supplements that increase fat metabolism.

  Obesity reviews : an official journal of the International Association for the Study of Obesity 20111001

• Prevention of free fatty acid-induced hepatic lipotoxicity by carnitine via reversal of mitochondrial dysfunction.

  Liver international : official journal of the International Association for the Study of the Liver 20111001

• An in vitro model for testing drugs to treat tinnitus.

  European journal of pharmacology 20110930

• L-carnitine enhances oocyte maturation and development of parthenogenetic embryos in pigs.

  Theriogenology 20110915

• Mildronate treatment improves functional recovery following middle cerebral artery occlusion in rats.

  Behavioural brain research 20110912

• Synthesis and in vitro characterization of drug conjugates of l-carnitine as potential prodrugs that target human Octn2.

  Journal of pharmaceutical sciences 20110901

• L-carnitine is an osmotic agent suitable for peritoneal dialysis.

  Kidney international 20110901

• L-carnitine--metabolic functions and meaning in humans life.

  Current drug metabolism 20110901

• Effects of L-carnitine supplementation on quality characteristics of fresh pork bellies from pigs fed 3 levels of corn oil.

  Journal of animal science 20110901

• Increased beta-oxidation and improved oocyte developmental competence in response to l-carnitine during ovarian in vitro follicle development in mice.

  Biology of reproduction 20110901

• Kinetics of butyrate metabolism in the normal colon and in ulcerative colitis: the effects of substrate concentration and carnitine on the β-oxidation pathway.

  Alimentary pharmacology & therapeutics 20110901

• Improvement of high-fat diet-induced obesity by a mixture of red grape extract, soy isoflavone and L-carnitine: implications in cardiovascular and non-alcoholic fatty liver diseases.

  Food and chemical toxicology : an international journal published for the British Industrial Biological Research Association 20110901

• Protective effect of L-carnitine against H(2)O(2)-induced neurotoxicity in neuroblastoma (SH-SY5Y) cells.

  Neurological research 20110901

• Regular endurance exercise improves the diminished hepatic carnitine status in mice fed a high-fat diet.

  Molecular nutrition & food research 20110901

• Effect of L-carnitine on oxidative stress and platelet activation after major surgery.

  Acta anaesthesiologica Scandinavica 20110901

• Rare magnetic resonance imaging findings in medium-chain acyl-coenzyme A dehydrogenase deficiency.

  Pediatric neurology 20110901

• Mildronate treatment alters γ-butyrobetaine and l-carnitine concentrations in healthy volunteers.

  The Journal of pharmacy and pharmacology 20110901

• The consequences of valproate overdose.

  Clinical chemistry 20110901

• L-carnitine: more than just an alternative to glucose as an osmotic agent for peritoneal dialysis?

  Kidney international 20110901

• Protective action of L-carnitine on cardiac mitochondrial function and structure against fatty acid stress.

  Biochemical and biophysical research communications 20110819

• Metabolomes of the psychrotolerant bacterium Listeria monocytogenes 10403S grown at 37 °C and 8 °C.

  International journal of food microbiology 20110802

• Early changes in oxidative stress markers in a rat model of acute stress: effect of l-carnitine on the striatum.

  Basic & clinical pharmacology & toxicology 20110801

• Expanded molecular features of carnitine acyl-carnitine translocase (CACT) deficiency by comprehensive molecular analysis.

  Molecular genetics and metabolism 20110801

• Fatal viral infection-associated encephalopathy in two Chinese boys: a genetically determined risk factor of thermolabile carnitine palmitoyltransferase II variants.

  Journal of human genetics 20110801

• Discovery of sexual dimorphisms in metabolic and genetic biomarkers.

  PLoS genetics 20110801

• Metabolic agents that enhance ATP can improve cognitive functioning: a review of the evidence for glucose, oxygen, pyruvate, creatine, and L-carnitine.

  Nutrients 20110801

• Role of L-carnitine in male infertility.

  JPMA. The Journal of the Pakistan Medical Association 20110801

• L-carnitine ameliorates cancer cachexia in mice by regulating the expression and activity of carnitine palmityl transferase.

  Cancer biology & therapy 20110715

• Mouse γ-butyrobetaine dioxygenase is regulated by peroxisome proliferator-activated receptor α through a PPRE located in the proximal promoter.

  Biochemical pharmacology 20110715

• Teaching NeuroImages: Glutaric aciduria type 1 (glutaryl-CoA dehydrogenase deficiency).

  Neurology 20110705

• Effects of oral L-carnitine supplementation on insulin sensitivity indices in response to glucose feeding in lean and overweight/obese males.

  Amino acids 20110701

• Long-chain acylcarnitine deficiency in patients with chronic fatigue syndrome. Potential involvement of altered carnitine palmitoyltransferase-I activity.

  Journal of internal medicine 20110701

• Dynamic adaptive changes of the serum carnitine esters during and after L-carnitine supplementation in patients with maintenance haemodialysis.

  Scandinavian journal of clinical and laboratory investigation 20110701

• Inflammation and oxidative stress in testicular torsion: do they deserve intensive treatment to save both guilty and innocent testes?

  Urology 20110701

• Metabolic remodeling of human skeletal myocytes by cocultured adipocytes depends on the lipolytic state of the system.

  Diabetes 20110701

• Offspring metabolomic response to maternal protein restriction in a rat model of intrauterine growth restriction (IUGR).

  Journal of proteome research 20110701

• Single dose administration of L-carnitine improves antioxidant activities in healthy subjects.

  The Tohoku journal of experimental medicine 20110701

• Effects of Zn(II) complex with vitamins C and U, and carnitine on metabolic syndrome model rats.

  Metallomics : integrated biometal science 20110701

• A 'conditionally essential' nutrient, L-carnitine, as a primary suspect in endometriosis.

  Fertility and sterility 20110630

• The disruption of L-carnitine metabolism by aluminum toxicity and oxidative stress promotes dyslipidemia in human astrocytic and hepatic cells.

  Toxicology letters 20110624

• L-Carnitine protects plasma components against oxidative alterations.

  Nutrition (Burbank, Los Angeles County, Calif.) 20110601

• Carnitine serum levels and levocarnitine administration in multiple sclerosis patients treated with natalizumab.

  European journal of neurology 20110601

• Increased mitochondrial substrate sensitivity in skeletal muscle of patients with type 2 diabetes.

  Diabetologia 20110601

• Positive newborn screen in a normal infant of a mother with asymptomatic very long-chain Acyl-CoA dehydrogenase deficiency.

  The Journal of pediatrics 20110601

• The possible role of L-carnitine on the skeletal muscle of ovariectomized rats.

  Journal of molecular histology 20110601

• Determination of betaines in vegetable oils by capillary electrophoresis tandem mass spectrometry--application to the detection of olive oil adulteration with seed oils.

  Electrophoresis 20110601

• Fatigue and serum carnitine levels in chronic liver disease.

  Alimentary pharmacology & therapeutics 20110601

• Carnitine deficiency increases susceptibility to bupivacaine-induced cardiotoxicity in rats.

  Anesthesiology 20110601

• Selective regulation of cardiac organic cation transporter novel type 2 (OCTN2) in dilated cardiomyopathy.

  The American journal of pathology 20110601

• L-carnitine protects against nickel-induced neurotoxicity by maintaining mitochondrial function in Neuro-2a cells.

  Toxicology and applied pharmacology 20110515

• Improved tandem mass spectrometry (MS/MS) derivatized method for the detection of tyrosinemia type I, amino acids and acylcarnitine disorders using a single extraction process.

  Clinica chimica acta; international journal of clinical chemistry 20110512

• Carnitine palmitoyltransferase (CPT) modulators: a medicinal chemistry perspective on 35 years of research.

  Journal of medicinal chemistry 20110512

• Carnitine is necessary to maintain the phenotype and function of brown adipose tissue.

  Laboratory investigation; a journal of technical methods and pathology 20110501

• Remote communication through solute carriers and ATP binding cassette drug transporter pathways: an update on the remote sensing and signaling hypothesis.

  Molecular pharmacology 20110501

• A role for proline synthesis and transport in Listeria monocytogenes barotolerance.

  Journal of applied microbiology 20110501

• Maternal medium-chain acyl-CoA dehydrogenase deficiency identified by newborn screening.

  Molecular genetics and metabolism 20110501

• Plasma acylcarnitines are associated with physical performance in elderly men.

  The journals of gerontology. Series A, Biological sciences and medical sciences 20110501

• Combination therapy for erectile dysfunction: an update review.

  Asian journal of andrology 20110501

• Pharmacological effects and clinical applications of propionyl-L-carnitine.

  Nutrition reviews 20110501

• Peyronie's disease: review of nonsurgical treatment options.

  The Urologic clinics of North America 20110501

• [Effect of valsartan and carnitine on cardiomyocyte Calpain-1 and Bcl-xl expressions of dogs with chronic alcohol intake-induced cardiomyopathy].

  Zhonghua xin xue guan bing za zhi 20110501

• [Effects of L-carnitine on the apoptosis of spermatogenic cells and epididymal sperm count and motility in rats with diabetes mellitus].

  Zhonghua nan ke xue = National journal of andrology 20110501

• Future directions in metabolic disease testing.

  Clinical biochemistry 20110501

• Selective screening for inborn errors of metabolism--assessment of metabolites in body fluids.

  Clinical biochemistry 20110501

• Differential metabolic impact of gastric bypass surgery versus dietary intervention in obese diabetic subjects despite identical weight loss.

  Science translational medicine 20110427

• Capillary electrophoresis with contactless conductivity detection for the determination of carnitine and acylcarnitines in clinical samples.

  Journal of chromatography. B, Analytical technologies in the biomedical and life sciences 20110415

• [Effects of fatigue and restraint stress on the expression of carnitine palmitoyltransferase-I and 5-hydroxytryptamine receptors in aorta of rats].

  Zhonghua yi xue za zhi 20110405

• The effects of long- or medium-chain fat diets on glucose tolerance and myocellular content of lipid intermediates in rats.

  Obesity (Silver Spring, Md.) 20110401

• mRNA expression of genes involved in fatty acid utilization in skeletal muscle and white adipose tissues of sows during lactation.

  Comparative biochemistry and physiology. Part A, Molecular & integrative physiology 20110401

• Evidence that L-carnitine and selenium supplementation reduces oxidative stress in phenylketonuric patients.

  Cellular and molecular neurobiology 20110401

• Retrospective review of Japanese sudden unexpected death in infancy: the importance of metabolic autopsy and expanded newborn screening.

  Molecular genetics and metabolism 20110401

• Transcellular movement of hydroxyurea is mediated by specific solute carrier transporters.

  Experimental hematology 20110401

• Plasma carnitine is associated with fatigue in chronic hepatitis C but not in the irritable bowel syndrome.

  Alimentary pharmacology & therapeutics 20110401

• Boosting fat burning with carnitine: an old friend comes out from the shadow.

  The Journal of physiology 20110401

• Analysis of inborn errors of metabolism: disease spectrum for expanded newborn screening in Hong Kong.

  Chinese medical journal 20110401

• Expanded newborn screening for detection of vitamin B12 deficiency.

  JAMA 20110323

• Proficiency testing outcomes of 3-hydroxyisovalerylcarnitine measurements by tandem mass spectrometry in newborn screening.

  Clinica chimica acta; international journal of clinical chemistry 20110318

• Ultra-high performance liquid chromatography tandem mass spectrometry for comprehensive analysis of urinary acylcarnitines.

  Analytica chimica acta 20110309

• Effects of combination of sibutramine and L-carnitine compared with sibutramine monotherapy on inflammatory parameters in diabetic patients.

  Metabolism: clinical and experimental 20110301

• Dietary L-carnitine alters gene expression in skeletal muscle of piglets.

  Molecular nutrition & food research 20110301

• Acute and subchronic toxicity of FCD, a soybean extract combined with L-carnitine, in Sprague-Dawley rats.

  Regulatory toxicology and pharmacology : RTP 20110301

• Glycosylation of the OCTN2 carnitine transporter: study of natural mutations identified in patients with primary carnitine deficiency.

  Biochimica et biophysica acta 20110301

• Pharmacological use of L-carnitine in uremic anemia: has its full potential been exploited?

  Pharmacological research 20110301

• Induction of PDK4 in the heart muscle of JVS mice, an animal model of systemic carnitine deficiency, does not appear to reduce glucose utilization by the heart.

  Molecular genetics and metabolism 20110301

• A high-fat diet elicits differential responses in genes coordinating oxidative metabolism in skeletal muscle of lean and obese individuals.

  The Journal of clinical endocrinology and metabolism 20110301

• L-carnitine improves oxidative stress and suppressed energy metabolism but not renal dysfunction following release of acute unilateral ureteral obstruction in rat.

  Neurourology and urodynamics 20110301

• Antioxidants in the treatment of diabetes.

  Current diabetes reviews 20110301

• Modulated human maternal and premature neonatal erythrocyte membrane enzyme activities in relation to the mode of delivery: in vitro restoration with L-carnitine.

  Clinical chemistry and laboratory medicine 20110301

• Clinical validation of cutoff target ranges in newborn screening of metabolic disorders by tandem mass spectrometry: a worldwide collaborative project.

  Genetics in medicine : official journal of the American College of Medical Genetics 20110301

• Carnitine and coenzyme Q10 levels in individuals with Prader-Willi syndrome.

  American journal of medical genetics. Part A 20110301

• Abnormally low serum acylcarnitine levels in narcolepsy patients.

  Sleep 20110301

• Effects of carnitine and coenzyme Q10 on lipid profile and serum levels of lipoprotein(a) in maintenance hemodialysis patients on statin therapy.

  Iranian journal of kidney diseases 20110301

• In vivo neuroprotective effect of L-carnitine against oxidative stress in maple syrup urine disease.

  Metabolic brain disease 20110301

• Aristolochic acid-induced destruction of organic ion transporters and fatty acid metabolic disorder in the kidney of rats.

  Toxicology letters 20110225

• Chronic oral ingestion of L-carnitine and carbohydrate increases muscle carnitine content and alters muscle fuel metabolism during exercise in humans.

  The Journal of physiology 20110215

• Altered glucose transport to utero-embryonic unit in relation to delayed embryonic development in the Indian short-nosed fruit bat, Cynopterus sphinx.

  Molecular and cellular endocrinology 20110210

• Hypoxia-mediated down-regulation of OCTN2 and PPARα expression in human placentas and in BeWo cells.

  Molecular pharmaceutics 20110207

• Short-term effects of dietary fatty acids on muscle lipid composition and serum acylcarnitine profile in human subjects.

  Obesity (Silver Spring, Md.) 20110201

• Clinical correlates of low serum carnitine levels in hospitalized psychiatric patients.

  The world journal of biological psychiatry : the official journal of the World Federation of Societies of Biological Psychiatry 20110201

• Lipid storage myopathy.

  Current neurology and neuroscience reports 20110201

• Long-term effects of neonatal treatment with dexamethasone, L-carnitine, and combinations thereof in rats.

  Pediatric research 20110201

• Urgent metabolic service improves survival in long-chain 3-hydroxyacyl-CoA dehydrogenase (LCHAD) deficiency detected by symptomatic identification and pilot newborn screening.

  Journal of inherited metabolic disease 20110201

• Questionnaire-based self-reported nutrition habits associate with serum metabolism as revealed by quantitative targeted metabolomics.

  European journal of epidemiology 20110201

• Effect of caloric restriction with and without exercise on metabolic intermediates in nonobese men and women.

  The Journal of clinical endocrinology and metabolism 20110201

• [Low L-carnitine levels: can it be a cause of nocturnal blood pressure changes in patients with type 2 diabetes mellitus?].

  Anadolu kardiyoloji dergisi : AKD = the Anatolian journal of cardiology 20110201

• A new method for the determination of free L-carnitine in serum samples based on high field single quantum coherence filtering 1H-NMR spectroscopy.

  Analytical and bioanalytical chemistry 20110201

• Selective reversible inhibition of liver carnitine palmitoyl-transferase 1 by teglicar reduces gluconeogenesis and improves glucose homeostasis.

  Diabetes 20110201

• Gender differences in locomotor and stereotypic behavior associated with l-carnitine treatment in mice.

  Gender medicine 20110201

• Upregulation of mammary gland OCTNs maintains carnitine homeostasis in suckling infants.

  Biochemical and biophysical research communications 20110128

• L-carnitine reduces doxorubicin-induced apoptosis through a prostacyclin-mediated pathway in neonatal rat cardiomyocytes.

  International journal of cardiology 20110121

• Role of FOXA and Sp1 in mitochondrial acylcarnitine carrier gene expression in different cell lines.

  Biochemical and biophysical research communications 20110107

• Enhanced bioavailability of L-carnitine after painless intradermal delivery vs. oral administration in rats.

  Pharmaceutical research 20110101

• LC-MS/MS progress in newborn screening.

  Clinical biochemistry 20110101

• Genotype-phenotype correlations in a large series of patients with muscle type CPT II deficiency.

  Neurological research 20110101

• Effect of propionyl-L-carnitine on a background of monitored exercise in patients with claudication secondary to peripheral artery disease.

  Journal of cardiopulmonary rehabilitation and prevention 20110101

• Therapeutic modulation of cerebral L-lysine metabolism in a mouse model for glutaric aciduria type I.

  Brain : a journal of neurology 20110101

• The alteration of asymmetric dimetilarginine (ADMA) levels in cardiac and gastrocnemius muscles following radioactive iodine application in guinea pigs and the effect of L-carnitine on this alteration.

  International journal of radiation biology 20110101

• Carnitine regulates myocardial metabolism by Peroxisome Proliferator-Activated Receptor-alpha (PPARalpha) in alcoholic cardiomyopathy.

  Medical science monitor : international medical journal of experimental and clinical research 20110101

• Acute encephalopathy in a child with secondary carnitine deficiency due to pivalate-conjugated antibiotics.

  The Pediatric infectious disease journal 20110101

• Risk factors and metabolic mechanisms in the pathogenesis of uraemic cardiac disease.

  Frontiers in bioscience (Landmark edition) 20110101

• Absorption enhancement effect of acylcarnitines through changes in tight junction protein in Caco-2 cell monolayers.

  Drug metabolism and pharmacokinetics 20110101

• Acylcarnitines: analysis in plasma and whole blood using tandem mass spectrometry.

  Methods in molecular biology (Clifton, N.J.) 20110101

• Clinical, biochemical and genetic analyses in two Korean patients with medium-chain acyl-CoA dehydrogenase deficiency.

  The Korean journal of laboratory medicine 20110101

• Carnitine and metabolic correlates in hospitalized psychiatric patients: a follow-through report.

  Journal of psychiatric practice 20110101

• Mutations of ACADS gene associated with short-chain acyl-coenzyme A dehydrogenase deficiency.

  Annals of clinical and laboratory science 20110101

• L-Carnitine attenuates ifosfamide-induced carnitine deficiency and decreased intramitochondrial CoA-SH in rat kidney tissues.

  Journal of nephrology 20110101

• L-Carnitine and intestinal inflammation.

  Vitamins and hormones 20110101

• Postnatal variations in blood free and acylcarnitines.

  Journal of clinical laboratory analysis 20110101

• Whole blood propionylcarnitine in newborns with orofacial cleft.

  Maternal & child nutrition 20110101

• Nutritional support and cardioprotection with L-carnitine: prescription appropriateness and safety concerns in Mexican neonates.

  Journal of population therapeutics and clinical pharmacology = Journal de la therapeutique des populations et de la pharamcologie clinique 20110101

• [L-carnitine treatment and fish odor syndrome: an unwaited adverse effect].

  Revue neurologique 20110101

• Critical update for the clinical use of L-carnitine analogs in cardiometabolic disorders.

  Vascular health and risk management 20110101

• The role of carnitine in preventing renal damage developed as a result of infrarenal aortic ischemia-reperfusion.

  Renal failure 20110101

• A combination of (ω-3) polyunsaturated fatty acids, polyphenols and L-carnitine reduces the plasma lipid levels and increases the expression of genes involved in fatty acid oxidation in human peripheral blood mononuclear cells and HepG2 cells.

  Annals of nutrition & metabolism 20110101

• Differential effects of short- and long-term high-fat diet feeding on hepatic fatty acid metabolism in rats.

  Biochimica et biophysica acta 20110101

• A prospective double-blind, randomized clinical trial of levocarnitine to treat autism spectrum disorders.

  Medical science monitor : international medical journal of experimental and clinical research 20110101

• Quantification of total and free carnitine in human plasma by hydrophilic interaction liquid chromatography tandem mass spectrometry.

  Journal of chromatographic science 20110101

• Efficacy and safety of two analogs of L-carnitine on rats made insulin resistant by a high-fructose diet.

  Pharmacology 20110101

• Diagnosis, treatment and outcome of glutaric aciduria type I in Zhejiang Province, China.

  Medical science monitor : international medical journal of experimental and clinical research 20110101

• SMA CARNIVAL TRIAL PART II: a prospective, single-armed trial of L-carnitine and valproic acid in ambulatory children with spinal muscular atrophy.

  PloS one 20110101

• [L-carnitine in peritoneal dialysis].

  Giornale italiano di nefrologia : organo ufficiale della Societa italiana di nefrologia 20110101

• Safety, efficacy and physiological actions of a lysine-free, arginine-rich formula to treat glutaryl-CoA dehydrogenase deficiency: focus on cerebral amino acid influx.

  Molecular genetics and metabolism 20110101

• Topical and transdermal delivery of L-carnitine.

  Skin pharmacology and physiology 20110101

• High degree of efficacy in the treatment of cyclic vomiting syndrome with combined co-enzyme Q10, L-carnitine and amitriptyline, a case series.

  BMC neurology 20110101

• Administration of L-carnitine and mildronate improves endothelial function and decreases mortality in hypertensive Dahl rats.

  Pharmacological reports : PR 20110101

• Enhancement of lipid metabolism with L-carnitine during in vitro maturation improves nuclear maturation and cleavage ability of follicular porcine oocytes.

  Reproduction, fertility, and development 20110101

• Cardiac involvement in inflammatory bowel disease: role of acylcarnitine esters.

  La Clinica terapeutica 20110101

• Sickness behavior clustering in children with cancer.

  Journal of pediatric oncology nursing : official journal of the Association of Pediatric Oncology Nurses 20110101

• Carnitine precursor γ-butyrobetaine is a novel substrate of the Na(+)- and Cl(-)-dependent GABA transporter Gat2.

  Drug metabolism and pharmacokinetics 20110101

• Bile acid sequestration reduces plasma glucose levels in db/db mice by increasing its metabolic clearance rate.

  PloS one 20110101

• Primary carnitine deficiency and sudden death: in vivo evidence of myocardial lipid peroxidation and sulfonylation of sarcoendoplasmic reticulum calcium ATPase 2.

  Cardiology 20110101

• Mouse studies to shape clinical trials for mitochondrial diseases: high fat diet in Harlequin mice.

  PloS one 20110101

• [L-carnitine in infant formulas].

  Voprosy pitaniia 20110101

• Covalent modification of gaseous peptide ions with N-hydroxysuccinimide ester reagent ions.

  Journal of the American Chemical Society 20101229

• Structural and mechanistic studies on γ-butyrobetaine hydroxylase.

  Chemistry & biology 20101222

• Sensitive determination of D-carnitine as enantiomeric impurity of levo-carnitine in pharmaceutical formulations by capillary electrophoresis-tandem mass spectrometry.

  Journal of pharmaceutical and biomedical analysis 20101215

• Maternal isovaleric acidemia: observation of distinctive changes in plasma amino acids and carnitine profiles during pregnancy.

  Clinica chimica acta; international journal of clinical chemistry 20101214

• Quantitative metabolomic profiling of serum and urine in DSS-induced ulcerative colitis of mice by (1)H NMR spectroscopy.

  Journal of proteome research 20101203

• Post-mortem MRI reveals CPT2 deficiency after sudden infant death.

  European journal of pediatrics 20101201

• Beta-oxidation is essential for mouse oocyte developmental competence and early embryo development.

  Biology of reproduction 20101201

• Global analysis of circulating metabolites in hibernating ground squirrels.

  Comparative biochemistry and physiology. Part D, Genomics & proteomics 20101201

• Effects of antioxidants on post-thawed bovine sperm and oxidative stress parameters: antioxidants protect DNA integrity against cryodamage.

  Cryobiology 20101201

• Ameliorating effects of L-carnitine on diabetic podocyte injury.

  Journal of medicinal food 20101201

• Carnitine status and lactate increase in patients with type I juvenile diabetes.

  Minerva pediatrica 20101201

• The influence of L-carnitine suplementation on the antioxidative abilities of serum and the central nervous system of ethanol-induced rats.

  Metabolic brain disease 20101201

• Cellular stress responses, mitostress and carnitine insufficiencies as critical determinants in aging and neurodegenerative disorders: role of hormesis and vitagenes.

  Neurochemical research 20101201

• [Blood spot carnitine and acylcarnitine in newborn to adolescence: measured by tandem mass spectrometry].

  Zhonghua er ke za zhi = Chinese journal of pediatrics 20101201

• Quantitative measurement of urinary excretion of 3-hydroxyisovaleryl carnitine by LC-MS/MS as an indicator of biotin status in humans.

  Analytical chemistry 20101115

• Cadmium toxicity in spermatogenesis and protective effects of L-carnitine in adult male rats.

  Biological trace element research 20101101

• L-carnitine supplementation and adipokines in patients with end-stage renal disease on regular hemodialysis.

  Experimental and clinical endocrinology & diabetes : official journal, German Society of Endocrinology [and] German Diabetes Association 20101101

• An acid hydrolysis method for quantification of plasma free and total carnitine by flow injection tandem mass spectrometry.

  Clinical biochemistry 20101101

• Compound muscle action potential and motor function in children with spinal muscular atrophy.

  Muscle & nerve 20101101

• Effect of L-carnitine on liver cell membranes in ethanol-intoxicated rats.

  Chemico-biological interactions 20101006

• Effects of phosphodiesterase-5 inhibitors on Leydig cell secretory function in oligoasthenospermic infertile men: a randomized trial.

  BJU international 20101001

• Effects of L-carnitine on oxidative stress responses in patients with renal disease.

  Medicine and science in sports and exercise 20101001

• Intestinal fermentation modulates postprandial acylcarnitine profile and nitrogen metabolism in a true carnivore: the domestic cat ( Felis catus).

  The British journal of nutrition 20101001

• Useful second-tier tests in expanded newborn screening of isovaleric acidemia and methylmalonic aciduria.

  Journal of inherited metabolic disease 20101001

• Tandem mass spectrometry screening for very long-chain acyl-CoA dehydrogenase deficiency: the value of second-tier enzyme testing.

  The Journal of pediatrics 20101001

• Functional expression of carnitine/organic cation transporter OCTN1/SLC22A4 in mouse small intestine and liver.

  Drug metabolism and disposition: the biological fate of chemicals 20101001

• Metabolomic profiles indicate distinct physiological pathways affected by two loci with major divergent effect on Bos taurus growth and lipid deposition.

  Physiological genomics 20101001

• Progression of cyclophosphamide-induced acute renal metabolic damage in carnitine-depleted rat model.

  Clinical and experimental nephrology 20101001

• Postprandial changes of amino acid and acylcarnitine concentrations in dried blood samples.

  Journal of inherited metabolic disease 20101001

• How to use acylcarnitine profiles to help diagnose inborn errors of metabolism.

  Archives of disease in childhood. Education and practice edition 20101001

• Effects of L-carnitine supplement on serum inflammatory cytokines, C-reactive protein, lipoprotein (a), and oxidative stress in hemodialysis patients with Lp (a) hyperlipoproteinemia.

  Hemodialysis international. International Symposium on Home Hemodialysis 20101001

• Cisplatin-induced downregulation of OCTN2 affects carnitine wasting.

  Clinical cancer research : an official journal of the American Association for Cancer Research 20101001

• Rehabilitative treatment in peripheral artery disease: protocol application and follow-up.

  Minerva cardioangiologica 20101001

• [Use of L-carnitine before percutaneous epididymal sperm aspiration-intracytoplasmic sperm injection for obstructive azoospermia].

  Zhonghua nan ke xue = National journal of andrology 20101001

• State of the art in muscle lipid diseases.

  Acta myologica : myopathies and cardiomyopathies : official journal of the Mediterranean Society of Myology 20101001

• Prevention by L-carnitine of DNA damage induced by propionic and L-methylmalonic acids in human peripheral leukocytes in vitro.

  Mutation research 20100930

• Laser desorption ionization mass spectrometry on silicon nanowell arrays.

  Analytical chemistry 20100915

• Analysis of amprolium by hydrophilic interaction liquid chromatography-tandem mass spectrometry.

  Journal of chromatography. A 20100910

• Structural basis of Na(+)-independent and cooperative substrate/product antiport in CaiT.

  Nature 20100909

• Effect of dietary ascorbate on lipogenesis and lipolysis activities in black sea bream, Acanthopagrus schlegelii.

  Fish physiology and biochemistry 20100901

• Increased levels of plasma acylcarnitines in obesity and type 2 diabetes and identification of a marker of glucolipotoxicity.

  Obesity (Silver Spring, Md.) 20100901

• Oxidative stress in erythrocytes: a study on the effect of antioxidant mixtures during intermittent exposures to high altitude.

  International journal of biometeorology 20100901

• OCTN2 is associated with carnitine transport capacity of rat skeletal muscles.

  Acta physiologica (Oxford, England) 20100901

• L-carnitine is essential to beta-oxidation of quarried fatty acid from mitochondrial membrane by PLA(2).

  Molecular and cellular biochemistry 20100901

• Metabolic profiling of muscle contraction in lean compared with obese rodents.

  American journal of physiology. Regulatory, integrative and comparative physiology 20100901

• Carnitine palmitoyltransferase 2: New insights on the substrate specificity and implications for acylcarnitine profiling.

  Biochimica et biophysica acta 20100901

• Rapid determination of C4-acylcarnitine and C5-acylcarnitine isomers in plasma and dried blood spots by UPLC-MS/MS as a second tier test following flow-injection MS/MS acylcarnitine profile analysis.

  Molecular genetics and metabolism 20100901

• Synthesis and biological evaluation of cyclic nitrogen mustards based on carnitine framework.

  European journal of medicinal chemistry 20100901

• Elevated neonatal 3-OH isovalerylcarnitine due to breast milk sources in maternal 3-MCC deficiency.

  Molecular genetics and metabolism 20100901

• Current and emerging strategies for treating hepatic encephalopathy.

  Critical care nursing clinics of North America 20100901

• A new twist in cellular resistance to the anticancer drug bleomycin-A5.

  Current drug metabolism 20100901

• [Treatment with carnitine, acetyl carnitine, L-arginine and ginseng improves sperm motility and sexual health in men with asthenopermia].

  Minerva urologica e nefrologica = The Italian journal of urology and nephrology 20100901

• Failure of carnitine in improving hepatic nitrogen content in alcoholic and non-alcoholic malnourished rats.

  Clinics (Sao Paulo, Brazil) 20100901

• Malonylcarnitine in newborns with non-syndromic cleft lip with or without cleft palate.

  International journal of oral science 20100901

• Testing the blood of autistic children for ammonia.

  Alternative medicine review : a journal of clinical therapeutic 20100901

• [The 'big heart' of carnitine].

  Giornale italiano di cardiologia (2006) 20100901

• Effects of acylcarnitines on efflux transporting system in Caco-2 cell monolayers.

  European journal of drug metabolism and pharmacokinetics 20100901

• Colon OCTN2 gene expression is up-regulated by peroxisome proliferator-activated receptor gamma in humans and mice and contributes to local and systemic carnitine homeostasis.

  The Journal of biological chemistry 20100827

• Inhibition of gene expression of heart fatty acid binding protein and organic cation/carnitine transporter in doxorubicin cardiomyopathic rat model.

  European journal of pharmacology 20100825

• Diagnosis, treatment, and long-term outcomes of late-onset (type III) multiple acyl-CoA dehydrogenase deficiency.

  Journal of child neurology 20100801

• l-Carnitine l-tartrate supplementation favorably affects biochemical markers of recovery from physical exertion in middle-aged men and women.

  Metabolism: clinical and experimental 20100801

• L-carnitine modulates blood platelet oxidative stress.

  Cell biology and toxicology 20100801

• Cardiac conduction improvement in two heterozygotes for primary carnitine deficiency on L-carnitine supplementation.

  Clinical genetics 20100801

• Renal tissue damage after experimental pyelonephritis: role of antioxidants and selective cyclooxygenase-2 inhibitors.

  Urology 20100801

• Molecular spectrum of SLC22A5 (OCTN2) gene mutations detected in 143 subjects evaluated for systemic carnitine deficiency.

  Human mutation 20100801

• Detection of pivaloylcarnitine in pediatric patients with hypocarnitinemia after long-term administration of pivalate-containing antibiotics.

  The Tohoku journal of experimental medicine 20100801

• Clinical and biochemical improvement of very long-chain acyl-CoA dehydrogenase deficiency in pregnancy.

  Journal of perinatology : official journal of the California Perinatal Association 20100801

• Carnitine reduces the lipoperoxidative damage of the membrane and apoptosis after induction of cell stress in experimental glaucoma.

  Cell death & disease 20100801

• L-Carnitine attenuates angiotensin II-induced proliferation of cardiac fibroblasts: role of NADPH oxidase inhibition and decreased sphingosine-1-phosphate generation.

  The Journal of nutritional biochemistry 20100701

• Mechanistic contribution of carnitine deficiency to geriatric frailty.

  Ageing research reviews 20100701

• Allelic diversity in MCAD deficiency: the biochemical classification of 54 variants identified during 5 years of ACADM sequencing.

  Molecular genetics and metabolism 20100701

• [Infant coma in the emergency department: 2 cases of MCAD deficiency].

  Archives de pediatrie : organe officiel de la Societe francaise de pediatrie 20100701

• Muscle insulin resistance: assault by lipids, cytokines and local macrophages.

  Current opinion in clinical nutrition and metabolic care 20100701

• Determination of carnitine in food and food supplements by capillary electrophoresis with contactless conductivity detection.

  Electrophoresis 20100701

• Carnitine palmitoyltransferase 2 deficiency: the time-course of blood and urinary acylcarnitine levels during initial L-carnitine supplementation.

  The Tohoku journal of experimental medicine 20100701

• Effects of in ovo injection of L-carnitine on hatchability and subsequent broiler performance and slaughter yield.

  Poultry science 20100701

• Pharmacological preconditioning with L-carnitine: relevance to myocardial hemodynamic function and glycogen and lactate content.

  Pakistan journal of pharmaceutical sciences 20100701

• Acetyl-L-carnitine improves aged brain function.

  Geriatrics & gerontology international 20100701

• Nutritional treatments for acute myocardial infarction.

  Alternative medicine review : a journal of clinical therapeutic 20100701

• Heat stress deteriorates mitochondrial beta-oxidation of long-chain fatty acids in cultured fibroblasts with fatty acid beta-oxidation disorders.

  Journal of chromatography. B, Analytical technologies in the biomedical and life sciences 20100615

• In vitro probe acylcarnitine profiling assay using cultured fibroblasts and electrospray ionization tandem mass spectrometry predicts severity of patients with glutaric aciduria type 2.

  Journal of chromatography. B, Analytical technologies in the biomedical and life sciences 20100615

• Mitochondrial respiration in subcutaneous and visceral adipose tissue from patients with morbid obesity.

  The Journal of physiology 20100615

• The plasma carnitine concentration regulates renal OCTN2 expression and carnitine transport in rats.

  European journal of pharmacology 20100610

• Comparison of the effects of L: -carnitine and alpha-tocopherol on acute ureteral obstruction-induced renal oxidative imbalance and altered energy metabolism in rats.

  Urological research 20100601

• L-carnitine supplementation to diet: a new tool in treatment of nonalcoholic steatohepatitis--a randomized and controlled clinical trial.

  The American journal of gastroenterology 20100601

• Valproate-induced hyperammonemic encephalopathy, rapidly improved by i.v. carnitine and glucose/thiamine.

  Scandinavian journal of gastroenterology 20100601

• New SUCLG1 patients expanding the phenotypic spectrum of this rare cause of mild methylmalonic aciduria.

  Mitochondrion 20100601

• The therapeutic prospects of using L-carnitine to manage hypertension-related organ damage.

  Drug discovery today 20100601

• Elevated hydroxyacylcarnitines in a carrier of LCHAD deficiency during acute liver disease of pregnancy - a common feature of the pregnancy complication?

  Molecular genetics and metabolism 20100601

• Relationship of octanoylcarnitine concentrations to age at sampling in unaffected newborns screened for medium-chain acyl-CoA dehydrogenase deficiency.

  Clinical chemistry 20100601

• Metabolic oxidation regulates embryonic stem cell differentiation.

  Nature chemical biology 20100601

• Pre-exercise medium-chain triglyceride application prevents acylcarnitine accumulation in skeletal muscle from very-long-chain acyl-CoA-dehydrogenase-deficient mice.

  Journal of inherited metabolic disease 20100601

• Systemic antioxidant properties of L-carnitine in two different models of arterial hypertension.

  Journal of physiology and biochemistry 20100601

• Checks before bolus epidural injection.

  Anaesthesia 20100601

• Effects of carnitine on peripheral blood mitochondrial DNA copy number and liver function in non-alcoholic fatty liver disease.

  The Korean journal of gastroenterology = Taehan Sohwagi Hakhoe chi 20100601

• Liquid chromatography-tandem mass spectrometry for analysis of acylcarnitines in dried blood specimens collected at autopsy from neonatal intensive care unit.

  Chinese medical sciences journal = Chung-kuo i hsueh k'o hsueh tsa chih 20100601

• Newborn screening for methylmalonic aciduria by tandem mass spectrometry: 7 years' experience from two centers in Taiwan.

  Journal of the Chinese Medical Association : JCMA 20100601

• [Expressions of sperm-specific genes in carnitine-cultured testis sperm of obstructive azoospermia patients].

  Zhonghua nan ke xue = National journal of andrology 20100601

• Quantitative measurement of plasma 3-hydroxyisovaleryl carnitine by LC-MS/MS as a novel biomarker of biotin status in humans.

  Analytical chemistry 20100515

• Aminocarnitine ureidic derivatives as inhibitors of carnitine palmitoyltransferase I.

  ChemMedChem 20100503

• Comparison of amino acids and acylcarnitines assay methods used in newborn screening assays by tandem mass spectrometry.

  Clinica chimica acta; international journal of clinical chemistry 20100502

• Effect of heat stress and bezafibrate on mitochondrial beta-oxidation: comparison between cultured cells from normal and mitochondrial fatty acid oxidation disorder children using in vitro probe acylcarnitine profiling assay.

  Brain & development 20100501

• Stabilization of blood methylmalonic acid level in methylmalonic acidemia after liver transplantation.

  Pediatric transplantation 20100501

• Identification of a neonate with hepatorenal tyrosinemia by combined routine newborn screening for succinylacetone, acylcarnitines and amino acids.

  Clinical biochemistry 20100501

• Increased mitochondrial content rescues in vivo muscle oxidative capacity in long-term high-fat-diet-fed rats.

  FASEB journal : official publication of the Federation of American Societies for Experimental Biology 20100501

• Diagnoses of newborns and mothers with carnitine uptake defects through newborn screening.

  Molecular genetics and metabolism 20100501

• Expression of OCTN2 and OCTN3 in the apical membrane of rat renal cortex and medulla.

  Journal of cellular physiology 20100501

• High affinity carnitine transporters from OCTN family in neural cells.

  Neurochemical research 20100501

• Carnitine supplementation has protective and detrimental effects in Saccharomyces cerevisiae that are genetically mediated.

  FEMS yeast research 20100501

• Enzymology of the carnitine biosynthesis pathway.

  IUBMB life 20100501

• Stevia rebaudiana Bertoni extract supplementation improves lipid and carnitine profiles in C57BL/6J mice fed a high-fat diet.

  Journal of the science of food and agriculture 20100501

• Inspiratory muscle strength is correlated with carnitine levels in type 2 diabetes.

  Endocrine research 20100501

• The role of oral L-carnitine therapy in chronic hemodialysis patients.

  Saudi journal of kidney diseases and transplantation : an official publication of the Saudi Center for Organ Transplantation, Saudi Arabia 20100501

• Iron chelation therapy in Upper Egyptian transfusion-dependent pediatric homozygous beta-thalassemia major: impact on serum L-carnitine/free fatty acids, osteoprotegerin/the soluble receptor activator of nuclear factor-kappabeta ligand systems, and bone mineral density.

  Journal of pediatric hematology/oncology 20100501

• Integration of metabolomics and transcriptomics data to aid biomarker discovery in type 2 diabetes.

  Molecular bioSystems 20100501

• [L-carnitine: safe and effective for asthenozoospermia].

  Zhonghua nan ke xue = National journal of andrology 20100501

• Effect of carnitine supplementation on mitochondrial enzymes in liver and skeletal muscle of rat after dietary lipid manipulation and physical activity.

  Indian journal of experimental biology 20100501

• Comparative effects of captopril and l-carnitine on blood pressure and antioxidant enzyme gene expression in the heart of spontaneously hypertensive rats.

  European journal of pharmacology 20100425

• L-carnitine attenuates oxidant injury in HK-2 cells via ROS-mitochondria pathway.

  Regulatory peptides 20100409

• The significance of microsurgical varicocelectomy in the treatment of subclinical varicocele.

  Fertility and sterility 20100401

• Effects of exercise on L-carnitine and lipid metabolism in African catfish (Clarias gariepinus) fed different dietary L-carnitine and lipid levels.

  The British journal of nutrition 20100401

• Neuroprotective effects of L-carnitine in a transgenic animal model of Huntington's disease.

  Biomedicine & pharmacotherapy = Biomedecine & pharmacotherapie 20100401

• L-carnitine attenuates cardiac remodelling rather than vascular remodelling in deoxycorticosterone acetate-salt hypertensive rats.

  Basic & clinical pharmacology & toxicology 20100401

• Reduction of lipid and protein damage in patients with disorders of propionate metabolism under treatment: a possible protective role of L-carnitine supplementation.

  International journal of developmental neuroscience : the official journal of the International Society for Developmental Neuroscience 20100401

• LMNA mutations, skeletal muscle lipid metabolism, and insulin resistance.

  The Journal of clinical endocrinology and metabolism 20100401

• Differential metabolomics for quantitative assessment of oxidative stress with strenuous exercise and nutritional intervention: thiol-specific regulation of cellular metabolism with N-acetyl-L-cysteine pretreatment.

  Analytical chemistry 20100401

• Vincristine-induced peripheral neuropathy in a neonate with congenital acute lymphoblastic leukemia.

  Journal of pediatric hematology/oncology 20100401

• Quantitative analysis of the dynamic signaling pathway involved in the cAMP mediated induction of l-carnitine biosynthesis in E. coli cultures.

  Molecular bioSystems 20100401

• Altered brain phospholipid and acylcarnitine profiles in propionic acid infused rodents: further development of a potential model of autism spectrum disorders.

  Journal of neurochemistry 20100401

• Outpatient treatment of propionic acidemia-associated hyperammonemia with N-carbamoyl-L-glutamate in an infant.

  Clinical therapeutics 20100401

• Effect of L-carnitine on proliferative response and mRNA expression of some of its associated factors in splenic mononuclear cells of male broiler chicks.

  Animal science journal = Nihon chikusan Gakkaiho 20100401

• Antiapoptotic effect of L-carnitine on testicular irradiation in rats.

  Journal of molecular histology 20100401

• Dilated cardiomyopathy in epidermolysis bullosa.

  Dermatologic clinics 20100401

• Effect of various carbohydrate-electrolyte fluids on cycling performance and maximal voluntary contraction.

  International journal of sport nutrition and exercise metabolism 20100401

• Randomised phase III clinical trial of 5 different arms of treatment on 332 patients with cancer cachexia.

  European review for medical and pharmacological sciences 20100401

• L-carnitine-supplemented parenteral nutrition improves fat metabolism but fails to support compensatory growth in premature Korean infants.

  Nutrition research (New York, N.Y.) 20100401

• A diet supplemented with L-carnitine improves the sperm quality of Piétrain but not of Duroc and Large White boars when photoperiod and temperature increase.

  Theriogenology 20100315

• Structural and functional characterization of plant aminoaldehyde dehydrogenase from Pisum sativum with a broad specificity for natural and synthetic aminoaldehydes.

  Journal of molecular biology 20100305

• SIRT3 regulates mitochondrial fatty-acid oxidation by reversible enzyme deacetylation.

  Nature 20100304

• Carnitine protects the intestine against reperfusion injury in rats.

  The Journal of surgical research 20100301

• [Multiple acyl-CoA dehydrogenase deficiency (MADD): a curable cause of genetic muscular lipidosis].

  Revue neurologique 20100301

• L-carnitine supplementation and EPO requirement in children on chronic hemodialysis.

  Pediatric nephrology (Berlin, Germany) 20100301

• Inhibition of hepatic carnitine palmitoyl-transferase I (CPT IA) by valproyl-CoA as a possible mechanism of valproate-induced steatosis.

  Biochemical pharmacology 20100301

• Flavin adenine dinucleotide status and the effects of high-dose riboflavin treatment in short-chain acyl-CoA dehydrogenase deficiency.

  Pediatric research 20100301

• Intramuscular triacylglycerol and insulin resistance: guilty as charged or wrongly accused?

  Biochimica et biophysica acta 20100301

• Lack of genotype-phenotype correlations and outcome in MCAD deficiency diagnosed by newborn screening in New York State.

  Molecular genetics and metabolism 20100301

• Propionyl-L-carnitine improves postischemic blood flow recovery and arteriogenetic revascularization and reduces endothelial NADPH-oxidase 4-mediated superoxide production.

  Arteriosclerosis, thrombosis, and vascular biology 20100301

• Preeclampsia and HELLP syndrome: impaired mitochondrial function in umbilical endothelial cells.

  Reproductive sciences (Thousand Oaks, Calif.) 20100301

• L-carnitine and taurine synergistically inhibit the proliferation and osteoblastic differentiation of vascular smooth muscle cells.

  Acta pharmacologica Sinica 20100301

• Serum carnitine levels in childhood leukemia.

  Journal of pediatric hematology/oncology 20100301

• The role of peroxisome proliferator-activated receptor alpha in transcriptional regulation of novel organic cation transporters.

  European journal of pharmacology 20100225

• L-carnitine in beta thalassemia.

  Indian pediatrics 20100201

• Urinary excretion of carnitine as a marker of proximal tubular damage associated with platin-based antineoplastic drugs.

  Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20100201

• Muscle carnitine deficiency: adult onset lipid storage myopathy with sensory neuropathy.

  Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology 20100201

• Newborn screening and early biochemical follow-up in combined methylmalonic aciduria and homocystinuria, cblC type, and utility of methionine as a secondary screening analyte.

  Molecular genetics and metabolism 20100201

• Lipid resuscitation in a carnitine deficient child following intravascular migration of an epidural catheter.

  Anaesthesia 20100201

• Organic cation/carnitine transporter, OCTN2, transcriptional activity is regulated by osmotic stress in epididymal cells.

  Molecular reproduction and development 20100201

• Oral carnitine therapy and insulin resistance.

  Hypertension (Dallas, Tex. : 1979) 20100201

• Study of inborn errors of metabolism in urine from patients with unexplained mental retardation.

  Journal of inherited metabolic disease 20100201

• Effects of in ovo injection of L-carnitine on subsequent broiler chick tissue nutrient profiles.

  Poultry science 20100201

• Randomized phase III clinical trial of five different arms of treatment in 332 patients with cancer cachexia.

  The oncologist 20100201

• Effects of in ovo administration of L-carnitine on hatchability performance, glycogen status and insulin-like growth factor-1 of broiler chickens.

  British poultry science 20100201

• [Clinical efficacy of intravenous L-carnitine in patients with right-sided heart failure induced by pulmonary arterial hypertension].

  Zhonghua xin xue guan bing za zhi 20100201

• [The supplementation of L-carnitine does not promote alterations in the resting metabolic rate and in the use of energetic substrates in physically active individuals].

  Arquivos brasileiros de endocrinologia e metabologia 20100201

• Achiral liquid chromatography with circular dichroism detection for the determination of carnitine enantiomers in dietary supplements and pharmaceutical formulations.

  Journal of pharmaceutical and biomedical analysis 20100120

• The effect of dietary supplementation with calcium salts of long chain fatty acids and/or L-carnitine on ovarian activity of Rahmani ewes.

  Animal reproduction science 20100101

• Involvement of OCTN2 in the transport of acetyl-L-carnitine across the inner blood-retinal barrier.

  Investigative ophthalmology & visual science 20100101

• Acylcarnitines: role in brain.

  Progress in lipid research 20100101

• Increased urinary losses of carnitine and decreased intramitochondrial coenzyme A in gentamicin-induced acute renal failure in rats.

  Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20100101

• Effect of combination therapy of hydroxyurea with l-carnitine and magnesium chloride on hematologic parameters and cardiac function of patients with beta-thalassemia intermedia.

  European journal of haematology 20100101

• Cardiomyopathies in propionic aciduria are reversible after liver transplantation.

  The Journal of pediatrics 20100101

• The ATP-binding cassette transporter Cbc (choline/betaine/carnitine) recruits multiple substrate-binding proteins with strong specificity for distinct quaternary ammonium compounds.

  Molecular microbiology 20100101

• [Late onset 3-HMG-CoA lyase deficiency: a rare but treatable disorder].

  Archives de pediatrie : organe officiel de la Societe francaise de pediatrie 20100101

• The antioxidant properties of carnitine in vitro.

  Cellular & molecular biology letters 20100101

• Maternal systemic primary carnitine deficiency uncovered by newborn screening: clinical, biochemical, and molecular aspects.

  Genetics in medicine : official journal of the American College of Medical Genetics 20100101

• Acylcarnitine analysis by tandem mass spectrometry.

  Current protocols in human genetics 20100101

• Cardiac and plasma lipid profiles in response to acute hypoxia in neonatal and young adult rats.

  Lipids in health and disease 20100101

• Measurement of plasma/serum acylcarnitines using tandem mass spectrometry.

  Methods in molecular biology (Clifton, N.J.) 20100101

• Compliance to clinical guidelines determines outcome in glutaric aciduria type I in the era of newborn screening.

  Klinische Padiatrie 20100101

• Mitochondrial fatty acid oxidation and oxidative stress: lack of reverse electron transfer-associated production of reactive oxygen species.

  Biochimica et biophysica acta 20100101

• Macronutrient composition and increased physical activity modulate plasma adipokines and appetite hormones during a weight loss intervention.

  Journal of women's health (2002) 20100101

• Clinical outcomes and low-dose levocarnitine supplementation in psychiatric inpatients with documented hypocarnitinemia: a retrospective chart review.

  Journal of psychiatric practice 20100101

• [Toward a more rational field-genetic epidemiology].

  Nihon eiseigaku zasshi. Japanese journal of hygiene 20100101

• Fatty acid-bearing albumin induces VCAM-1 expression through c-Src kinase-AP-1/NF-kB pathways: effect of L-carnitine.

  Kidney & blood pressure research 20100101

• The effects of L-carnitine therapy on respiratory function tests in chronic hemodialysis patients.

  Renal failure 20100101

• Metabolomic analyses of plasma reveals new insights into asphyxia and resuscitation in pigs.

  PloS one 20100101

• Carnitine deficiency aggravates cyclophosphamide-induced cardiotoxicity in rats.

  Chemotherapy 20100101

• Identification of a novel organic anion transporter mediating carnitine transport in mouse liver and kidney.

  Cellular physiology and biochemistry : international journal of experimental cellular physiology, biochemistry, and pharmacology 20100101

• Site-directed mutagenesis of charged amino acids of the human mitochondrial carnitine/acylcarnitine carrier: insight into the molecular mechanism of transport.

  Biochimica et biophysica acta 20100101

• [Pharmacokinetics of biological tags in a case of acute valpromide self poisoning].

  Annales de biologie clinique 20100101

• Low availability of carnitine precursors as a possible reason for the diminished plasma carnitine concentrations in pregnant women.

  BMC pregnancy and childbirth 20100101

• Increased urinary excretion of carnitine and acylcarnitine by mercuric chloride is reversed by 2,3-dimercapto-1-propanesulfonic acid in rats.

  International journal of toxicology 20100101

• Caloric restriction and L-carnitine administration improves insulin sensitivity in patients with impaired glucose metabolism.

  JPEN. Journal of parenteral and enteral nutrition 20100101

• Simultaneous determination of free and total carnitine in human serum by HPLC with UV detection.

  Journal of chromatographic science 20100101

• Oxidative stress in response to forearm ischemia-reperfusion with and without carnitine administration.

  International journal for vitamin and nutrition research. Internationale Zeitschrift fur Vitamin- und Ernahrungsforschung. Journal international de vitaminologie et de nutrition 20100101

• Enhancement of shortening velocity, power, and acto-myosin crossbridge (CB) kinetics following long-term treatment with propionyl-L-carnitine, coenzyme Q10, and omega-3 fatty acids in BIO TO-2 cardiomyopathic Syrian hamsters papillary muscle.

  BioFactors (Oxford, England) 20100101

• L-carnitine for acute valproic acid overdose: a systematic review of published cases.

  The Annals of pharmacotherapy 20100101

• Dilated cardiomyopathy in epidermolysis bullosa: a retrospective, multicenter study.

  Pediatric dermatology 20100101

• Medium chain acylcarnitines dominate the metabolite pattern in humans under moderate intensity exercise and support lipid oxidation.

  PloS one 20100101

• ESI-MS/MS measurement of free carnitine and its precursor γ-butyrobetaine in plasma and dried blood spots from patients with organic acidurias and fatty acid oxidation disorders.

  Molecular genetics and metabolism 20100101

• L-carnitine treatment in patients with mild diastolic heart failure is associated with improvement in diastolic function and symptoms.

  Cardiology 20100101

• Equine acquired multiple acyl-CoA dehydrogenase deficiency (MADD) in 14 horses associated with ingestion of Maple leaves (Acer pseudoplatanus) covered with European tar spot (Rhytisma acerinum).

  Molecular genetics and metabolism 20100101

• Orlistat and L-carnitine compared to orlistat alone on insulin resistance in obese diabetic patients.

  Endocrine journal 20100101

• [Relationships between endogenous carnitine content and growth as carcass traits in swine].

  Berliner und Munchener tierarztliche Wochenschrift 20100101

• Sibutramine and L-carnitine compared to sibutramine alone on insulin resistance in diabetic patients.

  Internal medicine (Tokyo, Japan) 20100101

• SMA CARNI-VAL trial part I: double-blind, randomized, placebo-controlled trial of L-carnitine and valproic acid in spinal muscular atrophy.

  PloS one 20100101

• L-carnitine decreases oxidative stress induced by experimental hypobaric hypoxia.

  Pediatric endocrinology, diabetes, and metabolism 20100101

• Safety and efficacy of clomiphene citrate and L-carnitine in idiopathic male infertility: a comparative study.

  Urology journal 20100101

• Effects of L-Carnitine supplement on plasma coagulation and anticoagulation factors in hemodialysis patients.

  Renal failure 20100101

• A novel mutation of the ACADM gene (c.145C>G) associated with the common c.985A>G mutation on the other ACADM allele causes mild MCAD deficiency: a case report.

  Orphanet journal of rare diseases 20100101

• Comparison of protective effects of L-carnitine and amifostine on radiation-induced toxicity to growing bone: histopathology and scintigraphy findings.

  Asian Pacific journal of cancer prevention : APJCP 20100101

• Preliminary study comparing the effects of locally and systemically applied L-carnitine on the healing of full-thickness skin defects.

  Scandinavian journal of surgery : SJS : official organ for the Finnish Surgical Society and the Scandinavian Surgical Society 20100101

• Transport of L-carnitine in human corneal and conjunctival epithelial cells.

  Molecular vision 20100101

• Setting up an emergency stock for metabolic diseases.

  La Clinica terapeutica 20100101

• L-carnitine pre-treatment reduces apoptotic cell death in seven-day-old rats hypoxia ischemia.

  Restorative neurology and neuroscience 20100101

• Analytical sciences.

  Chimia 20100101

• Just in the nick of time: targeting acute versus chronic disease.

  Oxidative medicine and cellular longevity 20100101

• Dilated cardiomyopathy in celiac disease: role of carnitine deficiency.

  Acta gastro-enterologica Belgica 20100101

• Doxorubicin toxicity can be ameliorated during antioxidant L-carnitine supplementation.

  Oxidative medicine and cellular longevity 20100101

• Tissue-specific short chain fatty acid metabolism and slow metabolic recovery after ischemia from hyperpolarized NMR in vivo.

  The Journal of biological chemistry 20091225

• Relationship between plasma free fatty acid, intramyocellular triglycerides and long-chain acylcarnitines in resting humans.

  The Journal of physiology 20091215

• Plasma carnitine ester profile in homozygous and heterozygous OCTN2 deficiency.

  Journal of inherited metabolic disease 20091201

• Positive newborn screen in the biochemically normal infant of a mother with treated holocarboxylase synthetase deficiency.

  Journal of inherited metabolic disease 20091201

• Effects of selenium and L-carnitine on oxidative stress in blood of rat induced by 2.45-GHz radiation from wireless devices.

  Biological trace element research 20091201

• Effects of long-term mildronate treatment on cardiac and liver functions in rats.

  Basic & clinical pharmacology & toxicology 20091201

• Plasma carnitine ester profiles in Crohn's disease and ulcerative colitis patients with different IGR2230a_1 genotypes.

  International journal of immunogenetics 20091201

• Organic cation/carnitine transporter OCTN3 is present in astrocytes and is up-regulated by peroxisome proliferators-activator receptor agonist.

  The international journal of biochemistry & cell biology 20091201

• Impact of experimental diabetes and insulin replacement on epididymal secretory products and sperm maturation in albino rats.

  Journal of cellular biochemistry 20091201

• Substrate discrimination by ergothioneine transporter SLC22A4 and carnitine transporter SLC22A5: gain-of-function by interchange of selected amino acids.

  Biochimica et biophysica acta 20091201

• Asymptomatic maternal combined homocystinuria and methylmalonic aciduria (cblC) detected through low carnitine levels on newborn screening.

  The Journal of pediatrics 20091201

• BJSM reviews: A-Z of nutritional supplements: dietary supplements, sports nutrition foods and ergogenic aids for health and performance Part 4.

  British journal of sports medicine 20091201

• False-positive newborn screening mimicking glutaric aciduria type I in infants with renal insufficiency.

  Journal of inherited metabolic disease 20091201

• [Protective effect of L-carnitine on the testis and epididymis against ornidazole-induced injury in male rats].

  Zhonghua nan ke xue = National journal of andrology 20091201

• Hypoketotic hypoglycemia with myolysis and hypoparathyroidism: an unusual association in medium chain acyl-CoA desydrogenase deficiency (MCADD).

  Journal of pediatric endocrinology & metabolism : JPEM 20091201

• Carnitine, mitochondrial function and therapy.

  Advanced drug delivery reviews 20091130

• Carnitine synthesis and uptake into cells are stimulated by fasting in pigs as a model of nonproliferating species.

  The Journal of nutritional biochemistry 20091101

• A case of holocarboxylase synthetase deficiency with insufficient response to prenatal biotin therapy.

  Brain & development 20091101

• Effect of L-carnitine on the size of low-density lipoprotein particles in type 2 diabetes mellitus patients treated with simvastatin.

  Metabolism: clinical and experimental 20091101

• Temperature-dependent specific transport of levofloxacin in human intestinal epithelial LS180 cells.

  Biopharmaceutics & drug disposition 20091101

• Failure of the feeding response to fasting in carnitine-deficient juvenile visceral steatosis (JVS) mice: involvement of defective acyl-ghrelin secretion and enhanced corticotropin-releasing factor signaling in the hypothalamus.

  Biochimica et biophysica acta 20091101

• Variation in the human lipidome associated with coffee consumption as revealed by quantitative targeted metabolomics.

  Molecular nutrition & food research 20091101

• Propionyl l-carnitine: intermittent claudication and peripheral arterial disease.

  Expert opinion on pharmacotherapy 20091101

• Carnitine in parenteral nutrition.

  Gastroenterology 20091101

• [The role of apoptosis and protective effect of carnitine in contralateral testicular injury in experimental unilateral testicular torsion].

  Ulusal travma ve acil cerrahi dergisi = Turkish journal of trauma & emergency surgery : TJTES 20091101

• Involvement of L-carnitine in cellular metabolism: beyond Acyl-CoA transport.

  Mini reviews in medicinal chemistry 20091101

• Statins, fibrates and retinoic acid upregulate mitochondrial acylcarnitine carrier gene expression.

  Biochemical and biophysical research communications 20091030

• Peroxisome proliferator-activated receptor alpha plays a crucial role in L-carnitine anti-apoptosis effect in renal tubular cells.

  Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20091001

• Oral supplementation of propionyl-l-carnitine reduces body weight and hyperinsulinaemia in obese Zucker rats.

  The British journal of nutrition 20091001

• Hepatic uptake of gamma-butyrobetaine, a precursor of carnitine biosynthesis, in rats.

  American journal of physiology. Gastrointestinal and liver physiology 20091001

• Nutrient deficiencies in the premature infant.

  Pediatric clinics of North America 20091001

• [Advances in the study of regulation of novel organic cation transporter-2].

  Yao xue xue bao = Acta pharmaceutica Sinica 20091001

• Searching for the needle in the Haystacks.

  Lancet (London, England) 20090905

• The risk of asymptomatic hyperammonemia in children with idiopathic epilepsy treated with valproate: relationship to blood carnitine status.

  Epilepsy research 20090901

• Fatty acid oxidation and meiotic resumption in mouse oocytes.

  Molecular reproduction and development 20090901

• Enzymatic evaluation of glutaric acidemia type 1 by an in vitro probe assay of acylcarnitine profiling using fibroblasts and electrospray ionization/tandem mass spectrometry (MS/MS).

  Journal of chromatography. B, Analytical technologies in the biomedical and life sciences 20090901

• Carnitine status of pregnant women: effect of carnitine supplementation and correlation between iron status and plasma carnitine concentration.

  European journal of clinical nutrition 20090901

• Relationships between circulating metabolic intermediates and insulin action in overweight to obese, inactive men and women.

  Diabetes care 20090901

• Influence of l-carnitine on metabolism and performance of sows.

  The British journal of nutrition 20090901

• Improved MS/MS analysis of succinylacetone extracted from dried blood spots when combined with amino acids and acylcarnitine butyl esters.

  Clinica chimica acta; international journal of clinical chemistry 20090901

• Human urinary metabolomic profile of PPARalpha induced fatty acid beta-oxidation.

  Journal of proteome research 20090901

• Effect of propionyl-L-carnitine, L-arginine and nicotinic acid on the efficacy of vardenafil in the treatment of erectile dysfunction in diabetes.

  Current medical research and opinion 20090901

• Influence of pharmacological PPARalpha activators on carnitine homeostasis in proliferating and non-proliferating species.

  Pharmacological research 20090901

• Carnitine and type 2 diabetes.

  Diabetes/metabolism research and reviews 20090901

• Effects of cryoprotectant treatments on bovine sperm function and osmolyte content.

  Asian journal of andrology 20090901

• A neonatal death due to medium-chain acyl-CoA dehydrogenase deficiency: utilization of the neonatal metabolic screen in a functional approach to sudden unexplained infant death.

  The American journal of forensic medicine and pathology 20090901

• Carnitine plasma levels and fatigue in children/adolescents receiving cisplatin, ifosfamide, or doxorubicin.

  Journal of pediatric hematology/oncology 20090901

• [Correlation between renal tubular dysfunction and serum carnitine deficiency in cases with valproate therapy].

  No to hattatsu = Brain and development 20090901

• Effect of dietary lipid, carnitine and exercise on lipid profile in rat blood, liver and muscle.

  Indian journal of experimental biology 20090901

• [D-2-hydroxyglutaric aciduria. Report of two cases].

  Investigacion clinica 20090901

• Effect of L-carnitine on postischemic inhibition of protein synthesis in the rat brain.

  General physiology and biophysics 20090901

• Comparison of vitamin E, L-carnitine and melatonin in ameliorating carbon tetrachloride and diabetes induced hepatic oxidative stress.

  Journal of physiology and biochemistry 20090901

• Carnitine conjugate of nipecotic acid: a new example of dual prodrug.

  Molecules (Basel, Switzerland) 20090831

• Carnitine insufficiency caused by aging and overnutrition compromises mitochondrial performance and metabolic control.

  The Journal of biological chemistry 20090821

• Interaction between pivaloylcarnitine and L-carnitine transport into L6 cells overexpressing hOCTN2.

  Chemico-biological interactions 20090814

• Corresponding increase in long-chain acyl-CoA and acylcarnitine after exercise in muscle from VLCAD mice.

  Journal of lipid research 20090801

• Role of L-carnitine in the prevention of seminiferous tubules damage induced by gamma radiation: a light and electron microscopic study.

  Archives of toxicology 20090801

• Site-directed mutagenesis of the His residues of the rat mitochondrial carnitine/acylcarnitine carrier: implications for the role of His-29 in the transport pathway.

  Biochimica et biophysica acta 20090801

• Identification and characterization of a complete carnitine biosynthesis pathway in Candida albicans.

  FASEB journal : official publication of the Federation of American Societies for Experimental Biology 20090801

• Deuterated palmitate-driven acylcarnitine formation by whole-blood samples for a rapid diagnostic exploration of mitochondrial fatty acid oxidation disorders.

  Clinica chimica acta; international journal of clinical chemistry 20090801

• Evidence for the participation of the stimulated sympathetic nervous system in the regulation of carnitine blood levels of soccer players during a game.

  Metabolism: clinical and experimental 20090801

• Carnitine reduces testicular damage in rats treated with etoposide in the prepubertal phase.

  Cell and tissue research 20090801

• Treatment recommendations in long-chain fatty acid oxidation defects: consensus from a workshop.

  Journal of inherited metabolic disease 20090801

• Mitochondrial long chain fatty acid beta-oxidation in man and mouse.

  Biochimica et biophysica acta 20090801

• Effect of carnitine on cutaneous wound healing in immunosuppressed rats.

  The Journal of surgical research 20090801

• Fluctuating liver functions in siblings with MPV17 mutations and possible improvement associated with dietary and pharmaceutical treatments targeting respiratory chain complex II.

  Molecular genetics and metabolism 20090801

• Pharmacological treatment of patients with chronic critical limb ischemia: L-propionyl-carnitine enhances the short-term effects of PGE-1.

  Cardiovascular drugs and therapy 20090801

• Early nerve ending rescue from oxidative damage and energy failure by L: -carnitine as post-treatment in two neurotoxic models in rat: recovery of antioxidant and reductive capacities.

  Experimental brain research 20090801

• Novel mutation of early, perinatal-onset, myopathic-type very-long-chain acyl-CoA dehydrogenase deficiency.

  Pediatric neurology 20090801

• Protective effects of mildronate in an experimental model of type 2 diabetes in Goto-Kakizaki rats.

  British journal of pharmacology 20090801

• Effects of simvastatin and carnitine versus simvastatin on lipoprotein(a) and apoprotein(a) in type 2 diabetes mellitus.

  Expert opinion on pharmacotherapy 20090801

• Modulator effects of L-carnitine and selenium on wireless devices (2.45 GHz)-induced oxidative stress and electroencephalography records in brain of rat.

  International journal of radiation biology 20090801

• Effect of triheptanoin on muscle metabolism during submaximal exercise in horses.

  American journal of veterinary research 20090801

• Electron transfer mediators and other metabolites and cofactors in the treatment of mitochondrial dysfunction.

  Nutrition reviews 20090801

• Dissection of biochemical borderline phenotypes in carriers and genetic variants of medium-chain acyl-CoA dehyrogenase deficiency: implications for newborn screening [corrected].

  Clinical genetics 20090801

• Determination of carnitine, its short chain acyl esters and metabolic precursors trimethyllysine and gamma-butyrobetaine by quasi-solid phase extraction and MS/MS detection.

  Journal of chromatography. B, Analytical technologies in the biomedical and life sciences 20090715

• [Protective effects of L-carnitine upon testicular ischemia-reperfusion damage in rats].

  Zhonghua yi xue za zhi 20090714

• Activities of gamma-butyrobetaine dioxygenase and concentrations of carnitine in tissues of pigs.

  Comparative biochemistry and physiology. Part A, Molecular & integrative physiology 20090701

• L-Carnitine supplementation during suckling intensifies the early postnatal skeletal myofiber formation in piglets of low birth weight.

  Journal of animal science 20090701

• Identification of genes required for Pseudomonas aeruginosa carnitine catabolism.

  Microbiology (Reading, England) 20090701

• 1H NMR to investigate metabolism and energy supply in rhesus macaque sperm.

  Reproductive toxicology (Elmsford, N.Y.) 20090701

• Longitudinal study of the effects of chronic hypothyroidism on skeletal muscle in dogs.

  American journal of veterinary research 20090701

• [L-carnitine improves the reproductive function of male rats with ornidazole-induced asthenospermia].

  Zhonghua nan ke xue = National journal of andrology 20090701

• Addition of formic acid improves acetonitrile extraction of dicarboxylic acylcarnitines.

  Clinica chimica acta; international journal of clinical chemistry 20090627

• Selective quantification of carnitine enantiomers using chiral cysteine-capped CdSe(ZnS) quantum dots.

  Analytical chemistry 20090615

• Rat serum carboxylesterase partly hydrolyses gamma-butyrobetaine esters.

  Arhiv za higijenu rada i toksikologiju 20090601

• Carnitine enhances the growth of Listeria monocytogenes in infant formula at 7 degrees C.

  Journal of food protection 20090601

• Inactivation by omeprazole of the carnitine transporter (OCTN2) reconstituted in liposomes.

  Chemico-biological interactions 20090515

• L-carnitine supplementation reduces oocyte cytoskeleton damage and embryo apoptosis induced by incubation in peritoneal fluid from patients with endometriosis.

  Fertility and sterility 20090501

• Cisplatin-induced kidney injury in the rat: L-carnitine modulates the relationship between MMP-9 and TIMP-3.

  Experimental and toxicologic pathology : official journal of the Gesellschaft fur Toxikologische Pathologie 20090501

• Carnitine/organic cation transporter OCTN2 (Slc22a5) is responsible for renal secretion of cephaloridine in mice.

  Drug metabolism and disposition: the biological fate of chemicals 20090501

• L-Carnitine in the lipid and protein protection against ethanol-induced oxidative stress.

  Alcohol (Fayetteville, N.Y.) 20090501

• Stability of acylcarnitines and free carnitine in dried blood samples: implications for retrospective diagnosis of inborn errors of metabolism and neonatal screening for carnitine transporter deficiency.

  Analytical chemistry 20090501

• Diagnostic assessment and long-term follow-up of 13 patients with Very Long-Chain Acyl-Coenzyme A dehydrogenase (VLCAD) deficiency.

  Neuromuscular disorders : NMD 20090501

• Pharmacological interventions for nonalcoholic fatty liver disease in adults and in children: a systematic review.

  Journal of pediatric gastroenterology and nutrition 20090501

• Histopathological and scintigraphic comparisons of the protective effects of L-carnitine and amifostine against radiation-induced late renal toxicity in rats.

  Clinical and experimental pharmacology & physiology 20090501

• Glycine propionyl-L-carnitine modulates lipid peroxidation and nitric oxide in human subjects.

  International journal for vitamin and nutrition research. Internationale Zeitschrift fur Vitamin- und Ernahrungsforschung. Journal international de vitaminologie et de nutrition 20090501

• Pharmacological analysis demonstrates dramatic alteration of D1 dopamine receptor neuronal distribution in the rat analog of L-DOPA-induced dyskinesia.

  The Journal of neuroscience : the official journal of the Society for Neuroscience 20090415

• Carnitine supplementation for inborn errors of metabolism.

  The Cochrane database of systematic reviews 20090415

• Metabolomic profiling reveals distinct patterns of myocardial substrate use in humans with coronary artery disease or left ventricular dysfunction during surgical ischemia/reperfusion.

  Circulation 20090407

• Metabolic profile changes in the testes of mice with streptozotocin-induced type 1 diabetes mellitus.

  International journal of andrology 20090401

• L-carnitine mediates protection against DNA damage in lymphocytes of aged rats.

  Biogerontology 20090401

• L-carnitine supplementation in patients with advanced cancer and carnitine deficiency: a double-blind, placebo-controlled study.

  Journal of pain and symptom management 20090401

• Muscle acylcarnitines during short-term fasting in lean healthy men.

  Clinical science (London, England : 1979) 20090401

• Quantification of malonylcarnitine in dried blood spots by use of MS/MS varies by stable isotope internal standard composition.

  Clinica chimica acta; international journal of clinical chemistry 20090401

• Identification and characterization of 3-iodothyronamine intracellular transport.

  Endocrinology 20090401

• Functional genetic variation in the basal promoter of the organic cation/carnitine transporters OCTN1 (SLC22A4) and OCTN2 (SLC22A5).

  The Journal of pharmacology and experimental therapeutics 20090401

• Ontogeny of Na(+)/L-carnitine transporter and of gamma-trimethylaminobutyraldehyde dehydrogenase and gamma-butyrobetaine hydroxylase genes expression in rat kidney.

  Mechanisms of ageing and development 20090401

• L-carnitine, a diet component and organic cation transporter OCTN ligand, displays immunosuppressive properties and abrogates intestinal inflammation.

  Clinical and experimental immunology 20090401

• Serum metabolomics reveals irreversible inhibition of fatty acid beta-oxidation through the suppression of PPARalpha activation as a contributing mechanism of acetaminophen-induced hepatotoxicity.

  Chemical research in toxicology 20090401

• Chemical form of dietary L-carnitine affects plasma but not tissue carnitine concentrations in male Sprague-Dawley rats.

  Journal of animal physiology and animal nutrition 20090401

• Increased plasma leptin through l-carnitine supplementation is associated with an enhanced glucose tolerance in healthy ponies.

  Journal of animal physiology and animal nutrition 20090401

• 3-Methylcrotonyl-CoA carboxylase deficiency: phenotypic variability in a family.

  Journal of child neurology 20090401

• L-carnitine, inflammation and hypertension.

  Nephrology (Carlton, Vic.) 20090401

• L-carnitine: a potential treatment for hyper-IgE syndrome.

  Giornale italiano di dermatologia e venereologia : organo ufficiale, Societa italiana di dermatologia e sifilografia 20090401

• Spondylocostal dysostosis associated with methylmalonic aciduria.

  Genetic testing and molecular biomarkers 20090401

• [Correlation of serum carnitine levels with age and sex among Chinese adults in Nanjing].

  Zhonghua nan ke xue = National journal of andrology 20090401

• [Peroxisome proliferator-activated receptor alpha and retinoid X receptor alpha expressions and intervention in alcoholic cardiomyopathy rats].

  Zhonghua xin xue guan bing za zhi 20090401

• Challenges and developments in tandem mass spectrometry based clinical metabolomics.

  Molecular and cellular endocrinology 20090325

• Progression of diethylnitrosamine-induced hepatic carcinogenesis in carnitine-depleted rats.

  World journal of gastroenterology 20090321

• Analysis of the hibernation cycle using LC-MS-based metabolomics in ground squirrel liver.

  Physiological genomics 20090303

• L-carnitine blood levels and oxidative stress in treated phenylketonuric patients.

  Cellular and molecular neurobiology 20090301

• Proteomic changes associated with diabetes in the BB-DP rat.

  American journal of physiology. Endocrinology and metabolism 20090301

• Endogenous plasma carnitine pool composition and response to erythropoietin treatment in chronic haemodialysis patients.

  Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20090301

• Influence of mitochondrial β-oxidation on early pea seedling development.

  The New phytologist 20090301

• Atypical presentation of VLCAD deficiency associated with a novel ACADVL splicing mutation.

  Muscle & nerve 20090301

• ETFDH mutations, CoQ10 levels, and respiratory chain activities in patients with riboflavin-responsive multiple acyl-CoA dehydrogenase deficiency.

  Neuromuscular disorders : NMD 20090301

• Phase II randomized study of Plitidepsin (Aplidin), alone or in association with L-carnitine, in patients with unresectable advanced renal cell carcinoma.

  Marine drugs 20090301

• Polymerization of cyclic esters initiated by carnitine and tin (II) octoate.

  Molecules (Basel, Switzerland) 20090204

• L-carnitine decreases DNA damage and improves the in vitro blastocyst development rate in mouse embryos.

  Fertility and sterility 20090201

• Induction of apoptosis by L-carnitine through regulation of two main pathways in Hepa1c1c 7 cells.

  Amino acids 20090201

• Carnitine deficiency: a possible risk factor in paracetamol hepatotoxicity.

  Archives of toxicology 20090201

• Cobalamin deficiency results in an abnormal increase in L-methylmalonyl-co-enzyme-A mutase expression in rat liver and COS-7 cells.

  The British journal of nutrition 20090201

• Metabolic profiling of PPARalpha-/- mice reveals defects in carnitine and amino acid homeostasis that are partially reversed by oral carnitine supplementation.

  FASEB journal : official publication of the Federation of American Societies for Experimental Biology 20090201

• The carnitine transporter SLC22A5 is not a general drug transporter, but it efficiently translocates mildronate.

  Drug metabolism and disposition: the biological fate of chemicals 20090201

• Changes of the plasma metabolome during an oral glucose tolerance test: is there more than glucose to look at?

  American journal of physiology. Endocrinology and metabolism 20090201

• Peroxisome proliferator-activated receptor alpha and enzymes of carnitine biosynthesis in the liver are down-regulated during lactation in rats.

  Metabolism: clinical and experimental 20090201

• L-carnitine and short chain ester in tears from patients with dry eye.

  Optometry and vision science : official publication of the American Academy of Optometry 20090201

• Serum total and free carnitine levels in children with asthma.

  World journal of pediatrics : WJP 20090201

• Comparison of pharmacokinetics of L-carnitine, acetyl-L-carnitine and propionyl-L-carnitine after single oral administration of L-carnitine in healthy volunteers.

  Clinical and investigative medicine. Medecine clinique et experimentale 20090201

• Bloodspot acylcarnitine and amino acid analysis in cord blood samples: efficacy and reference data from a large cohort study.

  Journal of inherited metabolic disease 20090201

• Supplementation of L-carnitine in pigs: absorption of carnitine and effect on plasma and tissue carnitine concentrations.

  Archives of animal nutrition 20090201

• Carnitine in the treatment of valproic acid-induced toxicity.

  Clinical toxicology (Philadelphia, Pa.) 20090201

• Comparative study of sesame lignans (sesamin, episesamin and sesamolin) affecting gene expression profile and fatty acid oxidation in rat liver.

  Journal of nutritional science and vitaminology 20090201

• Composition, disintegrative properties, and labeling compliance of commercially available taurine and carnitine dietary products.

  Journal of the American Veterinary Medical Association 20090115

• A moderate excess of dietary lysine lowers plasma and tissue carnitine concentrations in pigs.

  The British journal of nutrition 20090101

• Serum free L-carnitine in association with myoglobin as a diagnostic marker of acute myocardial infarction.

  Clinical biochemistry 20090101

• Neonatal NMDA receptor antagonist treatments have no effects on prepulse inhibition of postnatal day 25 Sprague-Dawley rats.

  Neurotoxicology 20090101

• A characteristic Glu17 residue of pig carnitine palmitoyltransferase 1 is responsible for the low Km for carnitine and the low sensitivity to malonyl-CoA inhibition of the enzyme.

  The FEBS journal 20090101

• Newborn screening of inborn errors of metabolism by capillary electrophoresis-electrospray ionization-mass spectrometry: a second-tier method with improved specificity and sensitivity.

  Analytical chemistry 20090101

• Evaluations of labrador retrievers with exercise-induced collapse, including response to a standardized strenuous exercise protocol.

  Journal of the American Animal Hospital Association 20090101

• Development of a CE-MS(2) method for the enantiomeric separation of L/D-carnitine: application to the analysis of infant formulas.

  Electrophoresis 20090101

• [The contribution of magnetic resonance imaging to the diagnosis of type I glutaric aciduria].

  Revista de neurologia 20090101

• Serum and muscle carnitine levels in epileptic children receiving sodium valproate.

  Journal of child neurology 20090101

• L-Carnitine ameliorates glycerol-induced myoglobinuric acute renal failure in rats.

  Renal failure 20090101

• Organic cation/carnitine transporter family expression patterns in adult murine heart.

  Pathology, research and practice 20090101

• Oxidative stress in response to aerobic and anaerobic power testing: influence of exercise training and carnitine supplementation.

  Research in sports medicine (Print) 20090101

• Vitagenes, dietary antioxidants and neuroprotection in neurodegenerative diseases.

  Frontiers in bioscience (Landmark edition) 20090101

• The metabolic treatment of patients with coronary artery disease: effects on quality of life and effort angina.

  Current pharmaceutical design 20090101

• Metabolic cardiology: the missing link in cardiovascular disease.

  Alternative therapies in health and medicine 20090101

• Malnutrition in the elderly patient on dialysis.

  Renal failure 20090101

• Mildronate, a regulator of energy metabolism, reduces atherosclerosis in apoE/LDLR-/- mice.

  Pharmacology 20090101

• High heritability of metabolomic profiles in families burdened with premature cardiovascular disease.

  Molecular systems biology 20090101

• Lipid metabolism and nutrigenomics - impact of sesame lignans on gene expression profiles and fatty acid oxidation in rat liver.

  Forum of nutrition 20090101

• [Effects of panthenol and carnitine on aldehyde metabolic enzymes in rats with tetrachloromethane-induced liver injury].

  Eksperimental'naia i klinicheskaia farmakologiia 20090101

• Metabolic cardiology: an integrative strategy in the treatment of congestive heart failure.

  Alternative therapies in health and medicine 20090101

• Children's toxicology from bench to bed--Liver injury (1): Drug-induced metabolic disturbance--toxicity of 5-FU for pyrimidine metabolic disorders and pivalic acid for carnitine metabolism.

  The Journal of toxicological sciences 20090101

• Pediatric parenteral nutrition: putting the microscope on macronutrients and micronutrients.

  Nutrition in clinical practice : official publication of the American Society for Parenteral and Enteral Nutrition 20090101

• In vitro studies on the inhibition of colon cancer by butyrate and carnitine.

  Nutrition (Burbank, Los Angeles County, Calif.) 20090101

• Syndrome of allergy, apraxia, and malabsorption: characterization of a neurodevelopmental phenotype that responds to omega 3 and vitamin E supplementation.

  Alternative therapies in health and medicine 20090101

• Two novel HADHB gene mutations in a Korean patient with mitochondrial trifunctional protein deficiency.

  Annals of clinical and laboratory science 20090101

• The effects of different levels of dietary protein and L-carnitine on blood sugar and lipids of the new GIFT strain of juvenile Nile tilapia (Oreochromis niloticus).

  TheScientificWorldJournal 20090101

• Reconstruction of the yeast Snf1 kinase regulatory network reveals its role as a global energy regulator.

  Molecular systems biology 20090101

• [Stress protection therapy in the prevention of macular morphological lesions in patients with diabetes mellitus at cataract microsurgery].

  Vestnik oftalmologii 20090101

• Mechanisms underlying metabolic and neural defects in zebrafish and human multiple acyl-CoA dehydrogenase deficiency (MADD).

  PloS one 20090101

• High anxiety: recognizing stress as the stressor.

  Oxidative medicine and cellular longevity 20090101

• Pro-inflammatory and oxidative stress pathways which compromise sperm motility and survival may be altered by L-carnitine.

  Oxidative medicine and cellular longevity 20090101

• Relationship between carnitine, fatty acids and insulin resistance.

  Gynakologisch-geburtshilfliche Rundschau 20090101

• Carnitine deficiency aggravates carboplatin nephropathy through deterioration of energy status, oxidant/anti-oxidant balance, and inflammatory endocoids.

  Toxicology 20081205

• Triple nutrient supplementation improves survival, infarct size and cardiac function following myocardial infarction in rats.

  Nutrition, metabolism, and cardiovascular diseases : NMCD 20081201

• Paradoxical increase of sperm motility and seminal carnitine associated with moderate leukocytospermia in infertile patients.

  Fertility and sterility 20081201

• Acute decompensation of isovaleric acidemia induced by Graves' disease.

  Intensive care medicine 20081201

• Assessment of puberty in relation to L-carnitine and hormonal replacement therapy in beta-thalassemic patients.

  Journal of tropical pediatrics 20081201

• Medium chain acyl CoA dehydrogenase deficiency causes unexplained coma in a 10-year-old child.

  Paediatric anaesthesia 20081201

• Urine acylcarnitine analysis by ESI-MS/MS: a new tool for the diagnosis of peroxisomal biogenesis disorders.

  Clinica chimica acta; international journal of clinical chemistry 20081201

• Mechanism of 3-nitropropionic acid-induced membrane permeability transition of isolated mitochondria and its suppression by L-carnitine.

  Cell biochemistry and function 20081201

• Precursor ion scan profiles of acylcarnitines by atmospheric pressure thermal desorption chemical ionization tandem mass spectrometry.

  Rapid communications in mass spectrometry : RCM 20081201

• Propionyl-L-carnitine prevents early graft dysfunction in allogeneic rat kidney transplantation.

  Kidney international 20081201

• Effects of feeding L-carnitine to gilts through day 70 of gestation on litter traits and the expression of insulin-like growth factor system components and L-carnitine concentration in foetal tissues.

  Journal of animal physiology and animal nutrition 20081201

• Pulmonary hypertension in beta-thalassemia major and the role of L-carnitine therapy.

  Pediatric hematology and oncology 20081201

• Carbohydrate, protein, and fat metabolism during exercise after oral carnitine supplementation in humans.

  International journal of sport nutrition and exercise metabolism 20081201

• Disorders of the carnitine cycle and detection by newborn screening.

  Annals of the Academy of Medicine, Singapore 20081201

• [The history, ingredients and effects of energy drinks].

  Orvosi hetilap 20081123

• Carnitine-palmitoyltransferase 2 deficiency: novel mutations and relevance of newborn screening.

  American journal of medical genetics. Part A 20081115

• Effects of carnitine supplementation on flow-mediated dilation and vascular inflammatory responses to a high-fat meal in healthy young adults.

  The American journal of cardiology 20081115

• A polarized localization of amino acid/carnitine transporter B(0,+) (ATB(0,+)) in the blood-brain barrier.

  Biochemical and biophysical research communications 20081114

• Hepatotoxicity associated with antiepileptic drugs.

  Acta neurologica Scandinavica 20081101

• Expression and localization of carnitine/organic cation transporter OCTN1 and OCTN2 in ocular epithelium.

  Investigative ophthalmology & visual science 20081101

• Neonatal PCP is more potent than ketamine at modifying preweaning behaviors of Sprague-Dawley rats.

  Toxicological sciences : an official journal of the Society of Toxicology 20081101

• Effects of L-carnitine on dialysis-related hypotension and muscle cramps: a meta-analysis.

  American journal of kidney diseases : the official journal of the National Kidney Foundation 20081101

• Determination of the reference range of endogenous plasma carnitines in healthy adults.

  Annals of clinical biochemistry 20081101

• The role of inflammatory markers in the cardioprotective effect of L-carnitine in L-NAME-induced hypertension.

  American journal of hypertension 20081101

• Carnitine in metabolic disease: potential for pharmacological intervention.

  Pharmacology & therapeutics 20081101

• Liquid chromatography/mass spectrometry determination of endogenous plasma acetyl and palmitoyl carnitines as potential biomarkers of beta-oxidation in mice.

  Rapid communications in mass spectrometry : RCM 20081101

• Increased C3-carnitine in a healthy premature infant.

  Clinical chemistry 20081101

• Plasma acylcarnitine and fatty acid profiles during exercise and training in Standardbreds.

  American journal of veterinary research 20081101

• [L-carnitine and cardiac metabolism and remodeling indices in alcoholic cardiomyopathy].

  Zhonghua nei ke za zhi 20081101

• Mildronate decreases carnitine availability and up-regulates glucose uptake and related gene expression in the mouse heart.

  Life sciences 20081024

• Effect of inhibiting carnitine biosynthesis on male rat sexual performance.

  Physiology & behavior 20081020

• Acetyl-L-carnitine suppresses apoptosis of thioredoxin 2-deficient DT40 cells.

  Archives of biochemistry and biophysics 20081015

• Study on the binding interaction between carnitine optical isomer and bovine serum albumin.

  European journal of medicinal chemistry 20081001

• L-carnitine supplementation attenuates intermittent hypoxia-induced oxidative stress and delays muscle fatigue in rats.

  Experimental physiology 20081001

• Impact of short- and medium-chain organic acids, acylcarnitines, and acyl-CoAs on mitochondrial energy metabolism.

  Biochimica et biophysica acta 20081001

• L-Carnitine suppresses oleic acid-induced membrane permeability transition of mitochondria.

  Cell biochemistry and function 20081001

• Lipid storage myopathies.

  Current opinion in neurology 20081001

• Self-consistent metabolic mixture analysis by heteronuclear NMR. Application to a human cancer cell line.

  Analytical chemistry 20081001

• L-carnitine supplementation and physical exercise restore age-associated decline in some mitochondrial functions in the rat.

  The journals of gerontology. Series A, Biological sciences and medical sciences 20081001

• Is oral L-acyl-carnitine an effective therapy for hepatic encephalopathy? Review of the literature.

  Digestive diseases and sciences 20080901

• Quantification of carnitine and acylcarnitines in biological matrices by HPLC electrospray ionization-mass spectrometry.

  Clinical chemistry 20080901

• Vitamin C is not essential for carnitine biosynthesis in vivo: verification in vitamin C-depleted senescence marker protein-30/gluconolactonase knockout mice.

  Biological & pharmaceutical bulletin 20080901

• An efficient transformation of cyclic ene-carbamates into omega-(N-formylamino)carboxylic acids by ruthenium tetroxide oxidation.

  Chemical & pharmaceutical bulletin 20080901

• [Statistical analysis of the consumption of nutritional and dietary supplements in gyms].

  Archivos latinoamericanos de nutricion 20080901

• Analysis of acetylcholine, choline and butyrobetaine in human liver tissues by hydrophilic interaction liquid chromatography-tandem mass spectrometry.

  Journal of pharmaceutical and biomedical analysis 20080805

• Beneficial impact of L-carnitine in liver: a study in a rat model of syndrome X.

  Amino acids 20080801

• L-carnitine protects against apoptosis of murine MC3T3-E1 osteoblastic cells.

  Amino acids 20080801

• Dietary l-carnitine supplementation improves bone mineral density by suppressing bone turnover in aged ovariectomized rats.

  Phytomedicine : international journal of phytotherapy and phytopharmacology 20080801

• Anesthetic management of a patient with 3-methylcrotonyl-CoA carboxylase deficiency.

  Anesthesia and analgesia 20080801

• Change in the membranous lipid composition accelerates lipid peroxidation in young rat hearts subjected to 2 weeks of hypoxia followed by hyperoxia.

  Circulation journal : official journal of the Japanese Circulation Society 20080801

• A high-throughput reporter gene assay to prove the ability of natural compounds to modulate glutathione peroxidase, superoxide dismutase and catalase gene promoters in V79 cells.

  Free radical research 20080801

• [Seminal plasma levocarnitine significantly correlated with semen quality].

  Zhonghua nan ke xue = National journal of andrology 20080801

• Antiarrhythmic and arrhythmogenic effects of L-carnitine in ischemia and reperfusion.

  Bulletin of experimental biology and medicine 20080801

• Determination of 3-hydroxyisovalerylcarnitine and other acylcarnitine levels using liquid chromatography-tandem mass spectrometry in serum and urine of a patient with multiple carboxylase deficiency.

  Journal of chromatography. B, Analytical technologies in the biomedical and life sciences 20080715

• Enhanced acyl-CoA dehydrogenase activity is associated with improved mitochondrial and contractile function in heart failure.

  Cardiovascular research 20080715

• Enhanced concentration-dependent cytotoxic effect of the dinuclear copper(II) complex of L-carnitine [Cu2(L-carnitine)2Cl2(H2O)2]Cl2, compared to L-carnitine or copper chloride dihydrate, in human leukemic cell lines.

  Journal of medicinal chemistry 20080710

• Rumen bypass and biodistribution of l-carnitine from dual-layered coated pellets in cows, in vitro and in vivo.

  International journal of pharmaceutics 20080709

• Cationic polyrotaxanes effectively inhibit uptake via carnitine/organic cationic transporters without cytotoxicity.

  Macromolecular bioscience 20080707

• Role of betaine:CoA ligase (CaiC) in the activation of betaines and the transfer of coenzyme A in Escherichia coli.

  Journal of applied microbiology 20080701

• Bioinformatics analysis of targeted metabolomics--uncovering old and new tales of diabetic mice under medication.

  Endocrinology 20080701

• Serum total L-carnitine levels in non-obese women with polycystic ovary syndrome.

  Human reproduction (Oxford, England) 20080701

• Hormonal and nutritional control of L-carnitine uptake in myoblastic C2C12 cells.

  Muscle & nerve 20080701

• Metabolomic analysis of the cerebrospinal fluid reveals changes in phospholipase expression in the CNS of SIV-infected macaques.

  The Journal of clinical investigation 20080701

• Effects of L-carnitine L-tartrate supplementation on muscle oxygenation responses to resistance exercise.

  Journal of strength and conditioning research 20080701

• Vigabatrin, lamotrigine, topiramate and serum carnitine levels.

  Pediatric neurology 20080701

• Identification of new mutations in the ETHE1 gene in a cohort of 14 patients presenting with ethylmalonic encephalopathy.

  Journal of medical genetics 20080701

• Treatment with pharmacological peroxisome proliferator-activated receptor alpha agonist clofibrate increases intestinal carnitine absorption in rats.

  Pharmacological research 20080701

• Rat liver mitochondrial carnitine palmitoyltransferase-I, hepatic carnitine, and malonyl-CoA: effect of starvation.

  Archives of physiology and biochemistry 20080701

• [Expression of hypoxia induced factor-1alpha and function of epididymis in varicocele: experiment with rats].

  Zhonghua yi xue za zhi 20080624

• Metabolic agents in the management of diabetic coronary patients: a new era.

  International journal of cardiology 20080623

• Interaction of beta-lactam antibiotics with the mitochondrial carnitine/acylcarnitine transporter.

  Chemico-biological interactions 20080617

• Interstitial deletion of 1p22.2p31.1 and medium-chain acyl-CoA dehydrogenase deficiency in a patient with global developmental delay.

  American journal of medical genetics. Part A 20080615

• High concentrations of stavudine impair fatty acid oxidation without depleting mitochondrial DNA in cultured rat hepatocytes.

  Toxicology in vitro : an international journal published in association with BIBRA 20080601

• Carnitine supplementation induces acylcarnitine production in tissues of very long-chain acyl-CoA dehydrogenase-deficient mice, without replenishing low free carnitine.

  Pediatric research 20080601

• PDZK1 regulates two intestinal solute carriers (Slc15a1 and Slc22a5) in mice.

  Drug metabolism and disposition: the biological fate of chemicals 20080601

• Cardiomyopathy and carnitine deficiency.

  Molecular genetics and metabolism 20080601

• Carnitine and carnitine acetyltransferases in the yeast Saccharomyces cerevisiae: a role for carnitine in stress protection.

  Current genetics 20080601

• Effects of oral L-carnitine, L-lysine administration and exercise on body composition and histological and biochemical parameters in pigeons.

  Journal of animal physiology and animal nutrition 20080601

• Acetyl-L-carnitine and alpha-lipoic acid: possible neurotherapeutic agents for mood disorders?

  Expert opinion on investigational drugs 20080601

• The effect of male and female supplementation of L-carnitine on reproductive traits of white leghorns.

  Poultry science 20080601

• Biochemical correction of short-chain acyl-coenzyme A dehydrogenase deficiency after portal vein injection of rAAV8-SCAD.

  Human gene therapy 20080601

• L-carnitine supplementation decreases the left ventricular mass in patients undergoing hemodialysis.

  Circulation journal : official journal of the Japanese Circulation Society 20080601

• Evaluation of the efficacy of propionyl-L-carnitine versus pulsed muscular compressions in diabetic and non-diabetic patients affected by obliterating arteriopathy Leriche stage II.

  International angiology : a journal of the International Union of Angiology 20080601

• Regulation of Octn2 transporter (SLC22A5) by peroxisome proliferator activated receptor alpha.

  Biological & pharmaceutical bulletin 20080601

• Effects of osmoprotectants on hyperosmolar stress in cultured human corneal epithelial cells.

  Cornea 20080601

• [New therapeutic approaches in mitochondrial fatty acid oxidation disorders].

  Archives de pediatrie : organe officiel de la Societe francaise de pediatrie 20080601

• Application of metabolomic principles to disorders of nucleotide metabolism reveals new metabolic perturbations.

  Nucleosides, nucleotides & nucleic acids 20080601

• [Physiological functions of carnitine and carnitine transporters in the central nervous system].

  Nihon shinkei seishin yakurigaku zasshi = Japanese journal of psychopharmacology 20080601

• Chronic suppression of acetyl-CoA carboxylase 1 in beta-cells impairs insulin secretion via inhibition of glucose rather than lipid metabolism.

  The Journal of biological chemistry 20080523

• Effect of L-carnitine administration on the modulated rat brain protein concentration, acetylcholinesterase, Na+K+-ATPase and Mg2+-ATPase activities induced by forced swimming.

  British journal of sports medicine 20080501

• Excitotoxic damage, disrupted energy metabolism, and oxidative stress in the rat brain: antioxidant and neuroprotective effects of L-carnitine.

  Journal of neurochemistry 20080501

• The in-depth evaluation of suspected mitochondrial disease.

  Molecular genetics and metabolism 20080501

• Maternal glutaric acidemia, type I identified by newborn screening.

  Molecular genetics and metabolism 20080501

• Tissue damage in rat ovaries subjected to torsion and detorsion: effects of L-carnitine and N-acetyl cysteine.

  Pediatric surgery international 20080501

• Effect of a dietary antioxidant supplementation on semen quality in pony stallions.

  Theriogenology 20080501

• Acquired multiple Acyl-CoA dehydrogenase deficiency in 10 horses with atypical myopathy.

  Neuromuscular disorders : NMD 20080501

• Pharmacological manipulation of L-carnitine transport into L6 cells with stable overexpression of human OCTN2.

  Cellular and molecular life sciences : CMLS 20080501

• Neonatal vitamin B12 deficiency secondary to maternal subclinical pernicious anemia: identification by expanded newborn screening.

  The Journal of pediatrics 20080501

• Spectrum of medium-chain acyl-CoA dehydrogenase deficiency detected by newborn screening.

  Pediatrics 20080501

• [Study of aerobic capacity in chronic hemodialized patients: effect of L-carnitine supplementation].

  Medicina clinica 20080405

• L-carnitine treatment reduces steatosis in patients with chronic hepatitis C treated with alpha-interferon and ribavirin.

  Digestive diseases and sciences 20080401

• Characterization of L-aminocarnitine, an inhibitor of fatty acid oxidation.

  Molecular genetics and metabolism 20080401

• A Delphi-based consensus clinical practice protocol for the diagnosis and management of 3-methylcrotonyl CoA carboxylase deficiency.

  Molecular genetics and metabolism 20080401

• Vitamin E and L-carnitine, separately or in combination, in the prevention of radiation-induced brain and retinal damages.

  Neurosurgical review 20080401

• Randomized phase III clinical trial of five different arms of treatment for patients with cancer cachexia: interim results.

  Nutrition (Burbank, Los Angeles County, Calif.) 20080401

• Combined newborn screening for succinylacetone, amino acids, and acylcarnitines in dried blood spots.

  Clinical chemistry 20080401

• Carnitine-dependent transport of acetyl coenzyme A in Candida albicans is essential for growth on nonfermentable carbon sources and contributes to biofilm formation.

  Eukaryotic cell 20080401

• Combined treatment with L-carnitine and a pan-caspase inhibitor effectively reverses amiodarone-induced injury in cultured human lung epithelial cells.

  Apoptosis : an international journal on programmed cell death 20080401

• Carnitine deficiency and L-carnitine supplementation in lysinuric protein intolerance.

  Metabolism: clinical and experimental 20080401

• The effect of dietary l-carnitine supplementation on pulmonary hypertension syndrome mortality in broilers exposed to low temperatures.

  Journal of animal physiology and animal nutrition 20080401

• Enhancing newborn screening for tyrosinemia type I.

  Clinical chemistry 20080401

• Effects of acute L-carnitine intake on metabolic and blood lactate levels of elite badminton players.

  Neuro endocrinology letters 20080401

• Clofibrate treatment up-regulates novel organic cation transporter (OCTN)-2 in tissues of pigs as a model of non-proliferating species.

  European journal of pharmacology 20080331

• A successfully treated adult patient with L-2-hydroxyglutaric aciduria.

  Neurology 20080325

• The inhibitory effects of fluoroquinolones on L-carnitine transport in placental cell line BeWo.

  International journal of pharmaceutics 20080303

• Carnitine-mediated improved response to erythropoietin involves induction of haem oxygenase-1: studies in humans and in an animal model.

  Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20080301

• Characteristics of L-carnitine import into heart cells.

  Biochimie 20080301

• Insulin action on glucose and protein metabolism during L-carnitine supplementation in maintenance haemodialysis patients.

  Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20080301

• Role of L-carnitine in the modulation of immune response in aged rats.

  Clinica chimica acta; international journal of clinical chemistry 20080301

• Optimization of a rapid capillary electrophoresis ESI-IT tandem mass spectrometry method for the analysis of short-chain carnitines in human plasma.

  Analytical and bioanalytical chemistry 20080301

• L: -carnitine fumarate and isovaleryl-L: -carnitine fumarate accelerate the recovery of bone volume/total volume ratio after experimetally induced osteoporosis in pregnant mice.

  Calcified tissue international 20080301

• Metabolic testing in the pediatric epilepsy unit.

  Pediatric neurology 20080301

• The effect of in ovo injection of L-carnitine on hatchability of white leghorns.

  Poultry science 20080301

• PPAR alpha mediates transcriptional upregulation of novel organic cation transporters-2 and -3 and enzymes involved in hepatic carnitine synthesis.

  Experimental biology and medicine (Maywood, N.J.) 20080301

• A case of hemoperfusion and L-carnitine management in valproic acid overdose.

  The American journal of emergency medicine 20080301

• [Neonatal onset of organic acidemia (propionic) diagnosed by tandem mass spectrometry].

  Biomedica : revista del Instituto Nacional de Salud 20080301

• Carnitine worsens both injury and recovery of contractile function after transient ischemia in perfused rat heart.

  Journal of physiology and biochemistry 20080301

• L-carnitine enhances resistance to oxidative stress by reducing DNA damage in Ataxia telangiectasia cells.

  Mutation research 20080227

• The effects of L-carnitine on the combination of, inhalation anesthetic-induced developmental, neuronal apoptosis in the rat frontal cortex.

  Neuroscience 20080219

• Prenatal diagnosis of methylmalonic aciduria by analysis of organic acids and total homocysteine in amniotic fluid.

  Chinese medical journal 20080205

• Oleic acid delays and modulates the transition from respiratory to fermentative metabolism in Saccharomyces cerevisiae after exposure to glucose excess.

  Applied microbiology and biotechnology 20080201

• Changes in redox ratio and protein glycation in precataractous lens from fructose-fed rats: effects of exogenous L-carnitine.

  Clinical and experimental pharmacology & physiology 20080201

• Contributions of phosphorylation to regulation of OCTN2 uptake of carnitine are minimal in BeWo cells.

  Biochemical pharmacology 20080201

• Synthesis and characterization of carnitine nitro-derivatives.

  Bioorganic & medicinal chemistry 20080201

• Toxicity of valproic acid in mice with decreased plasma and tissue carnitine stores.

  The Journal of pharmacology and experimental therapeutics 20080201

• Demographic and nutritional factors associated with prolonged cholestatic jaundice in the premature infant.

  Journal of perinatology : official journal of the California Perinatal Association 20080201

• Hyperammonemic encephalopathy caused by carnitine deficiency.

  Journal of general internal medicine 20080201

• Renoprotective action of L-carnitine in fructose-induced metabolic syndrome.

  Diabetes, obesity & metabolism 20080201

• L-carnitine supplementation in the dialysis population: are Australian patients missing out?

  Nephrology (Carlton, Vic.) 20080201

• Long chain fatty acyl-CoA modulation of H(2)O (2) release at mitochondrial complex I.

  Journal of bioenergetics and biomembranes 20080201

• Potential relationships between transaminase abnormality and valproic acid clearance or serum carnitine concentrations in Japanese epileptic patients.

  The Journal of pharmacy and pharmacology 20080201

• Effect of glycine propionyl-L-carnitine on aerobic and anaerobic exercise performance.

  International journal of sport nutrition and exercise metabolism 20080201

• Interaction of mildronate with the mitochondrial carnitine/acylcarnitine transport protein.

  Journal of biochemical and molecular toxicology 20080201

• Acylcarnitine profile analysis.

  Genetics in medicine : official journal of the American College of Medical Genetics 20080201

• Functional characterization of residues within the carnitine/acylcarnitine translocase RX2PANAAXF distinct motif.

  Molecular membrane biology 20080201

• Effect of tacrolimus on the cauda epididymis in rats: analysis of epididymal biochemical markers or antioxidant defense enzymes.

  Toxicology 20080114

• Expression patterns of the organic cation/carnitine transporter family in adult murine brain.

  Brain & development 20080101

• Carnitine membrane transporter deficiency: a rare treatable cause of cardiomyopathy and anemia.

  Pediatric cardiology 20080101

• Altered carnitine homeostasis is associated with decreased mitochondrial function and altered nitric oxide signaling in lambs with pulmonary hypertension.

  American journal of physiology. Lung cellular and molecular physiology 20080101

• Non-surgical therapy of Peyronie's disease.

  Asian journal of andrology 20080101

• The in vivo and in vitro effects of L-carnitine supplementation on the erythrocyte membrane acetylcholinesterase, Na+, K+-ATPase and Mg2+-ATPase activities in basketball players.

  Clinical chemistry and laboratory medicine 20080101

• Severe acute hyperammonemia after brief exposure to valproate.

  Psychosomatics 20080101

• Extracellular ATP increases L-carnitine transport and content in C2C12 cells.

  Pharmacology 20080101

• Effects of L-carnitine on obesity, diabetes, and as an ergogenic aid.

  Asia Pacific journal of clinical nutrition 20080101

• ATP production and TCA activity are stimulated by propionyl-L-carnitine in the diabetic rat heart.

  Drugs in R&D 20080101

• Fasting and caloric restriction increases mRNA concentrations of novel organic cation transporter-2 and carnitine concentrations in rat tissues.

  Annals of nutrition & metabolism 20080101

• Levo-propionyl-carnitine improves the effectiveness of supervised physical training on the absolute claudication distance in patients with intermittent claudication.

  Angiology 20080101

• No influence of SLC22A4 C6607T and RUNX1 G24658C genotypic variants on the circulating carnitine ester profile in patients with rheumatoid arthritis.

  Clinical and experimental rheumatology 20080101

• Single-laboratory validation of a liquid chromatographic/tandem mass spectrometric method for the determination of free and total carnitine in infant formula and raw ingredients.

  Journal of AOAC International 20080101

• [Adaptation of free and total plasma carnitine determination on the Dimension HM, X-Pand model (Dade Behring)].

  Annales de biologie clinique 20080101

• Effect of carnitine deprivation on carnitine homeostasis and energy metabolism in mice with systemic carnitine deficiency.

  Annals of nutrition & metabolism 20080101

• Propionyl-L-carnitine in Leriche-Fontaine stage II peripheral arterial obstructive disease.

  Annals of vascular surgery 20080101

• Mechanisms of zidovudine-induced mitochondrial toxicity and myopathy.

  Pharmacology 20080101

• Involvement of carnitine/organic cation transporter OCTN2 (SLC22A5) in distribution of its substrate carnitine to the heart.

  Drug metabolism and pharmacokinetics 20080101

• L-carnitine supplementation: influence upon physiological function.

  Current sports medicine reports 20080101

• Effect of oral L-carnitine administration on insulin sensitivity and lipid profile in type 2 diabetes mellitus patients.

  Annals of nutrition & metabolism 20080101

• Simultaneous determination of free carnitine and total choline by liquid chromatography/mass spectrometry in infant formula and health-care products: single-laboratory validation.

  Journal of AOAC International 20080101

• Role of Na+/L-carnitine transporter (OCTN2) in renal handling of pivaloylcarnitine and valproylcarnitine formed during pivalic acid-containing prodrugs and valproic acid treatment.

  Drug metabolism and pharmacokinetics 20080101

• Vegetarian diet affects genes of oxidative metabolism and collagen synthesis.

  Annals of nutrition & metabolism 20080101

• The effect of the mode of delivery on the maternal-neonatal carnitine blood levels and antioxidant status.

  Clinical chemistry and laboratory medicine 20080101

• L-carnitine treatment partially restores urinary bladder function of streptozotocin diabetic rats.

  Urologia internationalis 20080101

• Carnitine status in early-treated children, adolescents and young adults with phenylketonuria on low phenylalanine diets.

  Annals of nutrition & metabolism 20080101

• Positive inotropic effect of coenzyme Q10, omega-3 fatty acids and propionyl-L-carnitine on papillary muscle force-frequency responses of BIO TO-2 cardiomyopathic Syrian hamsters.

  BioFactors (Oxford, England) 20080101

• Restrictive dermopathy: report of one case and the metabolic and post-mortem findings.

  The Turkish journal of pediatrics 20080101

• L-carnitine and its derivatives: exciting experimental and clinical data are accumulating in the treatment of ocular disorders.

  Drugs in R&D 20080101

• The aging eye and the role of L-carnitine and its derivatives.

  Drugs in R&D 20080101

• Ocular disorders secondary to systemic disease and the potential role of carnitines.

  Drugs in R&D 20080101

• Inherited ocular disorders, ophthalmic procedures and carnitines.

  Drugs in R&D 20080101

• L-carnitine and its derivatives: a promising future in the treatment of ocular disorders.

  Drugs in R&D 20080101

• [Destabilization of the cytosolic calcium level and cardiomyocyte death in the presence of long-chain fatty acid derivatives].

  Biofizika 20080101

• Age-dependent upregulation of p53 and cytochrome c release and susceptibility to apoptosis in skeletal muscle fiber of aged rats: role of carnitine and lipoic acid.

  Free radical biology & medicine 20071215

• Antioxidant treatment associated with sildenafil reduces monocyte activation and markers of endothelial damage in patients with diabetic erectile dysfunction: a double-blind, placebo-controlled study.

  European urology 20071201

• Editorial comment on: Antioxidant treatment associated with sildenafil reduces monocyte activation and markers of endothelial damage in patients with diabetic erectile dysfunction: a double-blind, placebo-controlled study.

  European urology 20071201

• Editorial comment on: Antioxidant treatment associated with sildenafil reduces monocyte activation and markers of endothelial damage in patients with diabetic erectile dysfunction: a double-blind, placebo-controlled study.

  European urology 20071201

• Cystic renal dysplasia as a leading sign of inherited metabolic disease.

  Pediatric nephrology (Berlin, Germany) 20071201

• Choice of oils for essential fat supplements can enhance production of abnormal metabolites in fat oxidation disorders.

  Molecular genetics and metabolism 20071201

• Hemolytic uremic syndrome (HUS) secondary to cobalamin C (cblC) disorder.

  Pediatric nephrology (Berlin, Germany) 20071201

• Spontaneous development of intestinal and colonic atrophy and inflammation in the carnitine-deficient jvs (OCTN2(-/-)) mice.

  Molecular genetics and metabolism 20071201

• Metabolomics identifies perturbations in human disorders of propionate metabolism.

  Clinical chemistry 20071201

• L-carnitine as an adjunct therapy to percutaneous coronary intervention for non-ST elevation myocardial infarction.

  Cardiovascular drugs and therapy 20071201

• Peroxisome proliferator-activated receptor alpha-retinoid X receptor agonists induce beta-cell protection against palmitate toxicity.

  The FEBS journal 20071201

• Reversal of cisplatin-induced carnitine deficiency and energy starvation by propionyl-L-carnitine in rat kidney tissues.

  Clinical and experimental pharmacology & physiology 20071201

• [Acute heart failure in a 16-month child: onset of primary deficit of carnitine].

  Minerva pediatrica 20071201

• Carnitine is associated with fatty acid metabolism in plants.

  Plant physiology and biochemistry : PPB 20071201

• Separation and identification of plasma short-chain acylcarnitine isomers by HPLC/MS/MS for the differential diagnosis of fatty acid oxidation defects and organic acidemias.

  Journal of chromatography. B, Analytical technologies in the biomedical and life sciences 20071201

• Reduced carnitine level causes death from hypoglycemia: possible involvement of suppression of hypothalamic orexin expression during weaning period.

  Endocrine journal 20071201

• No mutation was found in the alpha-subunit of the mitochondrial tri-functional protein in one patient with severe acute fatty liver of pregnancy and her relatives.

  Journal of gastroenterology and hepatology 20071201

• [Determination of normal acylcarnitine levels in a healthy pediatric population as a diagnostic tool in inherited errors of mitochondrial fatty acid beta-oxidation].

  Anales de pediatria (Barcelona, Spain : 2003) 20071201

• [Application of tandem mass spectrometry on the diagnosis of fatty acid oxidation disorders].

  Zhonghua yi xue yi chuan xue za zhi = Zhonghua yixue yichuanxue zazhi = Chinese journal of medical genetics 20071201

• Acylcarnitine profiles during carnitine loading and fasting tests in a Japanese patient with medium-chain acyl-CoA dehydrogenase deficiency.

  The Tohoku journal of experimental medicine 20071201

• Comparison of the effects of sodium nitroprusside and L-carnitine in experimental ischemia-reperfusion injury in rats.

  Transplantation proceedings 20071201

• The myopathy of peripheral arterial occlusive disease: part 1. Functional and histomorphological changes and evidence for mitochondrial dysfunction.

  Vascular and endovascular surgery 20071201

• Subacute presentation of propionic acidemia.

  Journal of child neurology 20071201

• A new case of short-chain acyl-CoA dehydrogenase deficiency: clinical, biochemical, genetic and (1)H-NMR spectroscopic studies.

  Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology 20071201

• Two cases of valproic acid poisoning treated with L-carnitine.

  Human & experimental toxicology 20071201

• Hypocarnitinemic hypoglycemia and heart failure in an infant with a constant parenteral elementary nutrition during measles vaccination-related febrile illness.

  Neuropediatrics 20071201

• Carnitine and lipoate ameliorates lipofuscin accumulation and monoamine oxidase activity in aged rat heart.

  European journal of pharmacology 20071121

• Dietary oxidised fat up regulates the expression of organic cation transporters in liver and small intestine and alters carnitine concentrations in liver, muscle and plasma of rats.

  The British journal of nutrition 20071101

• Protective role of carnitine in breast cancer via decreasing arginase activity and increasing nitric oxide.

  Cell biology international 20071101

• Sex differences in the control of plasma concentrations and urinary excretion of glycine betaine in patients attending a lipid disorders clinic.

  Clinical biochemistry 20071101

• Indications that topical L-carnitin-L-tartrate promotes human hair growth in vivo.

  Journal of dermatological science 20071101

• Transport of butyryl-L-carnitine, a potential prodrug, via the carnitine transporter OCTN2 and the amino acid transporter ATB(0,+).

  American journal of physiology. Gastrointestinal and liver physiology 20071101

• L-carnitine-L-tartrate promotes human hair growth in vitro.

  Experimental dermatology 20071101

• Submitochondrial localization of 6-N-trimethyllysine dioxygenase - implications for carnitine biosynthesis.

  The FEBS journal 20071101

• Classic and late-onset neurological disease in two siblings with glutaryl-CoA dehydrogenase deficiency.

  Journal of inherited metabolic disease 20071101

• Conformation-dependent accessibility of Cys-136 and Cys-155 of the mitochondrial rat carnitine/acylcarnitine carrier to membrane-impermeable SH reagents.

  Biochimica et biophysica acta 20071101

• Transport of carnitine and acetylcarnitine by carnitine/organic cation transporter (OCTN) 2 and OCTN3 into epididymal spermatozoa.

  Reproduction (Cambridge, England) 20071101

• Cancer-related fatigue. Clinical Practice Guidelines in Oncology.

  Journal of the National Comprehensive Cancer Network : JNCCN 20071101

• Increase in nitric oxide and reductions in blood pressure, protein kinase C beta II and oxidative stress by L-carnitine: a study in the fructose-fed hypertensive rat.

  Clinical and experimental hypertension (New York, N.Y. : 1993) 20071101

• Redirecting metabolic fluxes through cofactor engineering: Role of CoA-esters pool during L(-)-carnitine production by Escherichia coli.

  Journal of biotechnology 20071031

• Prospective treatment in carnitine-acylcarnitine translocase deficiency.

  Journal of inherited metabolic disease 20071001

• Influence of dietary L-carnitine and chromium picolinate on blood hormones and metabolites of gestating sows fed one meal per day.

  Journal of animal science 20071001

• Plasmid maintenance and physiology of a genetically engineered Escherichia coli strain during continuous L-carnitine production.

  Biotechnology letters 20071001

• [Therapeutic approach to epilepsy from the nutritional view: current status of dietary treatment].

  Neurologia (Barcelona, Spain) 20071001

• cis-3,4-Methylene-heptanoylcarnitine: characterization and verification of the C8:1 acylcarnitine in human urine.

  Journal of chromatography. B, Analytical technologies in the biomedical and life sciences 20071001

• L-Carnitine in the treatment of fatigue in adult celiac disease patients: a pilot study.

  Digestive and liver disease : official journal of the Italian Society of Gastroenterology and the Italian Association for the Study of the Liver 20071001

• Deficiency of the carnitine transporter (OCTN2) with partial N-acetylglutamate synthase (NAGS) deficiency.

  Journal of inherited metabolic disease 20071001

• Comparison of vitamin E and propionyl-L-carnitine, separately or in combination, in patients with early chronic Peyronie's disease: a double-blind, placebo controlled, randomized study.

  The Journal of urology 20071001

• Hepatoprotective effect of L-carnitine against acute acetaminophen toxicity in mice.

  Experimental and toxicologic pathology : official journal of the Gesellschaft fur Toxikologische Pathologie 20071001

• Marfanoid features in a child with combined methylmalonic aciduria and homocystinuria (CblC type).

  Journal of inherited metabolic disease 20071001

• Protective effects of L-carnitine and alpha-lipoic acid in rats with adjuvant arthritis.

  Pharmacological research 20071001

• The effect of dietary L-carnitine on semen traits of White Leghorns.

  Poultry science 20071001

• Fatty acid chain-elongation in perfused rat heart: synthesis of stearoylcarnitine from perfused palmitate.

  FEBS letters 20070918

• Investigations of the effects of gender, diurnal variation, and age in human urinary metabolomic profiles.

  Analytical chemistry 20070915

• A new LC-ESI-MS/MS method to measure long-chain acylcarnitine levels in cultured cells.

  Analytica chimica acta 20070905

• L-carnitine increases liver alpha-tocopherol and lowers liver and plasma triglycerides in aging ovariectomized rats.

  The Journal of nutritional biochemistry 20070901

• L-carnitine inhibits a subset of platelet activation responses in chronic uraemia.

  Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20070901

• Lipase-catalyzed esterification of conjugated linoleic acid with L-carnitine in solvent-free system and acetonitrile.

  Bioprocess and biosystems engineering 20070901

• A pharmacokinetic model for L-carnitine in patients receiving haemodialysis.

  British journal of clinical pharmacology 20070901

• Cytochrome c oxidase rather than cytochrome c is a major determinant of mitochondrial respiratory capacity in skeletal muscle of aged rats: role of carnitine and lipoic acid.

  Rejuvenation research 20070901

• Pressure overload-induced cardiomyopathy in heterozygous carrier mice of carnitine transporter gene mutation.

  Hypertension (Dallas, Tex. : 1979) 20070901

• PPAR alpha-activation results in enhanced carnitine biosynthesis and OCTN2-mediated hepatic carnitine accumulation.

  Biochimica et biophysica acta 20070901

• Impact of fasting and postprandial state on plasma carnitine concentrations during aerobic exercise in type 2 diabetes.

  Acta diabetologica 20070901

• Carnitine-associated encephalopathy caused by long-term treatment with an antibiotic containing pivalic acid.

  Pediatrics 20070901

• Case files of the Children's Hospital of Michigan Regional Poison Control Center: the use of carnitine for the management of acute valproic acid toxicity.

  Journal of medical toxicology : official journal of the American College of Medical Toxicology 20070901

• A Japanese adult form of CPT II deficiency associated with a homozygous F383Y mutation.

  Neurology 20070821

• L-carnitine attenuates oxidative stress in hypertensive rats.

  The Journal of nutritional biochemistry 20070801

• ESI-MS/MS study of acylcarnitine profiles in urine from patients with organic acidemias and fatty acid oxidation disorders.

  Journal of chromatography. B, Analytical technologies in the biomedical and life sciences 20070801

• Plasma carnitine ester profiles in Crohn's disease patients characterized for SLC22A4 C1672T and SLC22A5 G-207C genotypes.

  The British journal of nutrition 20070801

• Serum carnitine, triglyceride and cholesterol profiles in Korean neonates.

  The British journal of nutrition 20070801

• Involvement of carrier-mediated transport system in uptake of tetrodotoxin into liver tissue slices of puffer fish Takifugu rubripes.

  Toxicon : official journal of the International Society on Toxinology 20070801

• Carnitine, acylcarnitine and amino acid profiles analyzed by tandem mass spectrometry in a surfactant/virus mouse model of acute hepatic encephalopathy.

  Chemosphere 20070801

• ETFDH mutations as a major cause of riboflavin-responsive multiple acyl-CoA dehydrogenation deficiency.

  Brain : a journal of neurology 20070801

• Population quantile-quantile plots for monitoring assay performance in newborn screening.

  Journal of inherited metabolic disease 20070801

• Diabetes-induced bradycardia is an intrinsic metabolic defect reversed by carnitine.

  Metabolism: clinical and experimental 20070801

• Effect of L-carnitine supplementation on secondary hyperparathyroidism and bone metabolism in hemodialyzed patients.

  Calcified tissue international 20070801

• Expanded newborn screening in Europe 2007.

  Journal of inherited metabolic disease 20070801

• Treatment with pharmacological peroxisome proliferator-activated receptor alpha agonist clofibrate causes upregulation of organic cation transporter 2 in liver and small intestine of rats.

  Pharmacological research 20070801

• l-carnitine and its propionate: improvement of endothelial function in SHR through superoxide dismutase-dependent mechanisms.

  Free radical research 20070801

• Carnitine deficiency in pregnancy.

  Obstetrics and gynecology 20070801

• Propionyl-L-carnitine prevents age-related myocardial remodeling in the rabbit.

  Journal of cardiovascular pharmacology 20070801

• Effects of low oxygen levels on the expression and function of transporter OCTN2 in BeWo cells.

  The Journal of pharmacy and pharmacology 20070801

• Effect of carni Q-gel (ubiquinol and carnitine) on cytokines in patients with heart failure in the Tishcon study.

  Acta cardiologica 20070801

• Determination of highly soluble L-carnitine in biological samples by reverse phase high performance liquid chromatography with fluorescent derivatization.

  Archives of pharmacal research 20070801

• The effect of supplementing sow with bioactive substances on neonatal small intestinal epithelium.

  Journal of physiology and pharmacology : an official journal of the Polish Physiological Society 20070801

• Regulation of lipid flux between liver and adipose tissue during transient hepatic steatosis in carnitine-depleted rats.

  The Journal of biological chemistry 20070720

• Supplementation with l-carnitine does not reduce the efficacy of epirubicin treatment in breast cancer cells.

  Cancer letters 20070718

• Dietary L-carnitine supplementation enhances the lipopolysaccharide-induced acute phase protein response in broiler chickens.

  Veterinary immunology and immunopathology 20070715

• Carnitine palmitoyltransferase 2: analysis of membrane association and complex structure with a substrate analog.

  FEBS letters 20070710

• Determination of free L-carnitine levels in type II diabetic women with and without complications.

  European journal of clinical nutrition 20070701

• Growth characteristics, blood metabolites, and insulin-like growth factor system components in maternal tissues of gilts fed L-carnitine through day seventy of gestation.

  Journal of animal science 20070701

• A novel functional assay for simultaneous determination of total fatty acid beta-oxidation flux and acylcarnitine profiling in human skin fibroblasts using (2)H(31)-palmitate by isotope ratio mass spectrometry and electrospray tandem mass spectrometry.

  Clinica chimica acta; international journal of clinical chemistry 20070701

• Pivalate lowers litter sizes and weights in female rats independent of its effect on carnitine status.

  Reproductive toxicology (Elmsford, N.Y.) 20070701

• Rapid 2nd-tier test for measurement of 3-OH-propionic and methylmalonic acids on dried blood spots: reducing the false-positive rate for propionylcarnitine during expanded newborn screening by liquid chromatography-tandem mass spectrometry.

  Clinical chemistry 20070701

• Feature construction can improve diagnostic criteria for high-dimensional metabolic data in newborn screening for medium-chain acyl-CoA dehydrogenase deficiency.

  Clinical chemistry 20070701

• Determination of carnitine ester patterns during the second half of pregnancy, at delivery, and in neonatal cord blood by tandem mass spectrometry: complex and dynamic involvement of carnitine in the intermediary metabolism.

  Pediatric research 20070701

• Disruption of AtOCT1, an organic cation transporter gene, affects root development and carnitine-related responses in Arabidopsis.

  The Plant journal : for cell and molecular biology 20070701

• Dietary L-carnitine affects periparturient nutrient metabolism and lactation in multiparous cows.

  Journal of dairy science 20070701

• Carnitine content in different muscles of patients receiving maintenance hemodialysis.

  Journal of renal nutrition : the official journal of the Council on Renal Nutrition of the National Kidney Foundation 20070701

• Exclusive cardiac dysfunction in familial primary carnitine deficiency cases: a genotype-phenotype correlation.

  Clinical genetics 20070701

• Hyperammonemia due to valproic acid in the psychiatric setting.

  The American journal of psychiatry 20070701

• [Clinical studies on fifty-seven Chinese patients with combined methylmalonic aciduria and homocysteinemia].

  Zhonghua er ke za zhi = Chinese journal of pediatrics 20070701

• Definition by functional and structural analysis of two malonyl-CoA sites in carnitine palmitoyltransferase 1A.

  The Journal of biological chemistry 20070622

• Functional characterization of the TMLH gene: promoter analysis, in situ hybridization, identification and mapping of alternative splicing variants.

  Gene 20070615

• Study the effects of different levels of fat and L-carnitine on performance, carcass characteristics and serum composition of broiler chicks.

  Pakistan journal of biological sciences : PJBS 20070615

• Urinary excretion of L-carnitine and its short-chain acetyl-L-carnitine in patients undergoing carboplatin treatment.

  Cancer chemotherapy and pharmacology 20070601

• New insights concerning the role of carnitine in the regulation of fuel metabolism in skeletal muscle.

  The Journal of physiology 20070601

• Carnitine transporter and holocarboxylase synthetase deficiencies in The Faroe Islands.

  Journal of inherited metabolic disease 20070601

• Transport and transporters in the endoplasmic reticulum.

  Biochimica et biophysica acta 20070601

• OCTN2VT, a splice variant of OCTN2, does not transport carnitine because of the retention in the endoplasmic reticulum caused by insertion of 24 amino acids in the first extracellular loop of OCTN2.

  Biochimica et biophysica acta 20070601

• Plasma L-carnitine concentration in healthy dogs and dogs with hepatopathy.

  Veterinary clinical pathology 20070601

• L-Carnitine inhibits protein glycation in vitro and in vivo: evidence for a role in diabetic management.

  Acta diabetologica 20070601

• Dietary supplements and nutraceuticals in the management of andrologic disorders.

  Endocrinology and metabolism clinics of North America 20070601

• Effect of chronic stress and L-carnitine on rat stomach.

  The journal of physiological sciences : JPS 20070601

• Association of carnitine deficiency in Indian continuous ambulatory peritoneal dialysis patients with anemia, erythropoietin use, residual renal function, and diabetes mellitus.

  Peritoneal dialysis international : journal of the International Society for Peritoneal Dialysis 20070601

• [Chronic fatigue syndrome and neurotransmitters].

  Nihon rinsho. Japanese journal of clinical medicine 20070601

• L-carnitine influence on oxidative stress induced by hind limb unloading in adult rats.

  Aviation, space, and environmental medicine 20070601

• Effects of breeder hen age and dietary L-carnitine on progeny embryogenesis.

  British poultry science 20070601

• L-carnitine protects human retinal pigment epithelial cells from oxidative damage.

  Current eye research 20070601

• [Correlation of free L-carnitine level with accessory gland markers and its clinical significance].

  Zhonghua nan ke xue = National journal of andrology 20070601

• [Rehabilitation program in patients with moderate-to-severe intermittent claudication: immediate results and one year follow-up].

  Monaldi archives for chest disease = Archivio Monaldi per le malattie del torace 20070601

• Rapid determination of short chain carnitines in human plasma by electrospray ionisation-ion trap mass spectrometry using capillary electrophoresis instrument as sampler.

  Journal of chromatography. A 20070525

• Effect of carnitine supplementation on lipid profile and anemia in children on chronic dialysis.

  Pediatric nephrology (Berlin, Germany) 20070501

• Investigation of the ligand spectrum of human sterol carrier protein 2 using a direct mass spectrometry assay.

  Archives of biochemistry and biophysics 20070501

• Effect of L-carnitine infusion and feed restriction on carnitine status in lactating Holstein cows.

  Journal of dairy science 20070501

• Childhood malignant diseases: which is the carnitine's role?

  Journal of pediatric hematology/oncology 20070501

• [A severe disabled case of incomplete Fanconi syndrome after discontinuation of carnitine supplementation during valproate sodium therapy].

  No to hattatsu = Brain and development 20070501

• [Glucose transponer type 1 deficiency síndrome (GLUT-1 SD) treated with ketogenic diet. Report of one case].

  Revista medica de Chile 20070501

• Analysis of cholinesterase binding to a carnitine-modified EQCM sensor.

  Biosensors & bioelectronics 20070415

• The level of adrenomedullin immunoreactivity in seminal fluid is higher in oligozoospermic subjects and correlates with semen biochemical parameters.

  European journal of obstetrics, gynecology, and reproductive biology 20070401

• The effect of L-carnitine in the prevention of ionizing radiation-induced cataracts: a rat model.

  Graefe's archive for clinical and experimental ophthalmology = Albrecht von Graefes Archiv fur klinische und experimentelle Ophthalmologie 20070401

• Expanded newborn screening identifies maternal primary carnitine deficiency.

  Molecular genetics and metabolism 20070401

• Long-term stability of amino acids and acylcarnitines in dried blood spots.

  Clinical chemistry 20070401

• Carnitine revisited: potential use as adjunctive treatment in diabetes.

  Diabetologia 20070401

• The use of carnitine in pediatric nutrition.

  Nutrition in clinical practice : official publication of the American Society for Parenteral and Enteral Nutrition 20070401

• The possible protective effect of L-carnitine on tilmicosin-induced cardiotoxicity in mice.

  Journal of veterinary medicine. A, Physiology, pathology, clinical medicine 20070401

• Mechanistic analysis for drug permeation through intestinal membrane.

  Drug metabolism and pharmacokinetics 20070401

• Carnitine as an antidote for acute valproate toxicity in children.

  Current opinion in pediatrics 20070401

• Ghrelin reduces hepatic mitochondrial fatty acid beta oxidation.

  Journal of endocrinological investigation 20070401

• Fructose-induced hepatic gluconeogenesis: effect of L-carnitine.

  Life sciences 20070306

• Salt stress effects on the central and carnitine metabolisms of Escherichia coli.

  Biotechnology and bioengineering 20070301

• Effect of L-carnitine administration on erythropoietin use in thalassemic minor haemodialysis patients.

  Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20070301

• Carbohydrate ingestion augments L-carnitine retention in humans.

  Journal of applied physiology (Bethesda, Md. : 1985) 20070301

• Determination of free L-carnitine in human seminal plasma by high performance liquid chromatography with pre-column ultraviolet derivatization and its clinical application in male infertility.

  Clinica chimica acta; international journal of clinical chemistry 20070301

• SUCLA2 mutations are associated with mild methylmalonic aciduria, Leigh-like encephalomyopathy, dystonia and deafness.

  Brain : a journal of neurology 20070301

• Carnitine deficiency provokes cisplatin-induced hepatotoxicity in rats.

  Basic & clinical pharmacology & toxicology 20070301

• A critical review of complementary therapies for cancer-related fatigue.

  Integrative cancer therapies 20070301

• Chemical knockout of pantothenate kinase reveals the metabolic and genetic program responsible for hepatic coenzyme A homeostasis.

  Chemistry & biology 20070301

• Natural approaches to epilepsy.

  Alternative medicine review : a journal of clinical therapeutic 20070301

• Differential expression of HSP70 and ultrastructure of heart and liver tissues of rats treated with adriamycin: protective role of L-carnitine.

  Investigacion clinica 20070301

• Effects of L-carnitine on RBC membrane composition and function in hyperinsulinemic rats.

  The Italian journal of biochemistry 20070301

• Propionyl-L-carnitine reduces proliferation and potentiates Bax-related apoptosis of aortic intimal smooth muscle cells by modulating nuclear factor-kappaB activity.

  The Journal of biological chemistry 20070216

• Concentrations of carnitine, glutamate and myo-inositol in epididymal fluid and spermatozoa from boars.

  Animal reproduction science 20070201

• An in vivo and in vitro study of erythrocyte membrane acetylcholinesterase, (Na+, K+)-ATPase and Mg2+-ATPase activities in basketball players on alpha-tocopherol supplementation. The role of L-carnitine.

  Clinical nutrition (Edinburgh, Scotland) 20070201

• Genetic mutation profile of isovaleric acidemia patients in Taiwan.

  Molecular genetics and metabolism 20070201

• A threshold exists for the stimulatory effect of insulin on plasma L-carnitine clearance in humans.

  American journal of physiology. Endocrinology and metabolism 20070201

• Increased lipolysis in LCHAD deficiency.

  Journal of inherited metabolic disease 20070201

• Mitigation of age-dependent oxidative damage to DNA in rat heart by carnitine and lipoic acid.

  Mechanisms of ageing and development 20070201

• Key role of insulin resistance in vascular injury among hemodialysis patients.

  Metabolism: clinical and experimental 20070201

• Modulation of p38 mitogen-activated protein kinase cascade and metalloproteinase activity in diaphragm muscle in response to free radical scavenger administration in dystrophin-deficient Mdx mice.

  The American journal of pathology 20070201

• Development of a newborn screening follow-up algorithm for the diagnosis of isobutyryl-CoA dehydrogenase deficiency.

  Genetics in medicine : official journal of the American College of Medical Genetics 20070201

• Responses of criterion variables to different supplemental doses of L-carnitine L-tartrate.

  Journal of strength and conditioning research 20070201

• [Level of free L-carnitine in human seminal plasma and its correlation with semen quality].

  Zhonghua nan ke xue = National journal of andrology 20070201

• Effects of dietary L-carnitine and coenzyme Q10 at different supplemental ages on growth performance and some immune response in ascites-susceptible broilers.

  Archives of animal nutrition 20070201

• 2-methylbutyryl-CoA dehydrogenase deficiency in Hmong infants identified by expanded newborn screen.

  WMJ : official publication of the State Medical Society of Wisconsin 20070201

• Changes of cholinesterase activities in the plasma and some tissues following administration of L-carnitine and galanthamine to rats.

  Neuroscience letters 20070116

• L-carnitine protects neurons from 1-methyl-4-phenylpyridinium-induced neuronal apoptosis in rat forebrain culture.

  Neuroscience 20070105

• Comparison of melatonin, vitamin E and L-carnitine in the treatment of neuro- and hepatotoxicity induced by thioacetamide.

  Cell biochemistry and function 20070101

• Carnitine: a therapeutic option for childhood psoriatic onycho-pachydermo-periostitis (POPP).

  Clinical rheumatology 20070101

• Intermittent hypobaric hypoxia-induced oxidative stress in rat erythrocytes: protective effects of vitamin E, vitamin C, and carnitine.

  Cell biochemistry and function 20070101

• Effect of temperature on the stability of long-chain acylcarnitines in human blood prior to plasma separation.

  Clinica chimica acta; international journal of clinical chemistry 20070101

• Protective effect of L-carnitine on testicular ischaemia-reperfusion injury in rats.

  Cell biochemistry and function 20070101

• Epithelial organic cation transporters ensure pH-dependent drug absorption in the airway.

  American journal of respiratory cell and molecular biology 20070101

• L-Carnitine L-tartrate (LCLT) and dehydroepiandrosterone sulfate (DHEAS) affect red and white blood cells in aged Sprague-Dawley rats.

  Archives of gerontology and geriatrics 20070101

• Cellular properties of human erythrocytes preserved in saline-adenine-glucose-mannitol in the presence of L-carnitine.

  American journal of hematology 20070101

• Effect of L-carnitine on the physical fitness of thalassemic patients.

  Annals of hematology 20070101

• Metabolic and genetic regulation of cardiac energy substrate preference.

  Comparative biochemistry and physiology. Part A, Molecular & integrative physiology 20070101

• Effect of L-carnitine supplementation and aerobic training on FABPc content and beta-HAD activity in human skeletal muscle.

  European journal of applied physiology 20070101

• Effects of beta-alanine supplementation on the onset of neuromuscular fatigue and ventilatory threshold in women.

  Amino acids 20070101

• Identification of novel mutations of the HADHA and HADHB genes in patients with mitochondrial trifunctional protein deficiency.

  International journal of molecular medicine 20070101

• Myocardial function, energy provision, and carnitine deficiency in experimental uremia.

  Journal of the American Society of Nephrology : JASN 20070101

• Advances in carnitine in chronic uremia.

  Journal of renal nutrition : the official journal of the Council on Renal Nutrition of the National Kidney Foundation 20070101

• Effects of valproate on acylcarnitines in children with epilepsy using ESI-MS/MS.

  Epilepsia 20070101

• OCTN2-mediated carnitine uptake in a newly discovered human proximal tubule cell line (Caki-1).

  Molecular pharmaceutics 20070101

• Simultaneous quantification of acylcarnitine isomers containing dicarboxylic acylcarnitines in human serum and urine by high-performance liquid chromatography/electrospray ionization tandem mass spectrometry.

  Rapid communications in mass spectrometry : RCM 20070101

• L-Propionyl carnitine, homocysteine and S-adenosylhomocysteine in hemodialysis.

  Journal of nephrology 20070101

• Effect of a single IV administration of L-propionylcarnitine on myocardial microcirculation assessed by coronary flow velocity reserve measurement in patients with systemic sclerosis: a pilot study.

  Clinical therapeutics 20070101

• Restoration of cellular energetic balance with L-carnitine in the neuro-bioenergetic approach for cancer prevention and treatment.

  Medical hypotheses 20070101

• Effect of L-carnitine and/or L-acetyl-carnitine in nutrition treatment for male infertility: a systematic review.

  Asia Pacific journal of clinical nutrition 20070101

• Assays of fatty acid beta-oxidation activity.

  Methods in cell biology 20070101

• Comparison of the effects of captopril, tamoxifen and L-carnitine on renal structure and fibrosis after total unilateral ureteral obstruction in the rat.

  Scandinavian journal of urology and nephrology 20070101

• Refractory seizures associated with an organic aciduria in a dog.

  Journal of the American Animal Hospital Association 20070101

• Effect of L-carnitine and propionyl-L-carnitine on endothelial function of small mesenteric arteries from SHR.

  Journal of vascular research 20070101

• High doses of stavudine induce fat wasting and mild liver damage without impairing mitochondrial respiration in mice.

  Antiviral therapy 20070101

• Transport of organic cations across the blood-testis barrier.

  Molecular pharmaceutics 20070101

• Effect of L-carnitine on skeletal muscle lipids and oxidative stress in rats fed high-fructose diet.

  Experimental diabetes research 20070101

• [Combined therapy with L-carnitine and erythropoietin of anemia in chronic kidney failure patients undergoing hemodialysis].

  Polskie Archiwum Medycyny Wewnetrznej 20070101

• Transient multiple acyl-CoA dehydrogenation deficiency in a newborn female caused by maternal riboflavin deficiency.

  Molecular genetics and metabolism 20070101

• A case of early diagnosed carnitine deficiency presenting with respiratory symptoms.

  Annals of nutrition & metabolism 20070101

• Role of wet experiment design in data generation: from in vivo to in silico and back.

  In silico biology 20070101

• [Secondary mitochondrial dysfunction in the pathogenesis of acute myocardial dysfunction: possibilities of diagnostics and principles of medication].

  Klinicheskaia meditsina 20070101

• [Experimental study of the effects of metabolic drugs on exercise tolerance].

  Voprosy kurortologii, fizioterapii, i lechebnoi fizicheskoi kultury 20070101

• Effect of L-carnitine supplementation on endurance exercise in normobaric/normoxic and hypobaric/hypoxic conditions.

  Wilderness & environmental medicine 20070101

• Impairing and monitoring glucose catabolite repression in L-carnitine biosynthesis.

  Biotechnology progress 20070101

• [The effect of mildronate and related substances on levels of thyroid hormones and some intermediates of lipid and carbohidrate metabolism in the hyperthyroid and hypothyroid rats].

  Biomeditsinskaia khimiia 20070101

• ENU mutagenesis identifies mice with cardiac fibrosis and hepatic steatosis caused by a mutation in the mitochondrial trifunctional protein beta-subunit.

  Human molecular genetics 20061215

• Co-regulation of dopamine D1 receptor and uncoupling protein-2 expression in 3-nitropropionic acid-induced neurotoxicity: neuroprotective role of L-carnitine.

  Neuroscience letters 20061213

• Encephalopathy due to carnitine deficiency in an adult patient with gluten enteropathy.

  Clinical neurology and neurosurgery 20061201

• Carnitine supplementation in premature neonates: effect on plasma and red blood cell total carnitine concentrations, nutrition parameters and morbidity.

  Clinical nutrition (Edinburgh, Scotland) 20061201

• Acute administration of 3-nitropropionic acid, a reactive oxygen species generator, boosts ethanol-induced locomotor stimulation. New support for the role of brain catalase in the behavioural effects of ethanol.

  Neuropharmacology 20061201

• An acute increase in skeletal muscle carnitine content alters fuel metabolism in resting human skeletal muscle.

  The Journal of clinical endocrinology and metabolism 20061201

• Studies on the critical micellar concentration and phase transitions of stearoylcarnitine.

  Bioscience reports 20061201

• Evaluation of the antineoplastic activity of mitoxantrone-L-carnitine combination therapy on an experimental solid form of ehrlich tumour in mice.

  Pharmacological research 20061201

• Carnitine-esters from the mushroom Suillus laricinus.

  Phytochemistry 20061201

• Experimental colitis: decreased Octn2 and Atb0+ expression in rat colonocytes induces carnitine depletion that is reversible by carnitine-loaded liposomes.

  FASEB journal : official publication of the Federation of American Societies for Experimental Biology 20061201

• Effects of L-carnitine supplementation in pregnant sows on plasma concentrations of insulin-like growth factors, various hormones and metabolites and chorion characteristics.

  Journal of animal physiology and animal nutrition 20061201

• Metabolic effects of abomasal L-carnitine infusion and feed restriction in lactating Holstein cows.

  Journal of dairy science 20061201

• Safety, tolerability and symptom outcomes associated with L-carnitine supplementation in patients with cancer, fatigue, and carnitine deficiency: a phase I/II study.

  Journal of pain and symptom management 20061201

• Effect of galantamine on acetylcholinesterase and butyrylcholinesterase activities in the presence of L-carnitine in rat selected brain and peripheral tissues.

  Neuro endocrinology letters 20061201

• Leigh syndrome with nephropathy and CoQ10 deficiency due to decaprenyl diphosphate synthase subunit 2 (PDSS2) mutations.

  American journal of human genetics 20061201

• Carnitine'S protective effect on oxidative stress is mediated by heme oxygenase-1.

  Nephrology (Carlton, Vic.) 20061201

• Mildronate, an inhibitor of carnitine biosynthesis, induces an increase in gamma-butyrobetaine contents and cardioprotection in isolated rat heart infarction.

  Journal of cardiovascular pharmacology 20061201

• Human embryonic stem cell-derived cardiomyocytes can be maintained in defined medium without serum.

  Stem cells and development 20061201

• Influence of hematocrit and localisation of punch in dried blood spots on levels of amino acids and acylcarnitines measured by tandem mass spectrometry.

  Clinica chimica acta; international journal of clinical chemistry 20061101

• Effects of L-carnitine infusions on inflammatory and nutritional markers in haemodialysis patients.

  Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20061101

• PDZ adaptor protein PDZK2 stimulates transport activity of organic cation/carnitine transporter OCTN2 by modulating cell surface expression.

  Drug metabolism and disposition: the biological fate of chemicals 20061101

• Acute renal failure due to phenazopyridine (Pyridium) overdose: case report and review of the literature.

  Pediatric nephrology (Berlin, Germany) 20061101

• Picolinyl ester fragmentation mechanism studies with application to the identification of acylcarnitine acyl groups following transesterification.

  Journal of the American Society for Mass Spectrometry 20061101

• Role of energetic coenzyme pools in the production of L-carnitine by Escherichia coli.

  Metabolic engineering 20061101

• Mechanism of the inhibitory effect of zwitterionic drugs (levofloxacin and grepafloxacin) on carnitine transporter (OCTN2) in Caco-2 cells.

  Biochimica et biophysica acta 20061101

• Functional genetic diversity in the high-affinity carnitine transporter OCTN2 (SLC22A5).

  Molecular pharmacology 20061101

• Smelling like dead fish: a case of trimethylaminuria in an adolescent.

  Clinical pediatrics 20061101

• Taurine and carnitine in canine cardiomyopathy.

  The Veterinary clinics of North America. Small animal practice 20061101

• Tandem mass neonatal screening in Taiwan--report from one center.

  Journal of the Formosan Medical Association = Taiwan yi zhi 20061101

• Late-onset multiple acyl-CoA dehydrogenase deficiency: a frequently missed diagnosis?

  Neurology 20061024

• Efficacy and tolerability of combined treatment with L-carnitine and simvastatin in lowering lipoprotein(a) serum levels in patients with type 2 diabetes mellitus.

  Atherosclerosis 20061001

• Carnitine transporter defect: diagnosis in asymptomatic adult women following analysis of acylcarnitines in their newborn infants.

  Journal of inherited metabolic disease 20061001

• Risk assessment for carnitine.

  Regulatory toxicology and pharmacology : RTP 20061001

• Persistent increase of plasma butyryl/isobutyrylcarnitine concentrations as marker of SCAD defect and ethylmalonic encephalopathy.

  Journal of inherited metabolic disease 20061001

• Drug therapy for idiopathic male infertility: rationale versus evidence.

  The Journal of urology 20061001

• The sigma factor RpoN (sigma54) is involved in osmotolerance in Listeria monocytogenes.

  FEMS microbiology letters 20061001

• Pathogenesis of cardiac conduction disorders in children genetic and histopathologic aspects.

  American journal of medical genetics. Part A 20061001

• Prolonged moderate-intensity exercise without and with L-carnitine supplementation in patients with MCAD deficiency.

  Journal of inherited metabolic disease 20061001

• Determination of free and total carnitine in plasma by an enzymatic reaction and spectrophotometric quantitation spectrophotometric determination of carnitine.

  Clinical biochemistry 20061001

• Disposition and metabolite kinetics of oral L-carnitine in humans.

  Journal of clinical pharmacology 20061001

• Normal muscle respiratory chain enzymes can complicate mitochondrial disease diagnosis.

  Pediatric neurology 20061001

• Free carnitine levels in respiratory distress syndrome during the first week of life.

  American journal of perinatology 20061001

• Susceptibility of human metabolic phenotypes to dietary modulation.

  Journal of proteome research 20061001

• Prolonged effect of single carnitine administration on fasted carnitine-deficient JVS mice regarding their locomotor activity and energy expenditure.

  Biochimica et biophysica acta 20061001

• Carnitine does not improve weight loss outcomes in valproate-treated bipolar patients consuming an energy-restricted, low-fat diet.

  Bipolar disorders 20061001

• Effects of methionine and betaine supplementation on growth performance, carcase composition and metabolism of lipids in male broilers.

  British poultry science 20061001

• Mutation in an adaptor protein PDZK1 affects transport activity of organic cation transporter OCTNs and oligopeptide transporter PEPT2.

  Drug metabolism and pharmacokinetics 20061001

• Oral L-carnitine: metabolite formation and hemodialysis.

  Current drug metabolism 20061001

• Effects of L-, D-, and DL-carnitine on morphometric parameters of skeletal muscle and exercise performance of laboratory animals receiving carnitine-deficient diet.

  Bulletin of experimental biology and medicine 20061001

• Crystal structures of murine carnitine acetyltransferase in ternary complexes with its substrates.

  The Journal of biological chemistry 20060922

• Dietary antioxidants and behavioral enrichment enhance neutrophil phagocytosis in geriatric Beagles.

  Veterinary immunology and immunopathology 20060915

• Effect of L-carnitine administration on erythrocyte survival in haemodialysis patients.

  Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20060901

• Organic cation/carnitine transporter OCTN2 (Slc22a5) is responsible for carnitine transport across apical membranes of small intestinal epithelial cells in mouse.

  Molecular pharmacology 20060901

• Taurine rescues hippocampal long-term potentiation from ammonia-induced impairment.

  Neurobiology of disease 20060901

• Short-term effects of nocturnal haemodialysis on carnitine metabolism.

  Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20060901

• Variations in IBD (ACAD8) in children with elevated C4-carnitine detected by tandem mass spectrometry newborn screening.

  Pediatric research 20060901

• [Optimum preparation of levocarnitine chloride solution in the hospital pharmacy].

  Yakugaku zasshi : Journal of the Pharmaceutical Society of Japan 20060901

• Imbalance between nitric oxide generation and oxidative stress in patients with peripheral arterial disease: effect of an antioxidant treatment.

  Journal of vascular surgery 20060901

• Neonatal screening for very long-chain acyl-coA dehydrogenase deficiency: enzymatic and molecular evaluation of neonates with elevated C14:1-carnitine levels.

  Pediatrics 20060901

• [Progress of researches on carnitines in the clinical therapy of andrology].

  Zhonghua nan ke xue = National journal of andrology 20060901

• Clinical, biochemical, and genetic heterogeneity in short-chain acyl-coenzyme A dehydrogenase deficiency.

  JAMA 20060823

• L-carnitine is synthesized in the human fetal-placental unit: potential roles in placental and fetal metabolism.

  Placenta 20060801

• Protective effect of L-carnitine against bilirubin-induced neuronal cell death.

  Brain & development 20060801

• Time course of acylcarnitine elevation in neonatal intrahepatic cholestasis caused by citrin deficiency.

  Journal of inherited metabolic disease 20060801

• Involvement of recognition and interaction of carnitine transporter in the decrease of L-carnitine concentration induced by pivalic acid and valproic acid.

  Pharmaceutical research 20060801

• Pericardial effusion in primary systemic carnitine deficiency.

  Journal of inherited metabolic disease 20060801

• Investigational agents for sickle cell disease.

  Expert opinion on investigational drugs 20060801

• L-carnitine ameliorates doxorubicin-induced nephrotic syndrome in rats.

  Nephrology (Carlton, Vic.) 20060801

• Carnitine esters prevent oxidative stress damage and energy depletion following transient forebrain ischaemia in the rat hippocampus.

  Clinical and experimental pharmacology & physiology 20060801

• Nutrient composition and concentrations of immunoglobulins in milk of sows supplemented with L-carnitine.

  Archives of animal nutrition 20060801

• L-carnitine supplementation of sows during pregnancy improves the suckling behaviour of their offspring.

  The British journal of nutrition 20060801

• [Carnitines and male reproduction].

  Zhonghua nan ke xue = National journal of andrology 20060801

• [Change of concentration of L-carnitine in blood and other tissues in rats on a background of the alcohol intake and influence of mildronate on its level].

  Georgian medical news 20060801

• Effects of L-carnitine pretreatment in methamphetamine and 3-nitropropionic acid-induced neurotoxicity.

  Annals of the New York Academy of Sciences 20060801

• Decrease of serum carnitine levels in patients with or without gastrointestinal cancer cachexia.

  World journal of gastroenterology 20060728

• Novel localization of OCTN1, an organic cation/carnitine transporter, to mammalian mitochondria.

  Biochemical and biophysical research communications 20060714

• Evidence for rapid inter- and intramolecular chlorine transfer reactions of histamine and carnosine chloramines: implications for the prevention of hypochlorous-acid-mediated damage.

  Biochemistry 20060704

• Plasma free carnitine in epilepsy children, adolescents and young adults treated with old and new antiepileptic drugs with or without ketogenic diet.

  Brain & development 20060701

• Possible mechanism for species difference on the toxicity of pivalic acid between dogs and rats.

  Toxicology and applied pharmacology 20060701

• Effect of L-carnitine supplementation on xenobiotic-metabolizing hepatic enzymes exposed to methanol.

  Experimental and toxicologic pathology : official journal of the Gesellschaft fur Toxikologische Pathologie 20060701

• Monitoring of ketogenic diet for carnitine metabolites by subcutaneous microdialysis.

  Pediatric research 20060701

• Measurement of carnitine biosynthesis enzyme activities by tandem mass spectrometry: differences between the mouse and the rat.

  Analytical biochemistry 20060701

• Valproate-induced hyperammonemic encephalopathy.

  Acta neurologica Scandinavica 20060701

• Antimyopathic effects of carnitine and nicotine.

  Current opinion in clinical nutrition and metabolic care 20060701

• Host invasion during rice-blast disease requires carnitine-dependent transport of peroxisomal acetyl-CoA.

  Molecular microbiology 20060701

• Androgenic responses to resistance exercise: effects of feeding and L-carnitine.

  Medicine and science in sports and exercise 20060701

• Pitfalls of neonatal screening for very-long-chain acyl-CoA dehydrogenase deficiency using tandem mass spectrometry.

  The Journal of pediatrics 20060701

• L-carnitine and alpha-lipoic acid improve age-associated decline in mitochondrial respiratory chain activity of rat heart muscle.

  The journals of gerontology. Series A, Biological sciences and medical sciences 20060701

• [Apoptosis of epididymal epithelium and the content of epididymal carnitine following testicular torsion/detorsion in rats].

  Zhonghua nan ke xue = National journal of andrology 20060701

• Effects of resistance exercise and growth hormone administration at low doses on lipid metabolism in middle-aged female rats.

  European journal of pharmacology 20060606

• Glucose and leucine kinetics in idiopathic ketotic hypoglycaemia.

  Archives of disease in childhood 20060601

• Effect of PLC on functional parameters and oxidative profile in type 2 diabetes-associated PAD.

  Diabetes research and clinical practice 20060601

• Oxidative stress-mediated macromolecular damage and dwindle in antioxidant status in aged rat brain regions: role of L-carnitine and DL-alpha-lipoic acid.

  Clinica chimica acta; international journal of clinical chemistry 20060601

• VLCAD deficiency: pitfalls in newborn screening and confirmation of diagnosis by mutation analysis.

  Molecular genetics and metabolism 20060601

• Combined therapy with PPARalpha agonist and L-carnitine rescues lipotoxic cardiomyopathy due to systemic carnitine deficiency.

  Cardiovascular research 20060601

• Pharmacological rescue of carnitine transport in primary carnitine deficiency.

  Human mutation 20060601

• Carnitine deficiency, mitochondrial metabolism, and abnormal response to anesthetics.

  Anesthesiology 20060601

• [Vas-to-Epididymis antidromic injection of 30% ethanol reduces sperm motility in rats].

  Zhonghua nan ke xue = National journal of andrology 20060601

• Abnormal increase in the expression level of proliferating cell nuclear antigen (PCNA) in the liver and hepatic injury in rats with dietary cobalamin deficiency.

  Journal of nutritional science and vitaminology 20060601

• Beef extract supplementation increases leg muscle mass and modifies skeletal muscle fiber types in rats.

  Journal of nutritional science and vitaminology 20060601

• Effects of chronic betaine ingestion on methionine-loading induced plasma homocysteine elevation in rats.

  Journal of nutritional science and vitaminology 20060601

• Glutaric acidemia type 1.

  American journal of medical genetics. Part C, Seminars in medical genetics 20060515

• Disorders of carnitine transport and the carnitine cycle.

  American journal of medical genetics. Part C, Seminars in medical genetics 20060515

• Bile acylcarnitine profiles in pediatric liver disease do not interfere with the diagnosis of long-chain fatty acid oxidation defects.

  Clinica chimica acta; international journal of clinical chemistry 20060501

• Fasting-induced reduction in locomotor activity and reduced response of orexin neurons in carnitine-deficient mice.

  Neuroscience research 20060501

• Measurement of the energy-generating capacity of human muscle mitochondria: diagnostic procedure and application to human pathology.

  Clinical chemistry 20060501

• Intracerebral accumulation of glutaric and 3-hydroxyglutaric acids secondary to limited flux across the blood-brain barrier constitute a biochemical risk factor for neurodegeneration in glutaryl-CoA dehydrogenase deficiency.

  Journal of neurochemistry 20060501

• Carnitine for the treatment of idiopathic asthenospermia: a randomized, double-blind, placebo-controlled trial.

  Fertility and sterility 20060501

• Microsphere-based protease assays and screening application for lethal factor and factor Xa.

  Cytometry. Part A : the journal of the International Society for Analytical Cytology 20060501

• II. Clinical practice guidelines and clinical practice recommendations for anemia in chronic kidney disease in adults.

  American journal of kidney diseases : the official journal of the National Kidney Foundation 20060501

• III. Clinical practice recommendations for anemia in chronic kidney disease in children.

  American journal of kidney diseases : the official journal of the National Kidney Foundation 20060501

• [Significance of serum carnitine in patients with liver diseases].

  Zhonghua gan zang bing za zhi = Zhonghua ganzangbing zazhi = Chinese journal of hepatology 20060501

• Asymptomatic cardiomyopathy in children and adolescents with type 1 diabetes mellitus: association of echocardiographic indicators with duration of diabetes mellitus and metabolic parameters.

  Journal of pediatric endocrinology & metabolism : JPEM 20060501

• Plasma free carnitine levels in 0-12-month-old infants in relation to feeding styles.

  International journal for vitamin and nutrition research. Internationale Zeitschrift fur Vitamin- und Ernahrungsforschung. Journal international de vitaminologie et de nutrition 20060501

• Glutaric aciduria types I and II.

  Brain & development 20060401

• Mitochondrial membrane damage during aging process in rat heart: potential efficacy of L-carnitine and DL alpha lipoic acid.

  Mechanisms of ageing and development 20060401

• So doctor, what exactly is wrong with my muscles? Glutaric aciduria type II presenting in a teenager.

  Neuromuscular disorders : NMD 20060401

• Functional expression of the organic cation/carnitine transporter 2 in rat astrocytes.

  Journal of neurochemistry 20060401

• Relationship between serum carnitine, acylcarnitines, and renal function in patients with chronic renal disease.

  Journal of renal nutrition : the official journal of the Council on Renal Nutrition of the National Kidney Foundation 20060401

• L-carnitine as an ergogenic aid for patients with chronic obstructive pulmonary disease submitted to whole-body and respiratory muscle training programs.

  Brazilian journal of medical and biological research = Revista brasileira de pesquisas medicas e biologicas 20060401

• A monotopic membrane protein goes solo.

  Structure (London, England : 1993) 20060401

• The crystal structure of carnitine palmitoyltransferase 2 and implications for diabetes treatment.

  Structure (London, England : 1993) 20060401

• Body composition, muscle fibre characteristics and postnatal growth capacity of pigs born from sows supplemented with L-carnitine.

  Archives of animal nutrition 20060401

• Results of a single blind, randomized, placebo-controlled clinical trial to study the effect of intravenous L-carnitine supplementation on health-related quality of life in Indian patients on maintenance hemodialysis.

  Indian journal of medical sciences 20060401

• Carnitine and lipoic acid alleviates protein oxidation in heart mitochondria during aging process.

  Biogerontology 20060401

• Oxidative stress and DNA single strand breaks in skeletal muscle of aged rats: role of carnitine and lipoicacid.

  Biogerontology 20060401

• Antioxidant activity of propionyl-L-carnitine in liver and heart of spontaneously hypertensive rats.

  Life sciences 20060320

• Effect of Shiga-like toxin II from Escherichia coli O157:H7 on intestinal clearance of norfloxacin in rats.

  Life sciences 20060320

• Carnitine/xenobiotics transporters in the human mammary gland epithelia, MCF12A.

  American journal of physiology. Regulatory, integrative and comparative physiology 20060301

• Modified and improved method for the measurement of plasma acylcarnitines by online extraction coupled to liquid chromatography-tandem mass spectrometry without derivatization.

  Clinica chimica acta; international journal of clinical chemistry 20060301

• Positive regulation of hepatic carnitine palmitoyl transferase 1A (CPT1A) activities by soy isoflavones and L-carnitine.

  European journal of nutrition 20060301

• The use of levo-carnitine in children with renal disease: a review and a call for future studies.

  Pediatric nephrology (Berlin, Germany) 20060301

• Propionyl-L-carnitine prevents the progression of cisplatin-induced cardiomyopathy in a carnitine-depleted rat model.

  Pharmacological research 20060301

• Neuroprotective effects of L-carnitine and vitamin E alone or in combination against ischemia-reperfusion injury in rats.

  The Journal of surgical research 20060301

• Changes in visual evoked potentials, lipid peroxidation and antioxidant enzymes in rats exposed to restraint stress: effect of L-carnitine.

  The International journal of neuroscience 20060301

• L-carnitine reduces severity of physical and mental fatigue and improves daily activities in the elderly.

  Southern medical journal 20060301

• Vitamin E and L-carnitine, separately or in combination, in the prevention of radiation-induced oral mucositis and myelosuppression: a controlled study in a rat model.

  Journal of radiation research 20060301

• Role of antioxidants, essential fatty acids, carnitine, vitamins, phytochemicals and trace elements in the treatment of diabetes mellitus and its chronic complications.

  Endocrine, metabolic & immune disorders drug targets 20060301

• Effects of L-carnitine on oxidant/antioxidant status in acetic acid-induced colitis.

  Digestive diseases and sciences 20060301

• Formaldehyde and some fully n-methylated substances in boar seminal fluids. Short communication.

  Acta biologica Hungarica 20060301

• Micronutrients and their supplementation in chronic cardiac failure. An update beyond theoretical perspectives.

  Heart failure reviews 20060301

• The management of conditioned nutritional requirements in heart failure.

  Heart failure reviews 20060301

• Oligomeric structure of the carnitine transporter CaiT from Escherichia coli.

  The Journal of biological chemistry 20060224

• [Three congenital metabolic diseases in the Faeroe Islands. Incidence, clinical and molecular genetic characteristics of Faeroese children with glycogen storage disease type IIIA, carnitine transporter deficiency and holocarboxylase synthetase deficiency].

  Ugeskrift for laeger 20060213

• Antioxidant effect of L-carnitine and its short chain esters: relevance for the protection from oxidative stress related cardiovascular damage.

  International journal of cardiology 20060208

• Effects of doxorubicin-containing chemotherapy and a combination with L-carnitine on oxidative metabolism in patients with non-Hodgkin lymphoma.

  Journal of cancer research and clinical oncology 20060201

• Effect of L-carnitine on the kinetics of carnitine, acylcarnitines and butyrobetaine in long-term haemodialysis.

  Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20060201

• Metabolic effects of intravenous LCT or MCT/LCT lipid emulsions in preterm infants.

  Journal of lipid research 20060201

• Measurement of stable isotopic enrichment and concentration of long-chain fatty acyl-carnitines in tissue by HPLC-MS.

  Journal of lipid research 20060201

• Biomarker discovery, disease classification, and similarity query processing on high-throughput MS/MS data of inborn errors of metabolism.

  Journal of biomolecular screening 20060201

• Insulin stimulates L-carnitine accumulation in human skeletal muscle.

  FASEB journal : official publication of the Federation of American Societies for Experimental Biology 20060201

• Carnitine treatment inhibits increases in cerebral carnitine esters and glutamate detected by mass spectrometry after hypoxia-ischemia in newborn rats.

  Stroke 20060201

• Acetylcarnitine and cellular stress response: roles in nutritional redox homeostasis and regulation of longevity genes.

  The Journal of nutritional biochemistry 20060201

• Falsely elevated C4-carnitine as expression of glutamate formiminotransferase deficiency in tandem mass spectrometry newborn screening.

  Journal of mass spectrometry : JMS 20060201

• Long-term effects of early-life dietary L-carnitine on lymphoid organs and immune responses in Leghorn-type chickens.

  Journal of animal physiology and animal nutrition 20060201

• Attenuation of cardiac hypertrophy in carnitine-deficient juvenile visceral steatosis (JVS) mice achieved by lowering dietary lipid.

  Journal of biochemistry 20060201

• Efficacy of l-carnitine administration on fatigue, nutritional status, oxidative stress, and related quality of life in 12 advanced cancer patients undergoing anticancer therapy.

  Nutrition (Burbank, Los Angeles County, Calif.) 20060201

• Does nutrition have a role in peripheral vascular disease?

  The British journal of nutrition 20060201

• Protective effect of L-propionylcarnitine in chronic cyclosporine-a induced nephrotoxicity.

  Biomedicine & pharmacotherapy = Biomedecine & pharmacotherapie 20060201

• Understanding and treating cancer-related fatigue.

  The journal of supportive oncology 20060201

• [Molecular mechanism in biological transport in the kidney: Organic cation/anion transporters].

  Nihon rinsho. Japanese journal of clinical medicine 20060201

• Refining the diagnosis of mitochondrial HMG-CoA synthase deficiency.

  Journal of inherited metabolic disease 20060201

• L-carnitine suppresses the onset of neuromuscular degeneration and increases the life span of mice with familial amyotrophic lateral sclerosis.

  Brain research 20060127

• Antioxidant and antiradical activities of L-carnitine.

  Life sciences 20060118

• Changes of plasma fasting carnitine ester profile in patients with ulcerative colitis.

  World journal of gastroenterology 20060107

• Is sudden death with vitamin C deficiency caused by lack of carnitine?

  Journal of clinical forensic medicine 20060101

• Effects of L-carnitine on neutrophil-mediated ischemia-reperfusion injury in rat stomach.

  Cell biochemistry and function 20060101

• Na+, K+ ATPase activity is markedly reduced by cis-4-decenoic acid in synaptic plasma membranes from cerebral cortex of rats.

  Experimental neurology 20060101

• In vivo release of non-neuronal acetylcholine from the human skin as measured by dermal microdialysis: effect of botulinum toxin.

  British journal of pharmacology 20060101

• Medium-chain acyl-CoA dehydrogenase deficiency: genotype-biochemical phenotype correlations.

  Molecular genetics and metabolism 20060101

• Differentiation of long-chain fatty acid oxidation disorders using alternative precursors and acylcarnitine profiling in fibroblasts.

  Molecular genetics and metabolism 20060101

• The protective effect of L-carnitine in peripheral blood human lymphocytes exposed to oxidative agents.

  Mutagenesis 20060101

• L-carnitine inhibits apoptotic DNA fragmentation induced by a new spin-labeled derivative of podophyllotoxin via caspase-3 in Raji cells.

  Oncology reports 20060101

• Debate forum: carnitine supplements have not been demonstrated as effective in patients on long-term dialysis therapy.

  Blood purification 20060101

• Carnitine treatment improved quality-of-life measure in a sample of Midwestern hemodialysis patients.

  JPEN. Journal of parenteral and enteral nutrition 20060101

• Supplemental conditionally essential nutrients in cardiovascular disease therapy.

  The Journal of cardiovascular nursing 20060101

• Systemic correction of a fatty acid oxidation defect by intramuscular injection of a recombinant adeno-associated virus vector.

  Human gene therapy 20060101

• Hsp70 accumulation and ultrastructural features of lung and liver induced by ethanol treatment with and without L-carnitine protection in rats.

  Experimental and toxicologic pathology : official journal of the Gesellschaft fur Toxikologische Pathologie 20060101

• Newer aspects of carnitine metabolism in uremia.

  Seminars in nephrology 20060101

• Cardio-protective effects of carnitine in streptozotocin-induced diabetic rats.

  Cardiovascular diabetology 20060101

• Diastolic dysfunction and pulmonary hypertension in sickle cell anemia: is there a role for L-carnitine treatment?

  Acta haematologica 20060101

• Protective effects of L-carnitine on myoglobinuric acute renal failure in rats.

  Clinical and experimental pharmacology & physiology 20060101

• L-Carnitine ameliorates methotrexate-induced oxidative organ injury and inhibits leukocyte death.

  Cell biology and toxicology 20060101

• Effect of propionylcarnitine on changes in endothelial function and plasma levels of adhesion molecules induced by acute exercise in patients with intermittent claudication.

  Angiology 20060101

• Managing erythropoietin hyporesponsiveness.

  Seminars in dialysis 20060101

• A randomised, controlled clinical trial evaluating changes in therapeutic efficacy and oxidative parameters after treatment with propionyl L-carnitine in patients with peripheral arterial disease requiring haemodialysis.

  Drugs & aging 20060101

• Assessing the properties of internal standards for quantitative matrix-assisted laser desorption/ionization mass spectrometry of small molecules.

  Rapid communications in mass spectrometry : RCM 20060101

• [Antioxidants, carnitine and erythropoietin].

  Giornale italiano di nefrologia : organo ufficiale della Societa italiana di nefrologia 20060101

• Direct determination of acylcarnitines in amniotic fluid by column-switching liquid chromatography with electrospray tandem mass spectrometry.

  Rapid communications in mass spectrometry : RCM 20060101

• Metabolic treatment with L-carnitine in acute anterior ST segment elevation myocardial infarction. A randomized controlled trial.

  Cardiology 20060101

• [Effect of L-carnitine to suppress the development of ischemic reperfusion injury in an excised heart of a diabetic rat].

  [Hokkaido igaku zasshi] The Hokkaido journal of medical science 20060101

• Serum carnitine levels in children with iron-deficiency anemia with or without pica.

  Pediatric hematology and oncology 20060101

• Hypocarnitinaemia induced by sodium pivalate in the rat is associated with left ventricular dysfunction and impaired energy metabolism.

  Drugs in R&D 20060101

• Carnitine supplementation induces long-chain acylcarnitine production--studies in the VLCAD-deficient mouse.

  Journal of inherited metabolic disease 20060101

• Newborn screening for medium-chain acyl-CoA dehydrogenase deficiency: a global perspective.

  Journal of inherited metabolic disease 20060101

• Neonatal screening for glutaric aciduria type I: strategies to proceed.

  Journal of inherited metabolic disease 20060101

• Certain aspects of uncoupling due to mitochondrial uncoupling proteins in vitro and in vivo.

  Biochimica et biophysica acta 20060101

• Propionyl-L-carnitine therapy: effects on endothelin-1 and homocysteine levels in patients with peripheral arterial disease and end-stage renal disease.

  Kidney & blood pressure research 20060101

• The protective effect of L-carnitine on ischemia-reperfusion heart.

  Journal of Huazhong University of Science and Technology. Medical sciences = Hua zhong ke ji da xue xue bao. Yi xue Ying De wen ban = Huazhong keji daxue xuebao. Yixue Yingdewen ban 20060101

• Metabolic control during exercise with and without medium-chain triglycerides (MCT) in children with long-chain 3-hydroxy acyl-CoA dehydrogenase (LCHAD) or trifunctional protein (TFP) deficiency.

  Molecular genetics and metabolism 20060101

• Measurement of carnitine in hemodialysis patients - adaptation of an enzymatic photometric method for an automatic analyzer.

  Clinical chemistry and laboratory medicine 20060101

• Dialysis-related carnitine disorder.

  Seminars in dialysis 20060101

• L-carnitine deficiency and red blood cell mechanical impairment in beta-thalassemia major.

  Clinical hemorheology and microcirculation 20060101

• [Comparative evaluation of the effects of carnitine stereoisomers and racemate on the cardio- and hemodynamics of rats on a carnitine-deficient diet].

  Vestnik Rossiiskoi akademii meditsinskikh nauk 20060101

• A retrospective epidemiological and etiological study of metabolic disorders in children with cardiomyopathies.

  Acta paediatrica Taiwanica = Taiwan er ke yi xue hui za zhi 20060101

• Relative bioavailability of carnitine supplementation in premature neonates.

  JPEN. Journal of parenteral and enteral nutrition 20060101

• [Asymptomatic carnitine depletion on ketogenic diet in patients with pharmacoresistant epilepsies].

  Klinische Padiatrie 20060101

• L-carnitine reduces cochlear damage induced by gamma irradiation in Guinea pigs.

  Annals of clinical and laboratory science 20060101

• How can erythropoietin requirements be reduced in dialysis patients?

  Seminars in dialysis 20060101

• Total carnitine and acylated carnitine ratio: relationship of free carnitine with lipid parameters in pediatric dialysis patients.

  Advances in peritoneal dialysis. Conference on Peritoneal Dialysis 20060101

• Frequency of low carnitine levels in children on dialysis.

  Advances in peritoneal dialysis. Conference on Peritoneal Dialysis 20060101

• [Reduction of hospitalization thanks to L-carnitine in hemodialyzed patients].

  Nefrologia : publicacion oficial de la Sociedad Espanola Nefrologia 20060101

• [Changes in myocardium, skeletal muscle and liver of rats fed carnitine-deficient diet and treated with carnitine optical isomers].

  Morfologiia (Saint Petersburg, Russia) 20060101

• Effect of genistein with carnitine administration on lipid parameters and obesity in C57Bl/6J mice fed a high-fat diet.

  Journal of medicinal food 20060101

• L-carnitine stimulates lipolysis via induction of the lipolytic gene expression and suppression of the adipogenic gene expression in 3T3-L1 adipocytes.

  Journal of medicinal food 20060101

• New treatments for chronic obstructive pulmonary disease using ergogenic aids.

  Jornal brasileiro de pneumologia : publicacao oficial da Sociedade Brasileira de Pneumologia e Tisilogia 20060101

• Gastroprotective effect of L-carnitine on indomethacin-induced gastric mucosal injury in rats: a preliminary study.

  Folia medica 20060101

• OCTN3 is a mammalian peroxisomal membrane carnitine transporter.

  Biochemical and biophysical research communications 20051230

• Effects of antioxidant therapy on leukocyte myeloperoxidase and Cu/Zn-superoxide dismutase and plasma malondialdehyde levels in experimental colitis.

  Mediators of inflammation 20051214

• Effects of L-carnitine in patients with hepatic encephalopathy.

  World journal of gastroenterology 20051207

• Acidified acetonitrile and methanol extractions for quantitative analysis of acylcarnitines in plasma by stable isotope dilution tandem mass spectrometry.

  Journal of chromatography. B, Analytical technologies in the biomedical and life sciences 20051205

• L -Carnitine and the recovery from exhaustive endurance exercise: a randomised, double-blind, placebo-controlled trial.

  European journal of applied physiology 20051201

• L-carnitine protects against glutamate- and kainic acid-induced neurotoxicity in cerebellar granular cell culture of rats.

  Brain & development 20051201

• Effect of aromatic ring-containing drugs on carnitine biosynthesis in rats with special regard to p-aminomethylbenzoic acid.

  Metabolism: clinical and experimental 20051201

• Age-associated deficit of mitochondrial oxidative phosphorylation in skeletal muscle: role of carnitine and lipoic acid.

  Molecular and cellular biochemistry 20051201

• Increased mitochondrial palmitoylcarnitine/carnitine countertransport by flavone causes oxidative stress and apoptosis in colon cancer cells.

  Cellular and molecular life sciences : CMLS 20051201

• Carnitine/organic cation transporter OCTN2-mediated transport of carnitine in primary-cultured epididymal epithelial cells.

  Reproduction (Cambridge, England) 20051201

• The effects of L-carnitine on sperm parameters in smoker and non-smoker patients with idiopathic sperm abnormalities.

  Journal of assisted reproduction and genetics 20051201

• Weight loss favorably modifies anthropometrics and reverses the metabolic syndrome in premenopausal women.

  Journal of the American College of Nutrition 20051201

• Metabolic modulators for chronic cardiac ischemia.

  Journal of cardiovascular pharmacology and therapeutics 20051201

• Effects of dietary ruminally protected L-carnitine on plasma metabolites in sheep following a sub-lethal ammonia challenge.

  Journal of animal physiology and animal nutrition 20051201

• Two newborns with nutritional vitamin B12 deficiency: challenges in newborn screening for vitamin B12 deficiency.

  Haematologica 20051201

• [Stereopharmacology of carnitine].

  Rossiiskii fiziologicheskii zhurnal imeni I.M. Sechenova 20051201

• Effects of four weeks L-carnitine L-tartrate ingestion on substrate utilization during prolonged exercise.

  International journal of sport nutrition and exercise metabolism 20051201

• Galantamine antiacetylcholinesterase activity in rat brain influenced by L-carnitine.

  Biomedical papers of the Medical Faculty of the University Palacky, Olomouc, Czechoslovakia 20051201

• Intestinal single-pass in situ perfusion technique in rat: the influence of L-carnitine on absorption of 7-methoxytacrine.

  Biomedical papers of the Medical Faculty of the University Palacky, Olomouc, Czechoslovakia 20051201

• Plasma carnitine ester profile in adult celiac disease patients maintained on long-term gluten free diet.

  World journal of gastroenterology 20051114

• L-Carnitine protects mammalian cells from chromosome aberrations but not from inhibition of cell proliferation induced by hydrogen peroxide.

  Mutation research 20051110

• Ammonia-mediated LTP inhibition: effects of NMDA receptor antagonists and L-carnitine.

  Neurobiology of disease 20051101

• Dietary fish oil attenuates cardiac hypertrophy in lipotoxic cardiomyopathy due to systemic carnitine deficiency.

  Cardiovascular research 20051101

• Determination of total and free plasma carnitine concentrations on the Dade Behring Dimension RxL: integrated chemistry system.

  Clinica chimica acta; international journal of clinical chemistry 20051101

• Unfolding and extraction of a transmembrane alpha-helical peptide: dynamic force spectroscopy and molecular dynamics simulations.

  Biophysical journal 20051101

• Novel metabolic and molecular findings in hepatic carnitine palmitoyltransferase I deficiency.

  Molecular genetics and metabolism 20051101

• Phase I and pharmacokinetic study of aplidine, a new marine cyclodepsipeptide in patients with advanced malignancies.

  Journal of clinical oncology : official journal of the American Society of Clinical Oncology 20051101

• Glutaryl-CoA dehydrogenase deficiency and newborn screening: retrospective analysis of a low excretor provides further evidence that some cases may be missed.

  Molecular genetics and metabolism 20051101

• Quantitative acylcarnitine profiling in peripheral blood mononuclear cells using in vitro loading with palmitic and 2-oxoadipic acids: biochemical confirmation of fatty acid oxidation and organic acid disorders.

  Pediatric research 20051101

• Mitochondrial efficiency in rat skeletal muscle: influence of respiration rate, substrate and muscle type.

  Acta physiologica Scandinavica 20051101

• Pivotal role of Harakiri in the induction and prevention of gentamicin-induced hearing loss.

  Proceedings of the National Academy of Sciences of the United States of America 20051101

• Acetyl-L-carnitine plus propionyl-L-carnitine improve efficacy of sildenafil in treatment of erectile dysfunction after bilateral nerve-sparing radical retropubic prostatectomy.

  Urology 20051101

• In vitro and in vivo studies on acyl-coenzyme A-dependent bioactivation of zomepirac in rats.

  Chemical research in toxicology 20051101

• Carnitine depletion in rat pups from mothers given mildronate: a model of carnitine deficiency in late fetal and neonatal life.

  Life sciences 20051028

• Effect of methanol on endogenous and exogenous carnitine levels in rat plasma.

  Archives of toxicology 20051001

• Efficacy of levo carnitine and alpha lipoic acid in ameliorating the decline in mitochondrial enzymes during aging.

  Clinical nutrition (Edinburgh, Scotland) 20051001

• Uptake of L-carnitine and its short-chain ester propionyl-L-carnitine in the isolated perfused rat liver.

  The Journal of pharmacology and experimental therapeutics 20051001

• Plasma and urinary carnitine and acylcarnitines in chronic fatigue syndrome.

  Clinica chimica acta; international journal of clinical chemistry 20051001

• Acquired carnitine deficiency: a clinical model for propofol infusion syndrome?

  Anesthesiology 20051001

• Prenatal and postnatal treatment in cobalamin C defect.

  The Journal of pediatrics 20051001

• Inflammation and perturbation of the l-carnitine system in heart failure.

  European journal of heart failure 20051001

• [A controlled randomized trial of the use of combined L-carnitine and acetyl-L-carnitine treatment in men with oligoasthenozoospermia].

  Zhonghua nan ke xue = National journal of andrology 20051001

• Adsorption of pesticides from water by functionalized organobentonites.

  Journal of agricultural and food chemistry 20050921

• Bezafibrate increases very-long-chain acyl-CoA dehydrogenase protein and mRNA expression in deficient fibroblasts and is a potential therapy for fatty acid oxidation disorders.

  Human molecular genetics 20050915

• L-carnitine and propionyl-L-carnitine improve endothelial dysfunction in spontaneously hypertensive rats: different participation of NO and COX-products.

  Life sciences 20050909

• Muscle carnitine in hypo- and hyperthyroidism.

  Muscle & nerve 20050901

• Effect of L-carnitine on acetyl-CoA content and activity of blood platelets in healthy and diabetic persons.

  Clinical chemistry 20050901

• Changes in the composition of carnitines in hemodialysis patients.

  Kidney international 20050901

• Weight loss associated with reduced intake of carbohydrate reduces the atherogenicity of LDL in premenopausal women.

  Metabolism: clinical and experimental 20050901

• Impact of haemodialysis on individual endogenous plasma acylcarnitine concentrations in end-stage renal disease.

  Annals of clinical biochemistry 20050901

• Placebo-controlled double-blind randomized trial on the use of L-carnitine, L-acetylcarnitine, or combined L-carnitine and L-acetylcarnitine in men with idiopathic asthenozoospermia.

  Fertility and sterility 20050901

• Effects of L-carnitine on thyroid hormone metabolism and on physical exercise tolerance.

  Hormone and metabolic research = Hormon- und Stoffwechselforschung = Hormones et metabolisme 20050901

• Roles of organic anion transporters (OATs) and a urate transporter (URAT1) in the pathophysiology of human disease.

  Clinical and experimental nephrology 20050901

• Oxidative stress and antioxidant status in rat blood, liver and muscle: effect of dietary lipid, carnitine and exercise.

  International journal for vitamin and nutrition research. Internationale Zeitschrift fur Vitamin- und Ernahrungsforschung. Journal international de vitaminologie et de nutrition 20050901

• Prenatal diagnosis for organic acid disorders using two mass spectrometric methods, gas chromatography mass spectrometry and tandem mass spectrometry.

  Journal of chromatography. B, Analytical technologies in the biomedical and life sciences 20050825

• L-carnitine inhibits hypoglycemia-induced brain damage in the rat.

  Brain research 20050816

• Clinical, pathological, and biochemical studies in a patient with propionic acidemia and fatal cardiomyopathy.

  Molecular genetics and metabolism 20050801

• L-carnitine and erythropoiesis: relationship with haeme oxygenase-1.

  Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20050801

• Effect of dietary L-carnitine supplementation on growth performance of piglets from control sows or sows treated with L-carnitine during pregnancy and lactation.

  Journal of animal physiology and animal nutrition 20050801

• Acute valproate poisoning: pharmacokinetics, alteration in fatty acid metabolism, and changes during therapy.

  Journal of clinical psychopharmacology 20050801

• Rapid measurement of plasma acylcarnitines by liquid chromatography-tandem mass spectrometry without derivatization.

  Clinica chimica acta; international journal of clinical chemistry 20050801

• Effects of L-carnitine on fetal growth and the IGF system in pigs.

  Journal of animal science 20050801

• Lethal cardiomyopathy in epidermolysis bullosa associated with amitriptyline.

  Archives of disease in childhood 20050801

• Effect of L-carnitine on diabetogenic action of streptozotocin in rats.

  Neuro endocrinology letters 20050801

• L-carnitine and neuroprotection in the animal model of mitochondrial dysfunction.

  Annals of the New York Academy of Sciences 20050801

• Effects of metabolic modifiers such as carnitines, coenzyme Q10, and PUFAs against different forms of neurotoxic insults: metabolic inhibitors, MPTP, and methamphetamine.

  Annals of the New York Academy of Sciences 20050801

• Propionyl-L-carnitine improves hemodynamics and metabolic markers of cardiac perfusion during coronary surgery in diabetic patients.

  Cardiovascular drugs and therapy 20050801

• Effects of acute versus chronic L-carnitine L-tartrate supplementation on metabolic responses to steady state exercise in males and females.

  International journal of sport nutrition and exercise metabolism 20050801

• Capillary electrophoresis determination of carnitine in food supplements.

  Journal of chromatography. A 20050715

• [Treatment of symptomatic hyperlactatemia and lactic acidosis in HIV+ patients under nucleoside reverse transcriptase inhibitors].

  Medicina clinica 20050709

• Mitochondrial glycerol-3-phosphate acyltransferase-1 is essential in liver for the metabolism of excess acyl-CoAs.

  The Journal of biological chemistry 20050708

• L-Carnitine halts apoptosis and myelosuppression induced by carboplatin in rat bone marrow cell cultures (BMC).

  Archives of toxicology 20050701

• Lack of effect of L-carnitine supplementation on weight gain in very preterm infants.

  Journal of perinatology : official journal of the California Perinatal Association 20050701

• Effect of L-carnitine during storage of buffy-coat platelet concentrates in an additive solution.

  Vox sanguinis 20050701

• The challenges of serial time dependent data?

  Fertility and sterility 20050701

• [L-carnitine in the treatment of liver diseases].

  Zhonghua gan zang bing za zhi = Zhonghua ganzangbing zazhi = Chinese journal of hepatology 20050701

• Developmental maturation and segmental distribution of rat small intestinal L-carnitine uptake.

  The Journal of membrane biology 20050701

• Late-onset neurologic disease in glutaryl-CoA dehydrogenase deficiency.

  Neurology 20050628

• L-carnitine and creatine in Friedreich's ataxia. A randomized, placebo-controlled crossover trial.

  Journal of neural transmission (Vienna, Austria : 1996) 20050601

• Mitochondrial tissue specificity of substrates utilization in rat cardiac and skeletal muscles.

  Journal of cellular physiology 20050601

• Tissue carnitine homeostasis in very-long-chain acyl-CoA dehydrogenase-deficient mice.

  Pediatric research 20050601

• Constitutive UCP3 overexpression at physiological levels increases mouse skeletal muscle capacity for fatty acid transport and oxidation.

  FASEB journal : official publication of the Federation of American Societies for Experimental Biology 20050601

• The prooxidant effect of sodium metabisulfite in rat liver and kidney.

  Regulatory toxicology and pharmacology : RTP 20050601

• In vitro correction of medium chain acyl CoA dehydrogenase deficiency with a recombinant adenoviral vector.

  Molecular genetics and metabolism 20050601

• L-carnitine and isovaleryl L-carnitine fumarate positively affect human osteoblast proliferation and differentiation in vitro.

  Calcified tissue international 20050601

• The additive effects of carnitine and ascorbic acid on distally burned dorsal skin flap in rats.

  Medical science monitor : international medical journal of experimental and clinical research 20050601

• Myocardial metabolism and improved outcomes after high risk heart surgery.

  Seminars in cardiothoracic and vascular anesthesia 20050601

• OCTN2-mediated transport of carnitine in isolated Sertoli cells.

  Reproduction (Cambridge, England) 20050601

• Decreasing oxidative stress with choline and carnitine in women.

  Journal of the American College of Nutrition 20050601

• Ontogeny and kinetics of carnitine palmitoyltransferase in liver and skeletal muscle of the domestic felid (Felis domestica).

  The Journal of nutritional biochemistry 20050601

• [Macrocephaly the first manifestation of glutaric aciduria type I: the importance of early diagnosis].

  Neurologia (Barcelona, Spain) 20050601

• Prediction of genotoxicity of chemical compounds by statistical learning methods.

  Chemical research in toxicology 20050601

• The effect of oral L-carnitine supplementation on the lipid profiles of hyperlipidaemic children.

  Acta paediatrica (Oslo, Norway : 1992) 20050601

• Identification by site-directed mutagenesis and chemical modification of three vicinal cysteine residues in rat mitochondrial carnitine/acylcarnitine transporter.

  The Journal of biological chemistry 20050520

• Inhibition of very long chain acyl-CoA dehydrogenase during cardiac ischemia.

  Archives of biochemistry and biophysics 20050515

• Differential carnitine/acylcarnitine translocase expression defines distinct metabolic signatures in skeletal muscle cells.

  Journal of cellular physiology 20050501

• Effect of L-carnitine on erythroid colony formation in mouse bone marrow cells.

  Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20050501

• Identification of ethylsuccinylcarnitine present in some human urines.

  Clinica chimica acta; international journal of clinical chemistry 20050501

• Oxidative stress on mitochondrial antioxidant defense system in the aging process: role of DL-alpha-lipoic acid and L-carnitine.

  Clinica chimica acta; international journal of clinical chemistry 20050501

• L-carnitine could not improve hepatic warm ischemia-reperfusion injury despite ameliorated blood flow.

  The Journal of surgical research 20050501

• [Glutaric aciduria type 1 with normal evolution: follow-up of one case until adult age].

  Neurologia (Barcelona, Spain) 20050501

• L-carnitine was safely administered in the setting of valproate toxicity.

  The American journal of emergency medicine 20050501

• Pregnancy increases urinary loss of carnitine and reduces plasma carnitine in Korean women.

  The British journal of nutrition 20050501

• Effects of L-carnitine supplementation on milk production, litter gains and back-fat thickness in sows with a low energy and protein intake during lactation.

  The British journal of nutrition 20050501

• Carnitine levels in valproic acid-treated psychiatric patients: a cross-sectional study.

  The Journal of clinical psychiatry 20050501

• Inflammation and endothelial dysfunction as therapeutic targets in patients with heart failure.

  International journal of cardiology 20050428

• Crystal structure of Escherichia coli crotonobetainyl-CoA: carnitine CoA-transferase (CaiB) and its complexes with CoA and carnitinyl-CoA.

  Biochemistry 20050419

• Accumulation of long-chain acylcarnitine and 3-hydroxy acylcarnitine molecular species in diabetic myocardium: identification of alterations in mitochondrial fatty acid processing in diabetic myocardium by shotgun lipidomics.

  Biochemistry 20050405

• Characterization of carnitine and fatty acid metabolism in the long-chain acyl-CoA dehydrogenase-deficient mouse.

  The Biochemical journal 20050401

• Polycarnitine--a new biomaterial.

  Applied microbiology and biotechnology 20050401

• A phytol-enriched diet induces changes in fatty acid metabolism in mice both via PPARalpha-dependent and -independent pathways.

  Journal of lipid research 20050401

• Carnitine levels in neonatal hypoxia.

  Journal of tropical pediatrics 20050401

• Age-related variations in acylcarnitine and free carnitine concentrations measured by tandem mass spectrometry.

  Clinical chemistry 20050401

• Effect of L-carnitine on plasma glycemic and lipidemic profile in patients with type II diabetes mellitus.

  European journal of clinical nutrition 20050401

• A biochemical perspective on the use of tandem mass spectrometry for newborn screening and clinical testing.

  Clinical biochemistry 20050401

• Abnormal concentrations of esterified carnitine in bile: a feature of pediatric acute liver failure with poor prognosis.

  Hepatology (Baltimore, Md.) 20050401

• Constitutive or induced elevated levels of L-carnitine correlate with the cytokine and cellular profile of endometriosis.

  Journal of reproductive immunology 20050401

• L-carnitine infusions may suppress serum C-reactive protein and improve nutritional status in maintenance hemodialysis patients.

  Journal of renal nutrition : the official journal of the Council on Renal Nutrition of the National Kidney Foundation 20050401

• Determination of L-carnitine in food supplement formulations using ion-pair chromatography with indirect conductimetric detection.

  Journal of chromatography. A 20050401

• Levocarnitine and dialysis: a review.

  Nutrition in clinical practice : official publication of the American Society for Parenteral and Enteral Nutrition 20050401

• OCTN3: A Na+-independent L-carnitine transporter in enterocytes basolateral membrane.

  Journal of cellular physiology 20050301

• Peroxisome proliferator activated receptor delta (PPARdelta) agonist but not PPARalpha corrects carnitine palmitoyl transferase 2 deficiency in human muscle cells.

  The Journal of clinical endocrinology and metabolism 20050301

• Validation of dye-binding/high-resolution thermal denaturation for the identification of mutations in the SLC22A5 gene.

  Human mutation 20050301

• Serum carnitine levels in patients with homozygous beta thalassemia: a possible new role for carnitine?

  European journal of pediatrics 20050301

• A placebo-controlled screening trial of olanzapine, valproate, and coenzyme Q10/L-carnitine for the treatment of cocaine dependence.

  Addiction (Abingdon, England) 20050301

• Identification and functional characterisation of genes and corresponding enzymes involved in carnitine metabolism of Proteus sp.

  Archives of microbiology 20050301

• Strategy for the isolation, derivatization, chromatographic separation, and detection of carnitine and acylcarnitines.

  Analytical chemistry 20050301

• Acyl-CoA dehydrogenase deficiency: varieties with neurological involvement.

  Developmental medicine and child neurology 20050301

• Modulation of age-associated oxidative DNA damage in rat brain cerebral cortex, striatum and hippocampus by L-carnitine.

  Experimental gerontology 20050301

• Monograph. L-carnitine.

  Alternative medicine review : a journal of clinical therapeutic 20050301

• Cardiac carnitine leakage is promoted by cardiomyopathy.

  Nutrition (Burbank, Los Angeles County, Calif.) 20050301

• Sodium valproate -- induced skeletal myopathy.

  Indian journal of pediatrics 20050301

• Carnitine promising, but no miracle for heart disease. Hype for the dietary supplement carnitine as a treatment for heart disease far outstrips the evidence.

  Harvard heart letter : from Harvard Medical School 20050301

• Towards an evidence-based understanding of Peyronie's disease.

  International journal of STD & AIDS 20050301

• L-carnitine supplementation does not promote weight loss in ovariectomized rats despite endurance exercise.

  International journal for vitamin and nutrition research. Internationale Zeitschrift fur Vitamin- und Ernahrungsforschung. Journal international de vitaminologie et de nutrition 20050301

• L-carnitine inhibits hepatocarcinogenesis via protection of mitochondria.

  International journal of cancer 20050220

• Cysteine-scanning mutagenesis of muscle carnitine palmitoyltransferase I reveals a single cysteine residue (Cys-305) is important for catalysis.

  The Journal of biological chemistry 20050211

• A family with pyruvate dehydrogenase complex deficiency due to a novel C>T substitution at nucleotide position 407 in exon 4 of the X-linked Epsilon1alpha gene.

  European journal of pediatrics 20050201

• Quantitation of long-chain acylcarnitines by HPLC/fluorescence detection: application to plasma and tissue specimens from patients with carnitine palmitoyltransferase-II deficiency.

  Clinica chimica acta; international journal of clinical chemistry 20050201

• The urinary excretion of glutarylcarnitine is an informative tool in the biochemical diagnosis of glutaric acidemia type I.

  Molecular genetics and metabolism 20050201

• Short-term carnitine supplementation does not augment LCPomega3 status of vegans and lacto-ovo-vegetarians.

  Journal of the American College of Nutrition 20050201

• Antiepileptic drugs alter reproductive endocrine hormones in men with epilepsy.

  European journal of neurology 20050201

• Effects of L-arginine and L-carnitine in hypoxia/reoxygenation-induced intestinal injury.

  Pediatrics international : official journal of the Japan Pediatric Society 20050201

• Plasma carnitine levels in preterm infants with respiratory distress syndrome.

  Pediatrics international : official journal of the Japan Pediatric Society 20050201

• Oral carnitine supplementation increases sperm motility in asthenozoospermic men with normal sperm phospholipid hydroperoxide glutathione peroxidase levels.

  Fertility and sterility 20050201

• Prevention of peritoneal sclerosis: a new proposal to substitute glucose with carnitine dialysis solution (biocompatibility testing in vitro and in rabbits).

  The International journal of artificial organs 20050201

• Breeder hen dietary L-carnitine affects progeny carcase traits.

  British poultry science 20050201

• Crystal structure of mouse carnitine octanoyltransferase and molecular determinants of substrate selectivity.

  The Journal of biological chemistry 20050107

• Novel organic cation transporter 2-mediated carnitine uptake in placental choriocarcinoma (BeWo) cells.

  The Journal of pharmacology and experimental therapeutics 20050101

• Malonyl-CoA and carnitine in regulation of fat oxidation in human skeletal muscle during exercise.

  American journal of physiology. Endocrinology and metabolism 20050101

• Protective effect of L-carnitine on renal ischaemia-reperfusion injury in the rat.

  Cell biochemistry and function 20050101

• Expression, localization, and function of the carnitine transporter octn2 (slc22a5) in human placenta.

  Drug metabolism and disposition: the biological fate of chemicals 20050101

• Homocysteine, glycine betaine, and N,N-dimethylglycine in patients attending a lipid clinic.

  Metabolism: clinical and experimental 20050101

• Effects of dietary supplementation with L-carnitine and fat on blood acid-base responses to handling in slaughter weight pigs.

  Journal of animal science 20050101

• Effect of L-carnitine on nucleic acid status of aged rat brain.

  Experimental neurology 20050101

• A novel therapeutic strategy for Ehlers-Danlos syndrome based on nutritional supplements.

  Medical hypotheses 20050101

• Antimony-induced cardiomyopathy in guinea-pig and protection by L-carnitine.

  British journal of pharmacology 20050101

• Haplotype analysis of carnitine transporters and left ventricular mass in human essential hypertension.

  Journal of renal nutrition : the official journal of the Council on Renal Nutrition of the National Kidney Foundation 20050101

• Inflammation and carnitine in hemodialysis patients.

  Journal of renal nutrition : the official journal of the Council on Renal Nutrition of the National Kidney Foundation 20050101

• Role of carnitine in modulating acute-phase protein synthesis in hemodialysis patients.

  Journal of renal nutrition : the official journal of the Council on Renal Nutrition of the National Kidney Foundation 20050101

• L-carnitine supplementation in dialysis patients: does the evidence justify its use?

  Seminars in dialysis 20050101

• [Role of L-carnitine in metabolism, nutrition and therapy].

  Postepy higieny i medycyny doswiadczalnej (Online) 20050101

• Expression of Cdv-iR gene in mouse epididymis as revealed by in situ hybridization.

  Archives of andrology 20050101

• Carnitine therapy... Let the patients benefit!

  Nephrology nursing journal : journal of the American Nephrology Nurses' Association 20050101

• Design of metabolic engineering strategies for maximizing L-(-)-carnitine production by Escherichia coli. Integration of the metabolic and bioreactor levels.

  Biotechnology progress 20050101

• Correlation between seminal carnitine and functional spermatozoal characteristics in men with semen dysfunction of various origins.

  Drugs in R&D 20050101

• Carnitine therapy is associated with decreased hospital utilization among hemodialysis patients.

  American journal of nephrology 20050101

• Gestational diabetes exhibits lack of carnitine deficiency despite relatively low carnitine levels and alterations in ketogenesis.

  The journal of maternal-fetal & neonatal medicine : the official journal of the European Association of Perinatal Medicine, the Federation of Asia and Oceania Perinatal Societies, the International Society of Perinatal Obstetricians 20050101

• [The importance of functional ingredients in pediatric milk formulas and cereals].

  Nutricion hospitalaria 20050101

• High mitochondrial redox potential may promote induction and activation of UCP2 in hepatocytes during hepatothermic therapy.

  Medical hypotheses 20050101

• Free and total carnitine concentrations in pig plasma after oral ingestion of various L-carnitine compounds.

  International journal for vitamin and nutrition research. Internationale Zeitschrift fur Vitamin- und Ernahrungsforschung. Journal international de vitaminologie et de nutrition 20050101

• Supplementation of L-carnitine improves mitochondrial enzymes in heart and skeletal muscle of aged rats.

  Experimental aging research 20050101

• In vivo evidence for the efflux transport of pentazocine from the brain across the blood-brain barrier using the brain efflux index method.

  Journal of drug targeting 20050101

• Lack of correlation between fatty acid oxidation disorders and haemolysis, elevated liver enzymes, low platelets (HELLP) syndrome?

  Acta paediatrica (Oslo, Norway : 1992) 20050101

• L-carnitine and exercise tolerance in medium-chain acyl-coenzyme A dehydrogenase (MCAD) deficiency: a pilot study.

  Journal of inherited metabolic disease 20050101

• Biochemical, clinical and molecular findings in LCHAD and general mitochondrial trifunctional protein deficiency.

  Journal of inherited metabolic disease 20050101

• Normal acylcarnitine levels during confirmation of abnormal newborn screening in long-chain fatty acid oxidation defects.

  Journal of inherited metabolic disease 20050101

• Newborns with C8-acylcarnitine level over the 90th centile have an increased frequency of the common MCAD 985A>G mutation.

  Journal of inherited metabolic disease 20050101

• The 625G>A SCAD gene variant is common but not associated with increased C4-carnitine in newborn blood spots.

  Journal of inherited metabolic disease 20050101

• Genotypic differences of MCAD deficiency in the Asian population: novel genotype and clinical symptoms preceding newborn screening notification.

  Genetics in medicine : official journal of the American College of Medical Genetics 20050101

• [Valproate-dependent changes in the spectrum of free amino acids in rats: l-carnitine effects].

  Eksperimental'naia i klinicheskaia farmakologiia 20050101

• Fatty acid oxidation defects as a cause of neuromyopathic disease in infants and adults.

  Clinical laboratory 20050101

• Evaluation of carnitine, acetylcarnitine and isovalerylcarnitine on immune function and apoptosis.

  Drugs under experimental and clinical research 20050101

• The evaluation of postdialysis L-carnitine administration and its effect on weekly requiring doses of rHuEPO in hemodialysis patients.

  Renal failure 20050101

• Common misconceptions about levocarnitine and dialysis.

  Seminars in dialysis 20050101

• Cardiomyopathy and hypotonia in a 5-month-old infant with malonyl-coa decarboxylase deficiency: potential for preclinical diagnosis with expanded newborn screening.

  Pediatric cardiology 20050101

• Model of central and trimethylammonium metabolism for optimizing L-carnitine production by E. coli.

  Metabolic engineering 20050101

• Effect of L-carnitine on the serum lipoproteins and HDL-C subclasses in hemodialysis patients.

  Nephron. Clinical practice 20050101

• [Pharmacological treatments for Duchenne and Becker dystrophies].

  Journal de la Societe de biologie 20050101

• Protective effect of L-carnitine on renal ischaemia-reperfusion injury in the rat.

  Cell biochemistry and function 20050101

• L-carnitine inhibits ethanol-induced gastric mucosal injury in rats.

  Pharmacological reports : PR 20050101

• Oxidative stress, male infertility and the role of carnitines.

  Folia medica 20050101

• Protective effect of L-carnitine against oxidative damage caused by experimental chronic aflatoxicosis in quail (Coturnix coturnix).

  Acta veterinaria Hungarica 20050101

• Use of L-carnitine and humate in laying quail diets.

  Acta veterinaria Hungarica 20050101

• Pharmacologic adjuvants to epoetin in the treatment of anemia in patients on hemodialysis.

  Hemodialysis international. International Symposium on Home Hemodialysis 20050101

• [Immunomodulating effects induced by the regulators of energy metabolism and the exposure to heat and cold in case of toxic affection of the kidneys].

  Patologicheskaia fiziologiia i eksperimental'naia terapiia 20050101

• Apoptosis in thalassemia major reduced by a butyrate derivative.

  Acta haematologica 20050101

• [The impact of L-carnitine on nutritional status in juvenile idiopathic dilated cardiomyopathy].

  Jornal de pediatria 20050101

• [The role of L-carnitine in nutritional status and echocardiographic parameters in idiopathic dilated cardiomyopathy in children].

  Jornal de pediatria 20050101

• Nutritional and herbal therapies in the treatment of heart disease in cats and dogs.

  Journal of the American Animal Hospital Association 20050101

• Science review: carnitine in the treatment of valproic acid-induced toxicity - what is the evidence?

  Critical care (London, England) 20050101

• Medium-chain acyl-CoA dehydrogenase deficiency: a case presentation.

  Neonatal network : NN 20050101

• Toward a design of affordable, topical microbicides: acylcarnitine analogues.

  Current pharmaceutical design 20050101

• Cytochrome C effect on respiration of heart mitochondria: influence of various factors.

  Bioscience reports 20050101

• Peripheric and automatic neuropathy in children with type 1 diabetes mellitus: the effect of L-carnitine treatment on the peripheral and autonomic nervous system.

  Electromyography and clinical neurophysiology 20050101

• Clinicopathologic conference: Barth Syndrome.

  Fetal and pediatric pathology 20050101

• Dietary rescue of fumble--a Drosophila model for pantothenate-kinase-associated neurodegeneration.

  Journal of inherited metabolic disease 20050101

• Methylcrotonyl-CoA carboxylase (MCC) deficiency associated with severe muscle pain and physical disability in an adult.

  Journal of inherited metabolic disease 20050101

• Rhabdomyolysis in early-onset very long-chain acyl-CoA dehydrogenase deficiency despite normal glucose after fasting.

  Journal of inherited metabolic disease 20050101

• Carnitine concentrations in term and preterm newborns at birth and during the first days of life.

  Prague medical report 20050101

• Effect of L-carnitine on cardiomyocyte apoptosis and cardiac function in patients undergoing heart valve replacement operation.

  Journal of Huazhong University of Science and Technology. Medical sciences = Hua zhong ke ji da xue xue bao. Yi xue Ying De wen ban = Huazhong keji daxue xuebao. Yixue Yingdewen ban 20050101

• [Vitamine-like substances L-carnitine and acetyl-L-carnitine: from biochemical studies to medicine].

  Ukrains'kyi biokhimichnyi zhurnal (1999 ) 20050101

• A metabolic approach to the treatment of dilated cardiomyopathy in BIO T0-2 cardiomyopathic Syrian hamsters.

  BioFactors (Oxford, England) 20050101

• Enantio- and chemo-selective HPLC separations by chiral-achiral tandem-columns approach: the combination of CHIROBIOTIC TAG and SCX columns for the analysis of propionyl carnitine and related impurities.

  Journal of chromatography. A 20041224

• [Carnitine transporter deficiency in two Faeroese children].

  Ugeskrift for laeger 20041206

• Phenotypic manifestations of the OCTN2 V295X mutation: sudden infant death and carnitine-responsive cardiomyopathy in Roma families.

  American journal of medical genetics. Part A 20041201

• Synthesis of phosphonic analogues of carnitine and gamma-amino-beta-hydroxybutyric acid.

  Bioorganic chemistry 20041201

• L-carnitine in cyclical vomiting syndrome.

  Archives of disease in childhood 20041201

• Improvement of statin-associated myotoxicity by L-carnitine.

  Journal of thrombosis and haemostasis : JTH 20041201

• Relative carnitine deficiency in autism.

  Journal of autism and developmental disorders 20041201

• Effects of dietary L-carnitine and coenzyme Q10 supplementation on performance and ascites mortality of broilers.

  Archives of animal nutrition 20041201

• Medical devices; clinical chemistry and clinical toxicology devices; classification of newborn screening test systems for amino acids, free carnitine, and acylcarnitines using tandem mass spectrometry. Final rule.

  Federal register 20041124

• L-carnitine.

  The Medical letter on drugs and therapeutics 20041122

• Increased formation of short-chain organic acids after chronic ethanol administration and its interaction with the carnitine pool in rat.

  Archives of biochemistry and biophysics 20041115

• Crystal structure of CaiB, a type-III CoA transferase in carnitine metabolism.

  Biochemistry 20041109

• Dual synergistic effect: the effect of dexamethasone plus carnitine on skin flap survival.

  Annals of plastic surgery 20041101

• 3-hydroxy-3-methylglutaryl-CoA lyase deficiency in an adult with leukoencephalopathy.

  Annals of neurology 20041101

• In vivo cardiac 1H-MRS in the mouse.

  Magnetic resonance in medicine 20041101

• Primary carnitine deficiency: adult onset lipid storage myopathy with a mild clinical course.

  Journal of clinical neuroscience : official journal of the Neurosurgical Society of Australasia 20041101

• Involvement of OCTN2 and B0,+ in the transport of carnitine through an in vitro model of the blood-brain barrier.

  Journal of neurochemistry 20041101

• Short term effects of L-carnitine on serum lipids in STZ-induced diabetic rats.

  Diabetes research and clinical practice 20041101

• The role of the carnitine system in human metabolism.

  Annals of the New York Academy of Sciences 20041101

• Structure and function of carnitine acyltransferases.

  Annals of the New York Academy of Sciences 20041101

• Kinetics, pharmacokinetics, and regulation of L-carnitine and acetyl-L-carnitine metabolism.

  Annals of the New York Academy of Sciences 20041101

• Carnitine deficiency disorders in children.

  Annals of the New York Academy of Sciences 20041101

• Carnitine replacement in end-stage renal disease and hemodialysis.

  Annals of the New York Academy of Sciences 20041101

• Carnitine and sports medicine: use or abuse?

  Annals of the New York Academy of Sciences 20041101

• Therapeutic effects of L-carnitine and propionyl-L-carnitine on cardiovascular diseases: a review.

  Annals of the New York Academy of Sciences 20041101

• Carnitine and peripheral arterial disease.

  Annals of the New York Academy of Sciences 20041101

• Carnitine in type 2 diabetes.

  Annals of the New York Academy of Sciences 20041101

• Delaying the mitochondrial decay of aging with acetylcarnitine.

  Annals of the New York Academy of Sciences 20041101

• Comparison of the effects of L-carnitine and acetyl-L-carnitine on carnitine levels, ambulatory activity, and oxidative stress biomarkers in the brain of old rats.

  Annals of the New York Academy of Sciences 20041101

• Carnitines and its congeners: a metabolic pathway to the regulation of immune response and inflammation.

  Annals of the New York Academy of Sciences 20041101

• Acetyl-L-carnitine for the treatment of HIV lipoatrophy.

  Annals of the New York Academy of Sciences 20041101

• Modulatory effects of L-carnitine on glucocorticoid receptor activity.

  Annals of the New York Academy of Sciences 20041101

• Effects of carnitine on thyroid hormone action.

  Annals of the New York Academy of Sciences 20041101

• L-carnitine supplementation for the treatment of fatigue and depressed mood in cancer patients with carnitine deficiency: a preliminary analysis.

  Annals of the New York Academy of Sciences 20041101

• The role of carnitine in the male reproductive system.

  Annals of the New York Academy of Sciences 20041101

• L-carnitine may attenuate free fatty acid-induced endothelial dysfunction.

  Annals of the New York Academy of Sciences 20041101

• [Carnitine].

  Nihon rinsho. Japanese journal of clinical medicine 20041101

• Carnitine. The science behind a conditionally essential nutrient. Proceedings of a conference. March 25-26, 2004. Bethesda, Maryland, USA.

  Annals of the New York Academy of Sciences 20041101

• Interaction between altered insulin and lipid metabolism in CEACAM1-inactive transgenic mice.

  The Journal of biological chemistry 20041022

• Carnitine supplementation for preterm infants with recurrent apnea.

  The Cochrane database of systematic reviews 20041018

• Pig muscle carnitine palmitoyltransferase I (CPTI beta), with low Km for carnitine and low sensitivity to malonyl-CoA inhibition, has kinetic characteristics similar to those of the rat liver (CPTI alpha) enzyme.

  Biochemistry 20041005

• Progression of cisplatin-induced nephrotoxicity in a carnitine-depleted rat model.

  Chemotherapy 20041001

• Comparative acute effects of l-carnitine and dl-carnitine on hepatic catabolism of l-alanine and l-glutamine in rats.

  Acta pharmacologica Sinica 20041001

• Impact of hemodialysis on endogenous plasma and muscle carnitine levels in patients with end-stage renal disease.

  Kidney international 20041001

• Leg ulcers in sickle cell disease.

  Advances in skin & wound care 20041001

• [Clinical progress of neonatal non-ketotic hyperglycinemia under treatment].

  Revista de neurologia 20041001

• Peritoneal macrophages function modulation by L-carnitine in aging rats.

  Aging clinical and experimental research 20041001

• Exercise training and supplementation with carnitine and antioxidants increases carnitine stores, triglyceride utilization, and endurance in exercising rats.

  Journal of nutritional science and vitaminology 20041001

• (S)-Nitroxycarnitine nitrate production from (S)-carnitine by using acetic anhydride/nitric acid/acetic acid mixtures: safety assessment.

  Journal of hazardous materials 20040910

• Neuroprotective effect of L-carnitine in the 3-nitropropionic acid (3-NPA)-evoked neurotoxicity in rats.

  Neuroscience letters 20040902

• Carnitine content and expression of mitochondrial beta-oxidation enzymes in placentas of wild-type (OCTN2(+/+)) and OCTN2 Null (OCTN2(-/-)) Mice.

  Pediatric research 20040901

• Treatment of disability in peripheral arterial disease: new drugs.

  Current drug targets. Cardiovascular & haematological disorders 20040901

• L-carnitine protects gastric mucosa by decreasing ischemia-reperfusion induced lipid peroxidation.

  Journal of physiology and pharmacology : an official journal of the Polish Physiological Society 20040901

• Preliminary observations on the use of propionyl-L-carnitine in combination with sildenafil in patients with erectile dysfunction and diabetes.

  Current medical research and opinion 20040901

• Carnitine system in uremic patients: molecular and clinical aspects.

  Seminars in nephrology 20040901

• [Initial observation on L-carnitine for asthenospermia with epididymal knob].

  Zhonghua nan ke xue = National journal of andrology 20040901

• A novel function for fatty acid translocase (FAT)/CD36: involvement in long chain fatty acid transfer into the mitochondria.

  The Journal of biological chemistry 20040827

• Progression despite replacement of a myopathic form of coenzyme Q10 defect.

  Neurology 20040824

• The influence on cognition of the interactions between lecithin, carnitine and carbohydrate.

  Psychopharmacology 20040801

• The role of insulin, glucagon, dexamethasone, and leptin in the regulation of ketogenesis and glycogen storage in primary cultures of porcine hepatocytes prepared from 60 kg pigs.

  Domestic animal endocrinology 20040801

• Effect of L-carnitine administration on the seminal characteristics of oligoasthenospermic stallions.

  Theriogenology 20040801

• L-Carnitine transport in human placental brush-border membranes is mediated by the sodium-dependent organic cation transporter OCTN2.

  American journal of physiology. Cell physiology 20040801

• Inhibitory effects of halothane on the thermogenic pathway in brown adipocytes: localization to adenylyl cyclase and mitochondrial fatty acid oxidation.

  Biochemical pharmacology 20040801

• The effect of l-carnitine on fat oxidation, protein turnover, and body composition in slightly overweight subjects.

  Metabolism: clinical and experimental 20040801

• Ischemic heart disease: metabolic approaches to management.

  Clinical cardiology 20040801

• Endothelium- and nitric oxide-dependent vasorelaxing activities of gamma-butyrobetaine esters: possible link to the antiischemic activities of mildronate.

  European journal of pharmacology 20040708

• L-carnitine and DL-alpha-lipoic acid reverse the age-related deficit in glutathione redox state in skeletal muscle and heart tissues.

  Mechanisms of ageing and development 20040701

• [The beneficial effect of L-carnitine in rat renal ischemia-reperfusion injury].

  Ulusal travma ve acil cerrahi dergisi = Turkish journal of trauma & emergency surgery : TJTES 20040701

• Influence of Carnichrome on the energy balance of gestating sows.

  Journal of animal science 20040701

• Genetic and biochemical study in a patient with glutaric acidemia type I.

  Journal of the Formosan Medical Association = Taiwan yi zhi 20040701

• Dobutamine alters carnitine metabolism in the neonatal piglet heart.

  Canadian journal of physiology and pharmacology 20040701

• Age-associated decreased activities of mitochondrial electron transport chain complexes in heart and skeletal muscle: role of L-carnitine.

  Chemico-biological interactions 20040630

• Functional food: a growing and not clearly controlled market with a risk potential ranging from a food to a drug.

  Swiss medical weekly 20040626

• Interaction of food supplement L-carnitine with oral anticoagulant acenocoumarol.

  Swiss medical weekly 20040626

• Myocardial carnitine palmitoyltransferase I expression and long-chain fatty acid oxidation in fetal and newborn lambs.

  American journal of physiology. Heart and circulatory physiology 20040601

• Structural and mutational characterization of L-carnitine binding to human carnitine acetyltransferase.

  Journal of structural biology 20040601

• The effects of L-carnitine on presbyacusis in the rat model.

  Clinical otolaryngology and allied sciences 20040601

• About the neuroprotective effects of FK-506, l-carnitine and azathioprine on spinal cord ischemia-reperfusion injury.

  European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic Surgery 20040601

• A high performance liquid chromatographic method for the measurement of total carnitine in human plasma and urine.

  Clinica chimica acta; international journal of clinical chemistry 20040601

• Homozygosity for a severe novel medium-chain acyl-CoA dehydrogenase (MCAD) mutation IVS3-1G > C that leads to introduction of a premature termination codon by complete missplicing of the MCAD mRNA and is associated with phenotypic diversity ranging from sudden neonatal death to asymptomatic status.

  Molecular genetics and metabolism 20040601

• Effects of supplemental L-carnitine in drinking water on performance and egg quality of laying hens exposed to a high ambient temperature.

  Journal of animal physiology and animal nutrition 20040601

• A placebo-controlled double-blind randomized trial of the use of combined l-carnitine and l-acetyl-carnitine treatment in men with asthenozoospermia.

  Fertility and sterility 20040601

• [Hyporesponsiveness to recombinant human erythropoietin therapy in anemic patients on hemodialysis].

  Nihon rinsho. Japanese journal of clinical medicine 20040601

• [Energy and nutrition in maintenance dialysis--significance of carnitine and cytokine in malnutrition].

  Nihon rinsho. Japanese journal of clinical medicine 20040601

• [A pilot study of selective screening for high risk children with inborn error of metabolism using tandem mass spectrometry in China].

  Zhonghua er ke za zhi = Chinese journal of pediatrics 20040601

• L-Carnitine is a modulator of the glucocorticoid receptor alpha.

  Annals of the New York Academy of Sciences 20040601

• Functional regions of organic cation/carnitine transporter OCTN2 (SLC22A5): roles in carnitine recognition.

  Drug metabolism and pharmacokinetics 20040601

• Structural model of carnitine palmitoyltransferase I based on the carnitine acetyltransferase crystal.

  The Biochemical journal 20040501

• Effects of dietary L-carnitine supplementation on semen characteristics in boars.

  Theriogenology 20040501

• The methylester of gamma-butyrobetaine, but not gamma-butyrobetaine itself, induces muscarinic receptor-dependent vasodilatation.

  Naunyn-Schmiedeberg's archives of pharmacology 20040501

• L-carnitine ameliorates oxidative damage due to chronic renal failure in rats.

  Journal of cardiovascular pharmacology 20040501

• Synthesis of dicarboxylic acylcarnitines.

  Chemistry and physics of lipids 20040501

• Renal transport of organic compounds mediated by mouse organic anion transporter 3 (mOat3): further substrate specificity of mOat3.

  Drug metabolism and disposition: the biological fate of chemicals 20040501

• Functional variants of OCTN cation transporter genes are associated with Crohn disease.

  Nature genetics 20040501

• Increased plasma carnitine concentrations in preeclampsia.

  Obstetrics and gynecology 20040501

• Ventricular fibrillation without overt cardiomyopathy as first presentation of organic cation transporter 2-deficiency in adolescence.

  Pacing and clinical electrophysiology : PACE 20040501

• Long-term treatment with antioxidants and a program of behavioral enrichment reduces age-dependent impairment in discrimination and reversal learning in beagle dogs.

  Experimental gerontology 20040501

• [Dilated cardiomyopathy].

  Nihon rinsho. Japanese journal of clinical medicine 20040501

• Prevention of postischemic spinal cord injury by means of regional infusion of adenosine and L-carnitine dissolved in normothermic saline.

  Annals of vascular surgery 20040501

• Study on conical columns with different conical angles for semi-preparative liquid chromatography.

  Journal of chromatography. A 20040416

• Response to therapy in carnitine/acylcarnitine translocase (CACT) deficiency due to a novel missense mutation.

  American journal of medical genetics. Part A 20040415

• Acetyl-L-carnitine supplementation restores decreased tissue carnitine levels and impaired lipid metabolism in aged rats.

  Journal of lipid research 20040401

• Identification of the up- and down-regulated genes in the heart of juvenile visceral steatosis mice.

  Biological & pharmaceutical bulletin 20040401

• The importance of gut motility in the metabolic control of propionic acidemia.

  The Journal of pediatrics 20040401

• Carnitine versus androgen administration in the treatment of sexual dysfunction, depressed mood, and fatigue associated with male aging.

  Urology 20040401

• Synthesis and evaluation of anti-apoptotic activity of L-carnitine cyclic analogues and amino acid derivatives.

  Farmaco (Societa chimica italiana : 1989) 20040401

• Effects of carnitines on rat sertoli cell protein metabolism.

  Hormone and metabolic research = Hormon- und Stoffwechselforschung = Hormones et metabolisme 20040401

• [Haemodialysis, L-carnitine therapy and valproic acid overdose].

  Annales francaises d'anesthesie et de reanimation 20040401

• Carnitines and male infertility.

  Reproductive biomedicine online 20040401

• [Clinical feature of Rett syndrome and MeCP2 genotype/phenotype correlation analysis].

  Zhonghua er ke za zhi = Chinese journal of pediatrics 20040401

• [Concentrations of L-carnitine and parameters of lipid metabolism during estrus in broodmares].

  DTW. Deutsche tierarztliche Wochenschrift 20040401

• [The human OCTN2 carnitine transporter and its mutations].

  Orvosi hetilap 20040328

• Role of L-carnitine in the prevention of acute liver damage induced by carbon tetrachloride in rats.

  Journal of gastroenterology and hepatology 20040301

• Implications of impaired ketogenesis in fatty acid oxidation disorders.

  Prostaglandins, leukotrienes, and essential fatty acids 20040301

• Hepatic expression of malonyl-CoA decarboxylase reverses muscle, liver and whole-animal insulin resistance.

  Nature medicine 20040301

• Role of carnitine supplementation in apnea of prematurity: a systematic review.

  Journal of perinatology : official journal of the California Perinatal Association 20040301

• Membrane transport of fatty acylcarnitine and free L-carnitine by rat liver microsomes.

  European journal of biochemistry 20040301

• Interaction between anticonvulsants and human placental carnitine transporter.

  Epilepsia 20040301

• Changes in blood carnitine and acylcarnitine profiles of very long-chain acyl-CoA dehydrogenase-deficient mice subjected to stress.

  European journal of clinical investigation 20040301

• Fatty acid oxidation and related gene expression in heart depleted of carnitine by mildronate treatment in the rat.

  Molecular and cellular biochemistry 20040301

• Rett's syndrome following bronchopneumonia.

  Indian pediatrics 20040301

• The influence of L-carnitine on methanol biotransformation in rats.

  Experimental and toxicologic pathology : official journal of the Gesellschaft fur Toxikologische Pathologie 20040301

• Severe lactic acidosis in association with reverse transcriptase inhibitors with potential response to L-carnitine in a pediatric HIV-positive patient.

  AIDS patient care and STDs 20040301

• [Biochemical mechanisms of mildronate action during ischemic stress].

  Likars'ka sprava 20040301

• Tyrosine residues affecting sodium stimulation of carnitine transport in the OCTN2 carnitine/organic cation transporter.

  The Journal of biological chemistry 20040220

• Different sensitivities of CPT I and CPT II for inhibition by l-aminocarnitine in human skeletal muscle.

  Biochimica et biophysica acta 20040215

• Reconstitution into liposomes and functional characterization of the carnitine transporter from renal cell plasma membrane.

  Biochimica et biophysica acta 20040210

• Plasma and liver carnitine levels of children with chronic hepatitis B.

  Journal of clinical gastroenterology 20040201

• Serum carnitine concentrations correlated to clinical outcome parameters in chronic hemodialysis patients.

  Clinical nutrition (Edinburgh, Scotland) 20040201

• Plasma carnitine concentrations in patients undergoing open heart surgery.

  Annals of thoracic and cardiovascular surgery : official journal of the Association of Thoracic and Cardiovascular Surgeons of Asia 20040201

• Intracranial venous thrombosis after hypoxic-ischemic brain insult in two newborns: could low serum carnitine levels have contributed?

  Nutritional neuroscience 20040201

• Improvement of cardiac function and beta-adrenergic signal transduction by propionyl L-carnitine in congestive heart failure due to myocardial infarction.

  Coronary artery disease 20040201

• GP7 can induce apoptotic DNA fragmentation of human leukemia cells through caspase-3-dependent and -independent pathways.

  International journal of molecular medicine 20040101

• Improving the bacteriological safety of platelet transfusions.

  Transfusion medicine reviews 20040101

• L-carnitine and its possible role in red cell and platelet storage.

  Transfusion medicine reviews 20040101

• Neuroprotective effects of FK-506, L-carnitine and azathioprine on spinal cord ischemia-reperfusion injury.

  European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic Surgery 20040101

• Betaine improves growth, but does not induce whole body or hepatic palmitate oxidation in swine (Sus scrofa domestica).

  Comparative biochemistry and physiology. Part A, Molecular & integrative physiology 20040101

• Effects of gamma-butyrobetaine and mildronate on nitric oxide production in lipopolysaccharide-treated rats.

  Basic & clinical pharmacology & toxicology 20040101

• A shift in myocardial substrate, improved endothelial function, and diminished sympathetic activity may contribute to the anti-anginal impact of very-low-fat diets.

  Medical hypotheses 20040101

• [Early diagnosis of neurometabolic diseases by tandem mass spectrometry. Acylcarnitine profile from cord blood].

  Revista de neurologia 20040101

• Dietary L-carnitine increases plasma leptin concentrations of gestating sows fed one meal per day.

  Domestic animal endocrinology 20040101

• Effects of putative epididymal osmolytes on sperm volume regulation of fertile and infertile c-ros transgenic Mice.

  Journal of andrology 20040101

• Vitamins, supplements, herbal medicines, and arrhythmias.

  Cardiology in review 20040101

• Blood acylcarnitine levels in normal newborns and heterozygotes for medium-chain acyl-CoA dehydrogenase deficiency: a relationship between genotype and biochemical phenotype?

  Journal of inherited metabolic disease 20040101

• Carnitine supplementation fails to maximize fat mass loss induced by endurance training in rats.

  Annals of nutrition & metabolism 20040101

• Clinical improvement in psoriatic arthritis symptoms during treatment for infertility with carnitine.

  Clinical and experimental rheumatology 20040101

• Traditional and nontraditional effective and noneffective therapies for cardiac disease in dogs and cats.

  The Veterinary clinics of North America. Small animal practice 20040101

• Improvement of cardiac function in thalassemia major treated with L-carnitine.

  Acta haematologica 20040101

• Exploratory open label, randomized study of acetyl- and propionylcarnitine in chronic fatigue syndrome.

  Psychosomatic medicine 20040101

• Report of two Turkish infants with Norman-Roberts syndrome.

  Genetic counseling (Geneva, Switzerland) 20040101

• Prior experience, antioxidants, and mitochondrial cofactors improve cognitive function in aged beagles.

  Veterinary therapeutics : research in applied veterinary medicine 20040101

• Carnitine-acylcarnitine translocase deficiency: identification of a novel molecular defect in a Bedouin patient.

  Journal of inherited metabolic disease 20040101

• Determination of carnitine and acylcarnitines in plasma by high-performance liquid chromatography/electrospray ionization ion trap tandem mass spectrometry.

  Rapid communications in mass spectrometry : RCM 20040101

• Supplementation of L-carnitine in athletes: does it make sense?

  Nutrition (Burbank, Los Angeles County, Calif.) 20040101

• Carnitine: a false dawn in the treatment of muscle weakness in end-stage renal failure patients?

  Nephron. Clinical practice 20040101

• Effects of carnitine supplementation on muscle metabolism by the use of magnetic resonance spectroscopy and near-infrared spectroscopy in end-stage renal disease.

  Nephron. Clinical practice 20040101

• Effects of propionyl-carnitine in patients with type 2 diabetes and peripheral vascular disease: results of a pilot trial.

  Drugs in R&D 20040101

• Effects of propionyl-carnitine on mitochondrial respiration and post-ischaemic cardiac function in the ischaemic underperfused diabetic rat heart.

  Drugs in R&D 20040101

• Serum carnitine and selenium levels in children with celiac disease.

  Indian journal of gastroenterology : official journal of the Indian Society of Gastroenterology 20040101

• Diagnostic difficulties in a case of primary systemic carnitine deficiency with idiopathic dilated cardiomyopathy.

  European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology Society 20040101

• L-carnitine improves pH and decreases surface phosphatidylserine expression in extended stored apheresis platelets.

  Journal of clinical apheresis 20040101

• Effects of very low-fat diets on anginal symptoms.

  Medical hypotheses 20040101

• Cinnoxicam and L-carnitine/acetyl-L-carnitine treatment for idiopathic and varicocele-associated oligoasthenospermia.

  Journal of andrology 20040101

• Pseudo-glutarylcarnitinaemia in medium-chain acyl-CoA dehydrogenase deficiency detected by tandem mass spectrometry newborn screening.

  Journal of inherited metabolic disease 20040101

• Carnitine deficiency in children and adolescents with type 1 diabetes.

  Journal of diabetes and its complications 20040101

• Carnitine: a nutritional, biosynthetic, and functional perspective.

  Molecular aspects of medicine 20040101

• Carnitine acyltransferases and their influence on CoA pools in health and disease.

  Molecular aspects of medicine 20040101

• Carnitine-acylcarnitine translocase deficiency, clinical, biochemical and genetic aspects.

  Molecular aspects of medicine 20040101

• Role of carnitine esters in brain neuropathology.

  Molecular aspects of medicine 20040101

• Carnitine: transport and physiological functions in the brain.

  Molecular aspects of medicine 20040101

• Carnitine prevents cyclic GMP-induced inhibition of peroxisomal enzyme activities.

  Cell biochemistry and function 20040101

• [The influence of panthotenic acid mitochondrial oxidation and oxidative phosphorylation in liver of rats with alimentary obesity].

  Voprosy pitaniia 20040101

• Isobutyryl-CoA dehydrogenase deficiency: isobutyrylglycinuria and ACAD8 gene mutations in two infants.

  Journal of inherited metabolic disease 20040101

• Maintenance treatment of glutaryl-CoA dehydrogenase deficiency.

  Journal of inherited metabolic disease 20040101

• [Biochemical basis of valproic acid toxicity: role of oxidative stress and effects of L-carnitine].

  Biomeditsinskaia khimiia 20040101

• Age-dependent alterations in mitochondrial enzymes in cortex, striatum and hippocampus of rat brain -- potential role of L-Carnitine.

  Biogerontology 20040101

• [Substantiation of the use of L-carnitine for the treatment of alcoholism].

  Eksperimental'naia i klinicheskaia farmakologiia 20040101

• Free and total carnitine levels in patients with celiac disease.

  Indian journal of gastroenterology : official journal of the Indian Society of Gastroenterology 20040101

• Free radical theory of apoptosis and metamorphosis.

  Redox report : communications in free radical research 20040101

• Carnitine transporter defect due to a novel mutation in the SLC22A5 gene presenting with peripheral neuropathy.

  Journal of inherited metabolic disease 20040101

• Stability of malonylcarnitine and glutarylcarnitine in stored blood spots.

  Journal of inherited metabolic disease 20040101

• Isovaleric acidemia diagnosed promptly by tandem mass spectrometry: report of one case.

  Acta paediatrica Taiwanica = Taiwan er ke yi xue hui za zhi 20040101

• [Carnitine level in human lens and density of cataract].

  Klinika oczna 20040101

• Filter paper cards contaminated with EMLA cream produce artefacts on acylcarnitine analysis.

  Journal of inherited metabolic disease 20040101

• Acanthopanax senticosus extract prepared from cultured cells decreases adiposity and obesity indices in C57BL/6J mice fed a high fat diet.

  Journal of medicinal food 20040101

• Serum carnitine levels in newborns with perinatal asphyxia and relation to neurologic prognosis.

  Nutritional neuroscience 20040101

• [Effect of L-carnitine on metabolic disorders in rats with experimental acyl-CoA dehydrogenase deficiency].

  Eksperimental'naia i klinicheskaia farmakologiia 20040101

• Clinical and echocardiographic findings in patients with myocardial toxicity due to scorpion sting.

  The National medical journal of India 20040101

• [Can the treatment with L-carnitine improve the inflammation in chronic hemodialysis patients?].

  Giornale italiano di nefrologia : organo ufficiale della Societa italiana di nefrologia 20040101

• Glutaric aciduria type 1 in a Kuwaiti infant.

  Eastern Mediterranean health journal = La revue de sante de la Mediterranee orientale = al-Majallah al-sihhiyah li-sharq al-mutawassit 20040101

• Nutrition. Long-term high-dose carnitine found to help heal damaged nerves.

  TreatmentUpdate 20040101

• L-carnitine ameliorates abnormal vulnerability of steatotic rat livers to cold ischemic preservation.

  Transplantation 20031227

• A knock-out mouse model for methylmalonic aciduria resulting in neonatal lethality.

  The Journal of biological chemistry 20031226

• Link between primary and secondary metabolism in the biotransformation of trimethylammonium compounds by escherichia coli.

  Biotechnology and bioengineering 20031220

• Mitochondrial generation of reactive oxygen species and its role in aerobic life.

  Current medicinal chemistry 20031201

• Effects of L-carnitine and its derivatives on postischemic cardiac function, ventricular fibrillation and necrotic and apoptotic cardiomyocyte death in isolated rat hearts.

  Molecular and cellular biochemistry 20031201

• [Regulation of myocardial metabolism: possibilities and application in cardiac surgery].

  Kardiologia polska 20031201

• Functional domains in the carnitine transporter OCTN2, defective in primary carnitine deficiency.

  The Journal of biological chemistry 20031128

• [Myocardial protective effect of L-carnitine in cardioplegia solution on patients undergoing heart valve replacement operation].

  Zhonghua yi xue za zhi 20031110

• L-carnitine reduces brain injury after hypoxia-ischemia in newborn rats.

  Pediatric research 20031101

• Carnitine supplementation improves apolipoprotein B levels in pediatric peritoneal dialysis patients.

  Pediatric nephrology (Berlin, Germany) 20031101

• A comparison of in vitro acylcarnitine profiling methods for the diagnosis of classical and variant short chain acyl-CoA dehydrogenase deficiency.

  Clinica chimica acta; international journal of clinical chemistry 20031101

• Use of tandem mass spectrometry for multianalyte screening of dried blood specimens from newborns.

  Clinical chemistry 20031101

• Short-chain Acyl-CoA dehydrogenase deficiency: studies in a large family adding to the complexity of the disorder.

  Pediatrics 20031101

• Relationship between semen quality and seminal plasma total carnitine in infertile men.

  Journal of obstetrics and gynaecology : the journal of the Institute of Obstetrics and Gynaecology 20031101

• Carnitine: a neuromodulator in aged rats.

  The journals of gerontology. Series A, Biological sciences and medical sciences 20031101

• Enzymatic synthesis of phosphocarnitine, phosphogabob and fosfomycin.

  Organic & biomolecular chemistry 20031021

• [Dietary supplements and functional food for weight reduction -- expectations and reality].

  MMW Fortschritte der Medizin 20031016

• A novel mitochondrial carnitine-acylcarnitine translocase induced by partial hepatectomy and fasting.

  The Journal of biological chemistry 20031003

• Low serum carnitine in HIV-infected children on antiretroviral treatment.

  European journal of clinical nutrition 20031001

• Defective hepatic mitochondrial respiratory chain in patients with nonalcoholic steatohepatitis.

  Hepatology (Baltimore, Md.) 20031001

• Successive thyroid storms treated with L-carnitine and low doses of methimazole.

  The American journal of medicine 20031001

• The effect of L-carnitine on the prevention of experimentally induced myringosclerosis in rats.

  Hearing research 20031001

• Effects of carnitine and taurine on fatty acid metabolism and lipid accumulation in the liver of cats during weight gain and weight loss.

  American journal of veterinary research 20031001

• Effects of L-carnitine treatment on oxidant/antioxidant state and vascular reactivity of streptozotocin-diabetic rat aorta.

  The Journal of pharmacy and pharmacology 20031001

• The carnitine system and body composition.

  Acta diabetologica 20031001

• Effects of L-carnitine administration on growth performance, carcass traits, blood serum parameters and abdominal fatty acid composition of ducks.

  Archiv fur Tierernahrung 20031001

• Simultaneous determination of L- and D-carnitine using a sequential injection analysis/amperometric biosensors system.

  Journal of pharmaceutical and biomedical analysis 20030919

• A single amino acid change (substitution of the conserved Glu-590 with alanine) in the C-terminal domain of rat liver carnitine palmitoyltransferase I increases its malonyl-CoA sensitivity close to that observed with the muscle isoform of the enzyme.

  The Journal of biological chemistry 20030905

• Protective role of carnitine esters against alcohol-induced gastric lesions in rats.

  Pharmacological research 20030901

• Adult presentation of MCAD deficiency revealed by coma and severe arrythmias.

  Intensive care medicine 20030901

• Accurate measurement of free carnitine in dried blood spots by isotope-dilution electrospray tandem mass spectrometry without butylation.

  Clinica chimica acta; international journal of clinical chemistry 20030901

• L- and DL-carnitine induce tetanic fade in rat neuromuscular preparation.

  Brazilian journal of medical and biological research = Revista brasileira de pesquisas medicas e biologicas 20030901

• Effects of increasing dietary L-carnitine on growth performance of weanling pigs.

  Journal of animal science 20030901

• [L-carnitine and lipid lowering].

  Deutsche medizinische Wochenschrift (1946) 20030822

• Rare disorders of metabolism with elevated butyryl- and isobutyryl-carnitine detected by tandem mass spectrometry newborn screening.

  Pediatric research 20030801

• The management of anemia in pediatric peritoneal dialysis patients. Guidelines by an ad hoc European committee.

  Pediatric nephrology (Berlin, Germany) 20030801

• L-carnitine: A nutritional modulator of glucocorticoid receptor functions.

  FASEB journal : official publication of the Federation of American Societies for Experimental Biology 20030801

• Utilization of long-chain fatty acids in human skeletal muscle during exercise.

  Acta physiologica Scandinavica 20030801

• Reproductive performance of rats supplemented with L-carnitine.

  Journal of animal physiology and animal nutrition 20030801

• Prevention of laryngotracheal stenosis with carnitine after tracheotomy: an experimental study on rats.

  International journal of pediatric otorhinolaryngology 20030801

• The effects of L-carnitine L-tartrate supplementation on hormonal responses to resistance exercise and recovery.

  Journal of strength and conditioning research 20030801

• L-carnitine transport in kidney of normotensive, Wistar-Kyoto rats: effect of chronic L-carnitine administration.

  Pharmaceutical research 20030801

• Serum carnitine levels during oxcarbazepine and carbamazepine monotherapies in children with epilepsy.

  Journal of child neurology 20030801

• Potential osmoprotectants for the lactic acid bacteria Pediococcus pentosaceus and Tetragenococcus halophila.

  International journal of food microbiology 20030715

• Effect of supplementation with L-carnitine at a small dose on acylcarnitine profiles in serum and urine and the renal handling of acylcarnitines in a patient with multiple acyl-coenzyme A dehydrogenation defect.

  Journal of chromatography. B, Analytical technologies in the biomedical and life sciences 20030715

• Acetylcholine recognition by a deep, biomimetic pocket.

  Angewandte Chemie (International ed. in English) 20030714

• Long-term follow-up of a new case of liver glycogen synthase deficiency.

  American journal of medical genetics. Part A 20030701

• Downregulation of carnitine acyltransferases and organic cation transporter OCTN2 in mononuclear cells in healthy elderly and patients with myelodysplastic syndromes.

  Journal of molecular medicine (Berlin, Germany) 20030701

• Rapid liquid chromatography-electrospray tandem mass spectrometry method for serum free and total carnitine.

  Clinical chemistry 20030701

• In vitro cytotoxicity of aplidin and crossresistance with other cytotoxic drugs in childhood leukemic and normal bone marrow and blood samples: a rational basis for clinical development.

  Leukemia 20030701

• Prospective diagnosis of 2-methylbutyryl-CoA dehydrogenase deficiency in the Hmong population by newborn screening using tandem mass spectrometry.

  Pediatrics 20030701

• Quantification of non-protein nitrogen components of infant formulae and follow-up milks: comparison with cows' and human milk.

  The British journal of nutrition 20030701

• A snapshot of carnitine acetyltransferase.

  Trends in biochemical sciences 20030701

• Reference ranges for muscle carnitine concentration in children.

  Annals of clinical biochemistry 20030701

• [The impact of carnitine on serum ammonia concentration and lipid metabolism in patients with alcoholic liver cirrhosis].

  Polski merkuriusz lekarski : organ Polskiego Towarzystwa Lekarskiego 20030701

• Characterization of organic cation/carnitine transporter family in human sperm.

  Biochemical and biophysical research communications 20030620

• Statin-associated myopathy with normal creatine kinase levels.

  Annals of internal medicine 20030617

• Characteristic acylcarnitine profiles in inherited defects of peroxisome biogenesis: a novel tool for screening diagnosis using tandem mass spectrometry.

  Pediatric research 20030601

• The role of the sigB gene in the general stress response of Listeria monocytogenes varies between a strain of serotype 1/2a and a strain of serotype 4c.

  Current microbiology 20030601

• Attenuation of levodopa-induced dyskinesia by normalizing dopamine D3 receptor function.

  Nature medicine 20030601

• Successful carnitine therapy for Raynaud's phenomenon in velo-cardio-facial syndrome.

  American journal of medical genetics. Part A 20030601

• Carnitine metabolism and deficit--when supplementation is necessary?

  Current pharmaceutical biotechnology 20030601

• Expanded newborn screening for inborn errors of metabolism by electrospray ionization-tandem mass spectrometry: results, outcome, and implications.

  Pediatrics 20030601

• Effect of experimental varicocele on structure and function of epididymis in adolescent rats.

  Asian journal of andrology 20030601

• Modulation of methylation in the FMR1 promoter region after long term treatment with L-carnitine and acetyl-L-carnitine.

  Journal of medical genetics 20030601

• Optimal dietary therapy of long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency.

  Molecular genetics and metabolism 20030601

• Activity of D-carnitine and its derivatives on Trypanosoma infections in rats and mice.

  Parasite (Paris, France) 20030601

• L-carnitine can be measured accurately--and cost-effectively.

  Nephrology news & issues 20030601

• Early events of the exogenously provided L-Carnitine in murine macrophages, T- and B-lymphocytes: modulation of prostaglandin E1 and E2 production in response to arachidonic acid.

  The Journal of nutritional biochemistry 20030601

• Glutaryl-CoA dehydrogenase deficiency: region-specific analysis of organic acids and acylcarnitines in post mortem brain predicts vulnerability of the putamen.

  Neuropediatrics 20030601

• Synthesis of water-soluble prodrugs of BMS-191011: a maxi-K channel opener targeted for post-stroke neuroprotection.

  Bioorganic & medicinal chemistry letters 20030519

• Ester synthesis from trimethylammonium alcohols in dry organic media catalyzed by immobilized Candida antarctica lipase B.

  Biotechnology and bioengineering 20030505

• Immunomodulatory effects of L-carnitine and q10 in mouse spleen exposed to low-frequency high-intensity magnetic field.

  Toxicology 20030503

• Neonatal blood carnitine concentrations: normative data by electrospray tandem mass spectometry.

  Pediatric research 20030501

• Effect of L-carnitine supplementation on cardiac carnitine palmitoyltransferase activities and plasma carnitine concentrations in adriamycin-treated rats.

  Pediatric research 20030501

• Expression and localization of organic cation/carnitine transporter OCTN2 in Caco-2 cells.

  American journal of physiology. Gastrointestinal and liver physiology 20030501

• The effects of carnitine on distally-burned dorsal skin flap: an experimental study in rats.

  Burns : journal of the International Society for Burn Injuries 20030501

• Human sperm volume regulation. Response to physiological changes in osmolality, channel blockers and potential sperm osmolytes.

  Human reproduction (Oxford, England) 20030501

• Beneficial effects of L-carnitine in myoblastic C2C12 cells. Interaction with zidovudine.

  Biochemical pharmacology 20030501

• Carnitine palmityltransferase II (CPT2) deficiency and migraine headache: two case reports.

  Headache 20030501

• Clinical quiz. Secondary carnitine deficiency due to celiac disease.

  Journal of pediatric gastroenterology and nutrition 20030501

• Possible mechanism for the neuroprotective effects of L-carnitine on methamphetamine-evoked neurotoxicity.

  Annals of the New York Academy of Sciences 20030501

• Neuroprotective effects of L-carnitine in induced mitochondrial dysfunction.

  Annals of the New York Academy of Sciences 20030501

• 3-nitropropionic acid inhibition of succinate dehydrogenase (complex II) activity in cultured Chinese hamster ovary cells: antagonism by L-carnitine.

  Annals of the New York Academy of Sciences 20030501

• The effect of L-carnitine on plasma lipoprotein(a) levels in hypercholesterolemic patients with type 2 diabetes mellitus.

  Clinical therapeutics 20030501

• Brain delivery of vasoactive intestinal peptide (VIP) following nasal administration to rats.

  International journal of pharmaceutics 20030414

• Molecular cloning and functional characterization of the OCTN2 transporter at the RBE4 cells, an in vitro model of the blood-brain barrier.

  Brain research 20030404

• Tandem mass spectrometric determination of malonylcarnitine: diagnosis and neonatal screening of malonyl-CoA decarboxylase deficiency.

  Clinical chemistry 20030401

• Mutations in the AUH gene cause 3-methylglutaconic aciduria type I.

  Human mutation 20030401

• Practice recommendations for the use of L-carnitine in dialysis-related carnitine disorder. National Kidney Foundation Carnitine Consensus Conference.

  American journal of kidney diseases : the official journal of the National Kidney Foundation 20030401

• Does exercise training interfere with the effects of L-carnitine supplementation?

  Nutrition (Burbank, Los Angeles County, Calif.) 20030401

• Detecting life-threatening lactic acidosis related to nucleoside-analog treatment of human immunodeficiency virus-infected patients, and treatment with L-carnitine.

  Critical care medicine 20030401

• The frequency of short-chain acyl-CoA dehydrogenase gene variants in the US population and correlation with the C(4)-acylcarnitine concentration in newborn blood spots.

  Molecular genetics and metabolism 20030401

• Late-onset form of beta-electron transfer flavoprotein deficiency.

  Molecular genetics and metabolism 20030401

• Impact on carnitine homeostasis of short-term treatment with the pivalate prodrug cefditoren pivoxil.

  Clinical pharmacology and therapeutics 20030401

• L-carnitine use in dialysis patients: is national coverage for supplementation justified? What were CMS regulators thinking--or were they?

  Nephrology news & issues 20030401

• CMS national coverage decision for L-carnitine injection--a reasonable process.

  Nephrology news & issues 20030401

• Clinical management of dialysis-related carnitine deficiency: three case studies.

  Nephrology news & issues 20030401

• On the evolving nature of understanding dialysis-related disorders.

  American journal of kidney diseases : the official journal of the National Kidney Foundation 20030401

• The role of carnitine in normal and altered fatty acid metabolism.

  American journal of kidney diseases : the official journal of the National Kidney Foundation 20030401

• Dialysis-related carnitine disorder and levocarnitine pharmacology.

  American journal of kidney diseases : the official journal of the National Kidney Foundation 20030401

• L-carnitine treatment of anemia.

  American journal of kidney diseases : the official journal of the National Kidney Foundation 20030401

• The role of carnitine in myocardial dysfunction.

  American journal of kidney diseases : the official journal of the National Kidney Foundation 20030401

• A review of the impact of L-carnitine therapy on patient functionality in maintenance hemodialysis.

  American journal of kidney diseases : the official journal of the National Kidney Foundation 20030401

• L-carnitine consecutively administered to patients on hemodialysis improves beta-cell response.

  The International journal of artificial organs 20030401

• Myocardial function and energy metabolism in carnitine-deficient rats.

  Cellular and molecular life sciences : CMLS 20030401

• Kinetic analysis of the selectivity of acylcarnitine synthesis in rat mitochondria.

  Lipids 20030401

• Effects of L-carnitine and niacin supplied by drinking water on fattening performance, carcass quality and plasma L-carnitine concentration of broiler chicks.

  Archiv fur Tierernahrung 20030401

• Effect of regular training on plasma thiols, malondialdehyde and carnitine concentrations in young soccer players.

  The Chinese journal of physiology 20030331

• Increased plasma concentration and brain penetration of methamphetamine in behaviorally sensitized rats.

  European journal of pharmacology 20030307

• Clinical effects of L-carnitine supplementation on apnea and growth in very low birth weight infants.

  Pediatrics 20030301

• Carnitine and hemodialysis.

  American journal of kidney diseases : the official journal of the National Kidney Foundation 20030301

• Effects of L-carnitine on neutrophil functions in aged rats.

  Mechanisms of ageing and development 20030301

• Metabolic modulation and optimization of energy consumption in heart failure.

  The Medical clinics of North America 20030301

• Effects of L-carnitine on growth performance, carcass composition, and metabolism of lipids in male broilers.

  Poultry science 20030301

• TBARS, carnitine, and reduced glutathione levels in human bladder carcinoma.

  Biochemistry. Biokhimiia 20030301

• New nitrogen mustards structurally related to (L)-carnitine.

  Bioorganic & medicinal chemistry 20030206

• L-Carnitine alters nitric oxide synthase activity in fibroblasts depending on the peroxisomal status.

  The international journal of biochemistry & cell biology 20030201

• Use of carnitine therapy in selected cases of male factor infertility: a double-blind crossover trial.

  Fertility and sterility 20030201

• Anti-diabetes effect of Zn(II)/carnitine complex by oral administration.

  Chemical & pharmaceutical bulletin 20030201

• Skeletal muscle metabolism in Duchenne muscular dystrophy (DMD): an in-vitro proton NMR spectroscopy study.

  Magnetic resonance imaging 20030201

• Effects of dietary supplemental L-carnitine and ascorbic acid on performance, carcass composition and plasma L-carnitine concentration of broiler chicks reared under different temperature.

  Archiv fur Tierernahrung 20030201

• A third human carnitine/organic cation transporter (OCTN3) as a candidate for the 5q31 Crohn's disease locus (IBD5).

  Biochemical and biophysical research communications 20030131

• Distinct transport activity of tetraethylammonium from L-carnitine in rat renal brush-border membranes.

  Biochimica et biophysica acta 20030131

• Determination of carnitine and acylcarnitines in urine by high-performance liquid chromatography-electrospray ionization ion trap tandem mass spectrometry.

  Journal of chromatography. A 20030117

• Discovery of a long-chain carbamoyl aminocarnitine derivative, a reversible carnitine palmitoyltransferase inhibitor with antiketotic and antidiabetic activity.

  Journal of medicinal chemistry 20030116

• Relative importance of malonyl CoA and carnitine in maturation of fatty acid oxidation in newborn rabbit heart.

  American journal of physiology. Heart and circulatory physiology 20030101

• Carnitine inhibits arachidonic acid turnover, platelet function, and oxidative stress.

  American journal of physiology. Heart and circulatory physiology 20030101

• Validation of an ESI-MS/MS screening method for acylcarnitine profiling in urine specimens of neonates, children, adolescents and adults.

  Clinica chimica acta; international journal of clinical chemistry 20030101

• Changes in distinct species of 1,2-diacylglycerol in cardiac hypertrophy due to energy metabolic disorder.

  Cardiovascular research 20030101

• Impact of mitochondrial beta-oxidation in fatty acid-mediated inhibition of glioma cell proliferation.

  Journal of lipid research 20030101

• Mechanisms of liver steatosis in rats with systemic carnitine deficiency due to treatment with trimethylhydraziniumpropionate.

  Journal of lipid research 20030101

• The pattern of urinary acylcarnitines determined by electrospray mass spectrometry: a new tool in the diagnosis of diabetes mellitus.

  Analytical and bioanalytical chemistry 20030101

• History of L-carnitine: implications for renal disease.

  Journal of renal nutrition : the official journal of the Council on Renal Nutrition of the National Kidney Foundation 20030101

• Nutritional effects of carnitine supplementation in hemodialysis patients.

  Clinical nephrology 20030101

• Plasma carnitine profile during chronic renal anemia treatment with recombinant human erythropoietin.

  The International journal of artificial organs 20030101

• Protection of the retina from ischemia-reperfusion injury by L-carnitine in guinea pigs.

  European journal of ophthalmology 20030101

• Investigation of the mechanisms of therapy-related hypoglycaemia in children with acute lymphoblastic leukaemia.

  Acta paediatrica (Oslo, Norway : 1992) 20030101

• Carnitine level in Chinese epileptic patients taking sodium valproate.

  Pediatric neurology 20030101

• Heart metabolic disturbances in cardiovascular diseases.

  Archives of medical research 20030101

• L-carnitine decreases severity and type of fatigue induced by interferon-alpha in the treatment of patients with hepatitis C.

  Neuropsychobiology 20030101

• Exercise-trained but not untrained rats maintain free carnitine reserves during acute exercise.

  Asia Pacific journal of clinical nutrition 20030101

• Effects of levocarnitine on mitochondrial antioxidant systems and oxidative stress in aged rats.

  Drugs in R&D 20030101

• Bench-to-bedside review: severe lactic acidosis in HIV patients treated with nucleoside analogue reverse transcriptase inhibitors.

  Critical care (London, England) 20030101

• Exercise intolerance during post-MI heart failure in rats: prevention with supplemental dietary propionyl-L-carnitine.

  Cardiovascular drugs and therapy 20030101

• Effect of salt stress on crotonobetaine and D(+)-carnitine biotransformation into L(-)-carnitine by resting cells of Escherichia coli.

  Journal of basic microbiology 20030101

• Evaluation of 3-methylcrotonyl-CoA carboxylase deficiency detected by tandem mass spectrometry newborn screening.

  Journal of inherited metabolic disease 20030101

• Levocarnitine administration in elderly subjects with rapid muscle fatigue: effect on body composition, lipid profile and fatigue.

  Drugs & aging 20030101

• [Anemia in chronic renal failure. The role of L-carnitine in the treatment of anemia of hemodialyzed patients].

  Polskie Archiwum Medycyny Wewnetrznej 20030101

• Magnetic resonance imaging and spectroscopy in a patient with treated methylmalonic acidemia.

  Journal of computer assisted tomography 20030101

• Carnitine transport: pathophysiology and metabolism of known molecular defects.

  Journal of inherited metabolic disease 20030101

• Treatment of carnitine deficiency.

  Journal of inherited metabolic disease 20030101

• L-carnitine in inborn errors of metabolism: what is the evidence?

  Journal of inherited metabolic disease 20030101

• [Concentrations of carnitine and further biochemical parameters in the blood serum of healthy dairy cows and cows with abomasal displacement (dislocatio abomasi) and puerperal disorders].

  Berliner und Munchener tierarztliche Wochenschrift 20030101

• Pharmacokinetics of L-carnitine.

  Clinical pharmacokinetics 20030101

• L-carnitine alleviates alcohol-induced liver damage in rats: role of tumour necrosis factor-alpha.

  Alcohol and alcoholism (Oxford, Oxfordshire) 20030101

• Effect of L-carnitine on carrageenan-induced inflammation in aged rats.

  Gerontology 20030101

• [Antioxidant activity of mildronate and L-carnitine in the treatment of patients with cerebrovascular diseases].

  Eksperimental'naia i klinicheskaia farmakologiia 20030101

• Mitochondrial and peroxisomal fatty acid oxidation capacities increase in the skeletal muscles of young pigs during early postnatal development but are not affected by cold stress.

  Reproduction, nutrition, development 20030101

• Betaine and carnitine uptake systems in Listeria monocytogenes affect growth and survival in foods and during infection.

  Journal of applied microbiology 20030101

• What is the role of medium-chain triglycerides in the management of long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency?

  Journal of inherited metabolic disease 20030101

• A case of mitochondrial trifunctional protein deficiency diagnosed by acylcarnitine profile and DNA analysis in a dried blood spot of a 4-day-old boy.

  Journal of inherited metabolic disease 20030101

• The mitochondrial acetoacetyl-CoA thiolase (T2) deficiency in Japanese patients: urinary organic acid and blood acylcarnitine profiles under stable conditions have subtle abnormalities in T2-deficient patients with some residual T2 activity.

  Journal of inherited metabolic disease 20030101

• L-Carnitine in the treatment of mild or moderate hepatic encephalopathy.

  Digestive diseases (Basel, Switzerland) 20030101

• Effects of propionyl-L-carnitine topical irrigation in distal ulcerative colitis: a preliminary report.

  Hepato-gastroenterology 20030101

• Carnitine profiles during differentiation and effects of carnitine on differentiation of 3T3-L1 cells.

  Journal of medicinal food 20030101

• Silent and symptomatic primary carnitine deficiency within the same family due to identical mutations in the organic cation/carnitine transporter OCTN2.

  Journal of inherited metabolic disease 20030101

• Rapid diagnosis of medium chain Acyl Co-A dehydrogenase (MCAD) deficiency in a newborn by liquid chromatography/tandem mass spectrometry.

  Rapid communications in mass spectrometry : RCM 20030101

• The role of food supplements in the treatment of the infertile man.

  Reproductive biomedicine online 20030101

• Carnitine.

  Journal of toxicology. Clinical toxicology 20030101

• Role of carnitine in valproic acid toxicity.

  Journal of toxicology. Clinical toxicology 20030101

• Respiratory complex II defect in siblings associated with a symptomatic secondary block in fatty acid oxidation.

  Journal of inherited metabolic disease 20030101

• A case of severe hyperlipidemia caused by long-term tube feedings.

  Journal of atherosclerosis and thrombosis 20030101

• Analysis of organic acids after incubation with (16-2H3)palmitic acid in fibroblasts from patients with mitochondrial beta-oxidation defects.

  Journal of inherited metabolic disease 20030101

• Serum free carnitine in medium chain acyl-CoA dehydrogenase deficiency.

  Bratislavske lekarske listy 20030101

• Modeling, optimization and experimental assessment of continuous L-(-)-carnitine production by Escherichia coli cultures.

  Biotechnology and bioengineering 20021230

• Adult onset glutaric aciduria type I presenting with a leukoencephalopathy.

  Neurology 20021210

• [Inherited and acquired disorders of mitochondrial DNA].

  Praxis 20021204

• Pivalate-generating prodrugs and carnitine homeostasis in man.

  Pharmacological reviews 20021201

• L-carnitine ameliorates gentamicin-induced renal injury in rats.

  Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20021201

• Antioxidant treatment with carnitines is effective in infertile patients with prostatovesiculoepididymitis and elevated seminal leukocyte concentrations after treatment with nonsteroidal anti-inflammatory compounds.

  Fertility and sterility 20021201

• Can claudication be improved with medication?

  Seminars in vascular surgery 20021201

• Mitochondrial oxidative metabolism in motor neuron degeneration (mnd) mouse central nervous system.

  The European journal of neuroscience 20021201

• [Biopharmaceutical studies on molecular mechanisms of membrane transport].

  Yakugaku zasshi : Journal of the Pharmaceutical Society of Japan 20021201

• Identification of human CDV-1R and mouse Cdv-1R, two novel proteins with putative signal peptides, especially highly expressed in testis and increased with the male sex maturation.

  Molecular biology reports 20021201

• Effect of L-carnitine supplementation on utilisation of energy and protein in broiler chicken fed different dietary fat levels.

  Archiv fur Tierernahrung 20021201

• Role of carnitine and fatty acid oxidation and its defects in infantile epilepsy.

  Journal of child neurology 20021201

• Hyperammonemia in carnitine-deficient adult JVS mice used by starvation.

  Metabolic brain disease 20021201

• Prevention of ammonia and glutamate neurotoxicity by carnitine: molecular mechanisms.

  Metabolic brain disease 20021201

• Primary systemic carnitine deficiency presenting as recurrent Reye-like syndrome and dilated cardiomyopathy.

  Chang Gung medical journal 20021201

• The role of L-carnitine in treatment of a murine model of asthma.

  Acta medica Okayama 20021201

• A synthetic receptor for choline and carnitine.

  Journal of the American Chemical Society 20021127

• Uremic myopathy.

  Kidney international 20021101

• Fat oxidation defect presenting with overwhelming ketonuria.

  Archives of disease in childhood 20021101

• Animal model of dementia induced by entorhinal synaptic damage and partial restoration of cognitive deficits by BDNF and carnitine.

  Journal of neuroscience research 20021101

• Chemoenzymatic synthesis of phosphocarnitine enantiomers.

  The Journal of organic chemistry 20021101

• Effects of oral L-carnitine supplementation on in vivo long-chain fatty acid oxidation in healthy adults.

  Metabolism: clinical and experimental 20021101

• Comprehensive screening of urine samples for inborn errors of metabolism by electrospray tandem mass spectrometry.

  Clinical chemistry 20021101

• Carnitine membrane transporter deficiency: a long-term follow up and OCTN2 mutation in the first documented case of primary carnitine deficiency.

  Molecular genetics and metabolism 20021101

• Acylcarnitine profiles of preterm infants over the first four weeks of life.

  Pediatric research 20021101

• Plasma free and total carnitine measured in children by tandem mass spectrometry.

  Brazilian journal of medical and biological research = Revista brasileira de pesquisas medicas e biologicas 20021101

• [The concentration of carnitine in the last trimester of pregnancy subject to glucose tolerance].

  Zentralblatt fur Gynakologie 20021101

• CaiT of Escherichia coli, a new transporter catalyzing L-carnitine/gamma -butyrobetaine exchange.

  The Journal of biological chemistry 20021018

• The acetyl group deficit at the onset of contraction in ischaemic canine skeletal muscle.

  The Journal of physiology 20021015

• Novel human cDNAs homologous to Drosophila Orct and mammalian carnitine transporters.

  Biochemical and biophysical research communications 20021011

• A method for quantitative acylcarnitine profiling in human skin fibroblasts using unlabelled palmitic acid: diagnosis of fatty acid oxidation disorders and differentiation between biochemical phenotypes of MCAD deficiency.

  Biochimica et biophysica acta 20021010

• Effects of acetyl-L-carnitine on regional cerebral glucose metabolism in awake rats.

  Brain research 20021004

• Gender and age differences in plasma carnitine, muscle strength, and exercise tolerance in haemodialysis patients.

  Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20021001

• Testicular toxicity effects of magnetic field exposure and prophylactic role of coenzyme Q10 and L-carnitine in mice.

  Pharmacological research 20021001

• Endothelium-dependent vasorelaxation induced by L-carnitine in isolated aorta from normotensive and hypertensive rats.

  The Journal of pharmacy and pharmacology 20021001

• Molecular identification of a novel carnitine transporter specific to human testis. Insights into the mechanism of carnitine recognition.

  The Journal of biological chemistry 20020927

• Novel mRNA molecules are induced in hypertrophied ventricles of carnitine-deficient mice and belong to a family of up-regulated gene in cells overexpressing c-erbB-2.

  Biochimica et biophysica acta 20020927

• A chiral HPLC method for the determination of low amounts of D-carnitine in L-carnitine after derivatization with (+)-FLEC.

  Journal of pharmaceutical and biomedical analysis 20020905

• L-Carnitine inhibits cisplatin-induced injury of the kidney and small intestine.

  Archives of biochemistry and biophysics 20020901

• L-Carnitine: a potential treatment for blocking apoptosis and preventing skeletal muscle myopathy in heart failure.

  American journal of physiology. Cell physiology 20020901

• Studies on functional sites of organic cation/carnitine transporter OCTN2 (SLC22A5) using a Ser467Cys mutant protein.

  The Journal of pharmacology and experimental therapeutics 20020901

• A founder mutation (R254X) of SLC22A5 (OCTN2) in Chinese primary carnitine deficiency patients.

  Human mutation 20020901

• L-carnitine does not exert any in vitro relaxant effect in Guinea pig trachea, lung parenchyma and human bronchial tissue.

  Experimental lung research 20020901

• Effect of increased fat availability on metabolism and exercise capacity.

  Medicine and science in sports and exercise 20020901

• Interactions of acyl carnitines with model membranes: a (13)C-NMR study.

  Journal of lipid research 20020901

• Dilated cardiomyopathy in dystrophic epidermolysis bullosa: a lethal complication of epidermolysis bullosa.

  European journal of anaesthesiology 20020901

• Hypoxia-induced lipid peroxidation in rat brain and protective effect of carnitine and phosphocreatine.

  Neurochemical research 20020901

• Oral L-carnitine combined with training promotes changes in skeletal muscle.

  Equine veterinary journal. Supplement 20020901

• Identification of two novel mutations in OCTN2 from two Saudi patients with systemic carnitine deficiency.

  Journal of inherited metabolic disease 20020901

• Relative importance of enhanced glucose uptake versus attenuation of long-chain acyl carnitines in protecting ischemic myocardium.

  Coronary artery disease 20020901

• Carnitine prevents NMDA receptor-mediated activation of MAP-kinase and phosphorylation of microtubule-associated protein 2 in cerebellar neurons in culture.

  Brain research 20020823

• Novel OCTN2 mutations: no genotype-phenotype correlations: early carnitine therapy prevents cardiomyopathy.

  American journal of medical genetics 20020815

• Multiple Methods for Reduction of Lipoprotein(a).

  Atherosclerosis 20020801

• Application of tandem mass spectrometry to biochemical genetics and newborn screening.

  Clinica chimica acta; international journal of clinical chemistry 20020801

• Protective effects of carnitine in an experimental ischemia-reperfusion injury.

  Clinical nutrition (Edinburgh, Scotland) 20020801

• Unexpectedly high prevalence of the mild form of propionic acidemia in Japan: presence of a common mutation and possible clinical implications.

  Human genetics 20020801

• Quantitative fibroblast acylcarnitine profiles in mitochondrial fatty acid beta-oxidation defects: phenotype/metabolite correlations.

  Molecular genetics and metabolism 20020801

• Very long-chain acyl-CoA dehydrogenase deficiency in an infant presenting with massive hepatomegaly.

  Journal of inherited metabolic disease 20020801

• Mildronate: cardioprotective action through carnitine-lowering effect.

  Trends in cardiovascular medicine 20020801

• [Carnitine deficiency myopathy: a case of late diagnosis].

  Anales de medicina interna (Madrid, Spain : 1984) 20020801

• Mitochondrial fatty acid oxidation disorders in Thai infants: a report of 3 cases.

  Journal of the Medical Association of Thailand = Chotmaihet thangphaet 20020801

• Reproductive performance of sows supplemented with dietary L-carnitine over three reproductive cycles.

  Archiv fur Tierernahrung 20020801

• Organic cation/carnitine transporter, OCTN2, is differentially expressed in the adult rat epididymis.

  Biology of reproduction 20020701

• Age-associated cardiomyopathy in heterozygous carrier mice of a pathological mutation of carnitine transporter gene, OCTN2.

  The journals of gerontology. Series A, Biological sciences and medical sciences 20020701

• Analysis of mitochondrial fatty acid oxidation intermediates by tandem mass spectrometry from intact mitochondria prepared from homogenates of cultured fibroblasts, skeletal muscle cells, and fresh muscle.

  Pediatric research 20020701

• Serum acylcarnitines and vitamin B12 deficiency.

  Clinical chemistry 20020701

• Substrate utilization during graded aerobic exercise in rainbow trout.

  The Journal of experimental biology 20020701

• The influence of l-carnitine supplementation on hematocrit and hemoglobin levels in patients with end stage renal failure on CAPD.

  Renal failure 20020701

• Efficacy of carnitine in the treatment of children with attention-deficit hyperactivity disorder.

  Prostaglandins, leukotrienes, and essential fatty acids 20020701

• Influence of fasting on the effects of ischemic preconditioning in the ischemic-reperfused rat heart.

  Archives of physiology and biochemistry 20020701

• Bicarbonate-induced alkalosis augments cellular acetyl group availability and isometric force during the rest-to-work transition in canine skeletal muscle.

  Experimental physiology 20020701

• Differential long-term subcellular responses in heart and liver to adriamycin stress. Exogenous L-carnitine cardiac and hepatic protection.

  Journal of submicroscopic cytology and pathology 20020701

• Carnitine uptake by AGP2 in yeast Saccharomyces cerevisiae is dependent on Hog1 MAP kinase pathway.

  Molecules and cells 20020630

• Potential role of levocarnitine supplementation for the treatment of chemotherapy-induced fatigue in non-anaemic cancer patients.

  British journal of cancer 20020617

• Osmoprotection by carnitine in a Listeria monocytogenes mutant lacking the OpuC transporter: evidence for a low affinity carnitine uptake system.

  FEMS microbiology letters 20020604

• Oral propionyl-l-carnitine and intraplaque verapamil in the therapy of advanced and resistant Peyronie's disease.

  BJU international 20020601

• Analysis of carnitine biosynthesis metabolites in urine by HPLC-electrospray tandem mass spectrometry.

  Clinical chemistry 20020601

• More on the metabolic autopsy.

  Clinical chemistry 20020601

• Enhancement of muscular performance by a coformulation of propionyl-L-carnitine, coenzyme Q10, nicotinamide, riboflavin and pantothenic acid in the rat.

  Physiology & behavior 20020601

• Assessment of plasma carnitine concentrations in relation to ceroid lipofuscinosis in Tibetan Terriers.

  American journal of veterinary research 20020601

• Comparative effects of dietary corn oil, safflower oil, fish oil and palm oil on metabolism of ethanol and carnitine in the rat.

  Journal of the American College of Nutrition 20020601

• Nutritional supplementation with MyoVive repletes essential cardiac myocyte nutrients and reduces left ventricular size in patients with left ventricular dysfunction.

  American heart journal 20020601

• Carnitine metabolism in diabetes mellitus.

  Journal of pediatric endocrinology & metabolism : JPEM 20020601

• The protective role of L-carnitine against neurotoxicity evoked by drug of abuse, methamphetamine, could be related to mitochondrial dysfunction.

  Annals of the New York Academy of Sciences 20020601

• Serum carnitine levels during the doxorubicin therapy. Its role in cardiotoxicity.

  Journal of experimental & clinical cancer research : CR 20020601

• Effects of L-carnitine and ginkgo biloba extract (EG b 761) in experimental bleomycin-induced lung fibrosis.

  Pharmacological research 20020601

• Friedreich's ataxia associated with mitochondrial myopathy: clinicopathologic report.

  Journal of child neurology 20020601

• L-carnitine reduces lymphocyte apoptosis and oxidant stress in HIV-1-infected subjects treated with zidovudine and didanosine.

  Antioxidants & redox signaling 20020601

• Effects of fasting and hypoxic preconditioning on the hypoxic-reoxygenated ventricular strips of the rat heart.

  Journal of physiology and biochemistry 20020601

• Elevated carnitine accumulation by Listeria monocytogenes impaired in glycine betaine transport is insufficient to restore wild-type cryotolerance in milk whey.

  International journal of food microbiology 20020505

• Protocols for identifying drug-nutrient interactions in patients: the role of the dietitian.

  Journal of the American Dietetic Association 20020501

• L-carnitine administration reverses acute mental status changes in a chronic hemodialysis patient with hepatitis C infection.

  Clinical nephrology 20020501

• Successful pregnancy in a woman with mut- methylmalonic acidaemia.

  Journal of inherited metabolic disease 20020501

• Gas chromatographic-mass spectrometric newborn screening for propionic acidaemia by targeting methylcitrate in dried filter-paper urine samples.

  Journal of inherited metabolic disease 20020501

• Practical management of combined methylmalonicaciduria and homocystinuria.

  Journal of child neurology 20020501

• A heterozygote phenotype is present in the jvs +/- mutant mouse livers.

  Molecular genetics and metabolism 20020501

• Hypocarnitinemia in lysinuric protein intolerance.

  Molecular genetics and metabolism 20020501

• [Vitamin supplements, protein preparations, carnitine and Co. What is the benefit for amateur athletes (interview by Dr. Ulrich Scharmer)].

  MMW Fortschritte der Medizin 20020425

• Carnitine biosynthesis in Neurospora crassa: identification of a cDNA coding for epsilon-N-trimethyllysine hydroxylase and its functional expression in Saccharomyces cerevisiae.

  FEMS microbiology letters 20020423

• L-carnitine accelerates the in vitro regeneration of neural network from adult murine brain cells.

  Brain research 20020405

• Long-term administration of L-carnitine to humans: effect on skeletal muscle carnitine content and physical performance.

  Clinica chimica acta; international journal of clinical chemistry 20020401

• Effect of L-carnitine on brain lipid peroxidation and antioxidant enzymes in old rats.

  The journals of gerontology. Series A, Biological sciences and medical sciences 20020401

• Long- and medium-chain fatty acid oxidation is increased in exercise-trained human skeletal muscle.

  Metabolism: clinical and experimental 20020401

• Role of L-carnitine in apnea of prematurity: a randomized, controlled trial.

  Pediatrics 20020401

• Effect of diet supplementation with l-carnitine on hepatic catabolism of l-alanine in rats.

  Acta pharmacologica Sinica 20020401

• Modulation of apoptosis and improved redox metabolism with the use of a new antioxidant formula.

  Biochemical pharmacology 20020401

• The effect of dietary carnitine on semen traits of white Leghorn roosters.

  Poultry science 20020401

• L-carnitine administration reduces number of episodes in cyclic vomiting syndrome.

  Clinical pediatrics 20020401

• [Drug therapy for mitochondrial diseases].

  Nihon rinsho. Japanese journal of clinical medicine 20020401

• [Primary carnitine deficiency].

  Nihon rinsho. Japanese journal of clinical medicine 20020401

• [Secondary carnitine deficiency].

  Nihon rinsho. Japanese journal of clinical medicine 20020401

• [Carnitine acylcarnitine translocase deficiency].

  Nihon rinsho. Japanese journal of clinical medicine 20020401

• [Mitochondrial carnitine acylcarnitine translocase].

  Nihon rinsho. Japanese journal of clinical medicine 20020401

• [Enzymes of mitochondrial beta-oxidation].

  Nihon rinsho. Japanese journal of clinical medicine 20020401

• [Assay of carnitine in plasma and urine of healthy adults].

  Zhongguo yi xue ke xue yuan xue bao. Acta Academiae Medicinae Sinicae 20020401

• Modeling of the biotransformation of crotonobetaine into L-(-)-carnitine by Escherichia coli strains.

  Biotechnology and bioengineering 20020330

• Dietary supplements in the treatment of nucleoside reverse transcriptase inhibitor-related mitochondrial toxicity.

  AIDS (London, England) 20020329

• Tandem mass spectrometric assay for the determination of carnitine palmitoyltransferase II activity in muscle tissue.

  Analytical biochemistry 20020315

• Complete beta-oxidation of valproate: cleavage of 3-oxovalproyl-CoA by a mitochondrial 3-oxoacyl-CoA thiolase.

  The Biochemical journal 20020315

• The first gas chromatographic resolution of carnitine enantiomers.

  Chemical communications (Cambridge, England) 20020307

• Propionyl-L-carnitine prevents renal function deterioration due to ischemia/reperfusion.

  Kidney international 20020301

• Effects of L-carnitine supplementation in maintenance hemodialysis patients: a systematic review.

  Journal of the American Society of Nephrology : JASN 20020301

• Acylcarnitine profiles in fibroblasts from patients with respiratory chain defects can resemble those from patients with mitochondrial fatty acid beta-oxidation disorders.

  Metabolism: clinical and experimental 20020301

• Thyroid hormone controls carnitine status through modifications of gamma-butyrobetaine hydroxylase activity and gene expression.

  Cellular and molecular life sciences : CMLS 20020301

• Dietary L-carnitine increases plasma insulin-like growth factor-I concentration in chicks fed a diet with adequate dietary protein level.

  British poultry science 20020301

• Serum and seminal markers in the diagnosis of disorders of the genital tract of the dog: a mini-review.

  Theriogenology 20020301

• Effect of L-carnitine treatment for valproate-induced hepatotoxicity.

  Neurology 20020212

• L-Carnitine L-tartrate supplementation favorably affects markers of recovery from exercise stress.

  American journal of physiology. Endocrinology and metabolism 20020201

• Palmitate-induced cardiac apoptosis is mediated through CPT-1 but not influenced by glucose and insulin.

  American journal of physiology. Heart and circulatory physiology 20020201

• Dietary l-carnitine stimulates carnitine acyltransferases in the liver of aged rats.

  The journal of histochemistry and cytochemistry : official journal of the Histochemistry Society 20020201

• Carnitine biosynthesis in mammals.

  The Biochemical journal 20020201

• Serum lipid and fatty acid profiles in adriamycin-treated rats after administration of L-carnitine.

  Pediatric research 20020201

• Parenteral nutrition-associated liver complications in children.

  Pharmacotherapy 20020201

• The effects of L-carnitine on spinal cord ischemia/reperfusion injury in rabbits.

  The Thoracic and cardiovascular surgeon 20020201

• Effect of hemodialysis on carnitine levels in children with chronic renal failure.

  Pediatrics international : official journal of the Japan Pediatric Society 20020201

• Free carnitine levels in children with steroid-sensitive nephrotic syndrome.

  Pediatrics international : official journal of the Japan Pediatric Society 20020201

• Screening for carnitine palmitoyltransferase II deficiency by tandem mass spectrometry.

  Journal of inherited metabolic disease 20020201

• L-Carnitine transport in mouse renal and intestinal brush-border and basolateral membrane vesicles.

  Biochimica et biophysica acta 20020102

• Propionyl-L-carnitine reduces intimal hyperplasia after injury in normocholesterolemic rabbit carotid artery by modulating proliferation and caspase 3-dependent apoptosis of vascular smooth muscle cells.

  Atherosclerosis 20020101

• Serum carnitine levels of pediatric cancer patients.

  Pediatric hematology and oncology 20020101

• Dilated cardiomyopathy in juvenile Portuguese Water Dogs.

  Journal of veterinary internal medicine 20020101

• Nutrition. L-carnitine for the treatment of hypertriglyceridemia in HIV.

  HIV clinician 20020101

• Safety of oral carnitine in dialysis patients.

  Seminars in dialysis 20020101

• Functional characterization of intestinal L-carnitine transport.

  The Journal of membrane biology 20020101

• Myocardial and hepatic free carnitine concentrations in pups of diabetic female rats.

  Annals of nutrition & metabolism 20020101

• L-carnitine in experimental retinal ischemia-reperfusion injury.

  Ophthalmologica. Journal international d'ophtalmologie. International journal of ophthalmology. Zeitschrift fur Augenheilkunde 20020101

• Carnitine action on red blood cell osmotic resistance in hemodialysis patients.

  Journal of nephrology 20020101

• Metabolic effects in neonates receiving intravenous medium-chain triglycerides.

  Acta paediatrica (Oslo, Norway : 1992) 20020101

• In vivo proton magnetic resonance spectroscopy (MRS) study of post polio residual paralysis (PPRP) patients.

  Magnetic resonance imaging 20020101

• Protective effect of dietary supplementation with L-arginine and L-carnitine on hypoxia/reoxygenation-induced necrotizing enterocolitis in young mice.

  Biology of the neonate 20020101

• [Determination of carnitine levels in plasma: importance in the study of patients with neuromuscular diseases].

  Acta medica portuguesa 20020101

• Adjunctive therapy in anaemia management.

  Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20020101

• Beneficial effects of L-carnitine in dialysis patients with impaired left ventricular function: an observational study.

  Current medical research and opinion 20020101

• Carnitine as adjuvant therapy in the management of renal anemia.

  Contributions to nephrology 20020101

• [Immune and metabolic effects of carnitine and biotin in hemolytic anemia].

  Eksperimental'naia i klinicheskaia farmakologiia 20020101

• [Immunomodulating effects of carbohydrate and lipid metabolism activators in acute cold stress].

  Eksperimental'naia i klinicheskaia farmakologiia 20020101

• Effect of L-carnitine on weight loss and body composition of rats fed a hypocaloric diet.

  Annals of nutrition & metabolism 20020101

• [Circadian rhythm of serum levo-carnitine: parameters].

  La Clinica terapeutica 20020101

• Pharmacotherapy for peripheral arterial disease: emerging therapeutic options.

  Angiology 20020101

• [Ischemic remodeling of the left ventricle (definition, pathogenesis, diagnosis, medical and surgical correction)].

  Kardiologiia 20020101

• Neonatal presentation of ventricular tachycardia and a Reye-like syndrome episode associated with disturbed mitochondrial energy metabolism.

  BMC pediatrics 20020101

• Defects of beta-oxidation including carnitine deficiency.

  International review of neurobiology 20020101

• The role of L-carnitine on a restricted number of myeloid leukemia progenitor cells: generation of atypical cell types.

  Haematologia 20020101

• Primary carnitine deficiency in a male adult.

  Journal of medicine 20020101

• Liver L-carnitine biosynthesis in non-pregnant, pregnant and lactating rabbits.

  Research communications in molecular pathology and pharmacology 20020101

• Neuroprotective role of L-carnitine in the 3-nitropropionic acid induced neurotoxicity.

  Toxicology letters 20011215

• Relevance of fatty acid oxidation in regulation of the outer mitochondrial membrane permeability for ADP.

  FEBS letters 20011207

• Specificity of the interactions between Glu-3, Ser-24, and Gln-30 within the N-terminal segment of rat liver mitochondrial overt carnitine palmitoyltransferase (L-CPT I) in determining the malonyl-CoA sensitivity of the enzyme.

  Biochemistry 20011204

• Age and sex dependency of carnitine concentration in human serum and skeletal muscle.

  Clinical chemistry 20011201

• Association between seminal plasma carnitine and sperm mitochondrial enzymatic activities.

  International journal of andrology 20011201

• Medium-term open label trial of L-carnitine in Rett syndrome.

  Brain & development 20011201

• Functional relevance of carnitine transporter OCTN2 to brain distribution of L-carnitine and acetyl-L-carnitine across the blood-brain barrier.

  Journal of neurochemistry 20011201

• Low serum carnitine concentrations in healthy children with iron deficiency anemia.

  Pediatric hematology and oncology 20011201

• Dietary L-carnitine suppresses mitochondrial branched-chain keto acid dehydrogenase activity and enhances protein accretion and carcass characteristics of swine.

  Journal of animal science 20011201

• Effects of carnitine coingested caffeine on carnitine metabolism and endurance capacity in athletes.

  Journal of nutritional science and vitaminology 20011201

• [Levels of carnitine and homocysteine in plasma of long-term hemodialysis patients with chronic renal failure].

  Polskie Archiwum Medycyny Wewnetrznej 20011201

• Hyposmotically-activated efflux of L-carnitine from a human mammary cancer cell line.

  Bioscience reports 20011201

• Plasma carnitine in HIV-associated neuropathy.

  AIDS (London, England) 20011109

• Carnitine as a free radical scavenger in aging.

  Experimental gerontology 20011101

• Rapid diagnosis of methylmalonic and propionic acidemias: quantitative tandem mass spectrometric analysis of propionylcarnitine in filter-paper blood specimens obtained from newborns.

  Clinical chemistry 20011101

• Effects of treatment with carnitines in infertile patients with prostato-vesiculo-epididymitis.

  Human reproduction (Oxford, England) 20011101

• Safety measures of L-carnitine L-tartrate supplementation in healthy men.

  Journal of strength and conditioning research 20011101

• Determination of plasma free carnitine by electrospray tandem mass spectrometry.

  Annals of clinical biochemistry 20011101

• Changes in fatty acid concentrations in tissues of African catfish, Clarias gariepinus Burchell, as a consequence of dietary carnitine, fat and lysine supplementation.

  The British journal of nutrition 20011101

• Role of intrapartum hypoxia in carnitine nutritional status during the early neonatal period.

  Early human development 20011101

• Cognitive behavioral therapy and fasting therapy for a patient with chronic fatigue syndrome.

  Internal medicine (Tokyo, Japan) 20011101

• Characterization of altered myocardial fatty acid metabolism in patients with inherited cardiomyopathy.

  Journal of inherited metabolic disease 20011101

• Pharmacotherapy of intermittent claudication.

  Expert opinion on pharmacotherapy 20011101

• Characterization of plasma acylcarnitines in patients under valproate monotherapy using ESI-MS/MS.

  Clinical biochemistry 20011101

• Carnitine levels and the ketogenic diet.

  Epilepsia 20011101

• Studies on the transport of acetyl groups from peroxisomes to mitochondria in isolated liver cells oxidizing the polyunsaturated fatty acid 22:4n-6.

  Biochimica et biophysica acta 20011031

• Roles of long chain fatty acids and carnitine in mitochondrial membrane permeability transition.

  Biochemical pharmacology 20011015

• Suppression of T(3)- and fatty acid-induced membrane permeability transition by L-carnitine.

  Comparative biochemistry and physiology. Part B, Biochemistry & molecular biology 20011001

• Hepatic carnitine palmitoyltransferase I deficiency: acylcarnitine profiles in blood spots are highly specific.

  Clinical chemistry 20011001

• Carnitine metabolism in uremia.

  American journal of kidney diseases : the official journal of the National Kidney Foundation 20011001

• The effects of increasing exercise intensity on muscle fuel utilisation in humans.

  The Journal of physiology 20011001

• Oxidation of unsaturated fatty acids by human fibroblasts with very-long-chain acyl-CoA dehydrogenase deficiency: aspects of substrate specificity and correlation with clinical phenotype.

  Clinica chimica acta; international journal of clinical chemistry 20011001

• Effects of dietary fat and L-carnitine on plasma and whole blood taurine concentrations and cardiac function in healthy dogs fed protein-restricted diets.

  American journal of veterinary research 20011001

• Effects of ischaemic stress on leukocyte activation processes in patients with chronic peripheral occlusive arterial disease: role of L-propionyl carnitine administration.

  Pharmacological research 20011001

• Pharmacologic options available to treat symptomatic intradialytic hypotension.

  American journal of kidney diseases : the official journal of the National Kidney Foundation 20011001

• Short-term carnitine deficiency does not alter aerobic rat heart function but depresses reperfusion recovery after ischemia.

  Canadian journal of physiology and pharmacology 20011001

• [Glutaric aciduria type I: an organic acidemia without acidosis with severe movement disorders].

  Neurologia (Barcelona, Spain) 20011001

• [Glutaric aciduria type I: diagnosis in adulthood and phenotypic variability].

  Neurologia (Barcelona, Spain) 20011001

• Prenatal diagnosis of multiple acyl-CoA dehydrogenase deficiency: association with elevated alpha-fetoprotein and cystic renal changes.

  Prenatal diagnosis 20011001

• Congenital nemaline myopathy due to ACTA1-gene mutation and carnitine insufficiency: a case report.

  Neuropediatrics 20011001

• Insulin-like effects of a physiologic concentration of carnitine on cardiac metabolism.

  Molecular and cellular biochemistry 20011001

• L-Carnitine changes the levels of insulin-like growth factors (IGFs) and IGF binding proteins in streptozotocin-induced diabetic rat.

  Journal of nutritional science and vitaminology 20011001

• Neonatal screening for medium-chain acyl-CoA dehydrogenase deficiency.

  Lancet (London, England) 20010929

• HIV protease inhibitor substitution in patients with lipodystrophy: a randomized, controlled, open-label, multicentre study.

  AIDS (London, England) 20010928

• Evaluation and application of liquid chromatographic columns coated with 'intelligent' ligands: (I) acylcarnitine column.

  Journal of chromatography. A 20010921

• Involvement of coenzyme A esters and two new enzymes, an enoyl-CoA hydratase and a CoA-transferase, in the hydration of crotonobetaine to L-carnitine by Escherichia coli.

  Biochemistry 20010918

• The effect of carnitine on random-pattern flap survival in rats.

  Plastic and reconstructive surgery 20010915

• Gestational, pathologic and biochemical differences between very long-chain acyl-CoA dehydrogenase deficiency and long-chain acyl-CoA dehydrogenase deficiency in the mouse.

  Human molecular genetics 20010915

• Molecular and Biochemical Characterization of Rat epsilon -N-Trimethyllysine Hydroxylase, the First Enzyme of Carnitine Biosynthesis.

  The Journal of biological chemistry 20010907

• Evaluation of newborn screening for medium chain acyl-CoA dehydrogenase deficiency in 275 000 babies.

  Archives of disease in childhood. Fetal and neonatal edition 20010901

• Effect of propionyl-L-carnitine on exercise performance in peripheral arterial disease.

  Medicine and science in sports and exercise 20010901

• L-carnitine prevents the progression of atherosclerotic lesions in hypercholesterolaemic rabbits.

  Pharmacological research 20010901

• L-carnitine modifies the humoral immune response in mice after in vitro or in vivo treatment.

  International immunopharmacology 20010901

• Carnitine-deficient myopathy as a presentation of tyrosinemia type I.

  Journal of child neurology 20010901

• Antioxidant changes in the hypertrophied heart due to energy metabolic disorder.

  Basic research in cardiology 20010901

• Epididymal markers in rats exposed to the xenoestrogen p-nonylphenol: no biochemical effects at low dosages.

  Andrologia 20010901

• The effect of pivalate treatment of pregnant rats on body mass and insulin levels in the adult offspring.

  Life sciences 20010831

• L-carnitine prevents increase in diastolic [CA2+] induced by doxorubicin in cardiac cells.

  European journal of pharmacology 20010810

• Independent organic cation transport activity of Na(+)-L-carnitine cotransport system in LLC-PK(1) cells.

  American journal of physiology. Renal physiology 20010801

• Protection of ischemic hearts perfused with an anion exchange inhibitor, DIDS, is associated with beneficial changes in substrate metabolism.

  Cardiovascular research 20010801

• Plasma and liver carnitine status of children with chronic liver disease and cirrhosis.

  Pediatrics international : official journal of the Japan Pediatric Society 20010801

• Hyperinsulinism in short-chain L-3-hydroxyacyl-CoA dehydrogenase deficiency reveals the importance of beta-oxidation in insulin secretion.

  The Journal of clinical investigation 20010801

• Usefulness of L-carnitine, a naturally occurring peripheral antagonist of thyroid hormone action, in iatrogenic hyperthyroidism: a randomized, double-blind, placebo-controlled clinical trial.

  The Journal of clinical endocrinology and metabolism 20010801

• Carnitine transport by organic cation transporters and systemic carnitine deficiency.

  Molecular genetics and metabolism 20010801

• Valproate induces in vitro accumulation of long-chain fatty acylcarnitines.

  Molecular genetics and metabolism 20010801

• Carnitine for high triglycerides.

  TreatmentUpdate 20010801

• Reversible carnitine palmitoyltransferase inhibitors with broad chemical diversity as potential antidiabetic agents.

  Journal of medicinal chemistry 20010719

• Effects of propionyl-L-carnitine on isolated mitochondrial function in the reperfused diabetic rat heart.

  Diabetes research and clinical practice 20010701

• Influence of L-carnitine and its derivatives on myocardial metabolism and function in ischemic heart disease and during cardiopulmonary bypass.

  Cardiovascular research 20010701

• Multiple acyl-CoA-dehydrogenase deficiency (MADD): use of acylcarnitines and fatty acids to monitor the response to dietary treatment.

  Pediatric research 20010701

• Neuroprotective effect of regional carnitine on spinal cord ischemia--reperfusion injury.

  European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic Surgery 20010701

• Effect of L-carnitine supplementation in hemodialysis patients.

  Nephron 20010701

• Carnitine protects the molecular chaperone activity of lens alpha-crystallin and decreases the post-translational protein modifications induced by oxidative stress.

  FASEB journal : official publication of the Federation of American Societies for Experimental Biology 20010701

• Biochemical properties of porcine white adipose tissue mitochondria and relevance to fatty acid oxidation.

  Comparative biochemistry and physiology. Part B, Biochemistry & molecular biology 20010701

• Effects of propyonil-l-carnitine topical irrigation in distal ulcerative colitis: a preliminary report.

  The American journal of gastroenterology 20010701

• A rapid and quantitative mass spectrometry method for determining the concentration of acylcarnitines and aminoacids in amniotic fluid.

  Prenatal diagnosis 20010701

• Serum L-carnitine levels and lipoprotein compositions in chronic viral hepatitis patients.

  Clinical biochemistry 20010701

• Acute regulation of fatty acid oxidation and amp-activated protein kinase in human umbilical vein endothelial cells.

  Circulation research 20010622

• L-Carnitine for the treatment of highly active antiretroviral therapy-related hypertriglyceridemia in HIV-infected adults.

  AIDS (London, England) 20010615

• Distinct kinetics of carnitine palmitoyltransferase i in contact sites and outer membranes of rat liver mitochondria.

  The Journal of biological chemistry 20010608

• Na(+)-coupled transport of L-carnitine via high-affinity carnitine transporter OCTN2 and its subcellular localization in kidney.

  Biochimica et biophysica acta 20010606

• Medium-chain acyl-CoA dehydrogenase (MCAD) mutations identified by MS/MS-based prospective screening of newborns differ from those observed in patients with clinical symptoms: identification and characterization of a new, prevalent mutation that results in mild MCAD deficiency.

  American journal of human genetics 20010601

• Propionyl-L-carnitine improves exercise performance and functional status in patients with claudication.

  The American journal of medicine 20010601

• Metabolic and structural abnormalities in dogs with early left ventricular dysfunction induced by incessant tachycardia.

  American journal of veterinary research 20010601

• Effects of L-carnitine-hydrochloride in the cold ischemic preservation of fatty liver grafts.

  Transplantation proceedings 20010601

• Propionyl-L-carnitine as protector against adriamycin-induced cardiomyopathy.

  Pharmacological research 20010601

• Effect of dietary L-carnitine on growth performance and body composition in nursery and growing-finishing pigs.

  Journal of animal science 20010601

• Effect of L-carnitine pretreatment on 3-nitropropionic acid-induced inhibition of rat brain succinate dehydrogenase activity.

  Annals of the New York Academy of Sciences 20010601

• Carnitine as a preventive agent in experimental renal ischemia-reperfusion injury.

  Urological research 20010601

• Compound heterozygosity in four asymptomatic siblings with medium-chain acyl-CoA dehydrogenase deficiency.

  Journal of inherited metabolic disease 20010601

• Carnitine-responsive carnitine insufficiency in a case of mtDNA 8993T>C mutation associated Leigh syndrome.

  Journal of inherited metabolic disease 20010601

• Effect of L-carnitine treatment for valproate-induced hepatotoxicity.

  Neurology 20010522

• Metabolic, idiosyncratic toxicity of drugs: overview of the hepatic toxicity induced by the anxiolytic, panadiplon.

  Chemico-biological interactions 20010516

• Intravenous L-carnitine increases plasma carnitine, reduces fatigue, and may preserve exercise capacity in hemodialysis patients.

  American journal of kidney diseases : the official journal of the National Kidney Foundation 20010501

• Carnitine-dependent metabolic activities in Saccharomyces cerevisiae: three carnitine acetyltransferases are essential in a carnitine-dependent strain.

  Yeast (Chichester, England) 20010501

• A polymeric microfluidic chip for CE/MS determination of small molecules.

  Analytical chemistry 20010501

• Peroxisomal fatty acid alpha- and beta-oxidation in humans: enzymology, peroxisomal metabolite transporters and peroxisomal diseases.

  Biochemical Society transactions 20010501

• Impact of the intramitochondrial enzyme organization on fatty acid oxidation.

  Biochemical Society transactions 20010501

• Biotransformation of crotonobetaine to L(-)-carnitine in Proteus sp.

  Archives of microbiology 20010501

• Molecular and functional characterisation of mild MCAD deficiency.

  Human genetics 20010501

• The effects of dietary L-carnitine supplementation on the performance, organ weights and circulating hormone and metabolite concentrations of broiler chickens reared under a normal or low temperature schedule.

  British poultry science 20010501

• Simultaneous side effects of both clozapine and valproate.

  Intensive care medicine 20010501

• Brief intense exercise followed by passive recovery modifies the pattern of fuel use in humans during subsequent sustained intermittent exercise.

  Acta physiologica Scandinavica 20010501

• Plasma carnitine levels of pregnant adolescents in labor.

  Journal of pediatric and adolescent gynecology 20010501

• Conversion of gamma-butyrobetaine to L-carnitine by Achromobacter cycloclast.

  Journal of industrial microbiology & biotechnology 20010501

• Adult-onset combined methylmalonic aciduria and homocystinuria (cblC).

  Neurology 20010424

• Absorbing competition for carnitine.

  The Journal of physiology 20010415

• Na+- and Cl--coupled active transport of carnitine by the amino acid transporter ATB(0,+) from mouse colon expressed in HRPE cells and Xenopus oocytes.

  The Journal of physiology 20010415

• Errors caused by the use of D,L-octanoylcarnitine for blood-spot calibrators.

  Clinical chemistry 20010401

• Transport of L-carnitine in isolated cerebral cortex neurons.

  European journal of biochemistry 20010401

• Carnitine transporter defect diagnosed by newborn screening with electrospray tandem mass spectrometry.

  The Journal of pediatrics 20010401

• The role of L-carnitine and glycine betaine in the survival and sub-lethal injury of non-growing Listeria monocytogenes cells during chilled storage.

  Letters in applied microbiology 20010401

• Comparison of histopathologic effects of carnitine and ascorbic acid on reperfusion injury.

  European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic Surgery 20010401

• Chip-based quantitative capillary electrophoresis/mass spectrometry determination of drugs in human plasma.

  Analytical chemistry 20010401

• Effect of carnitine on stress-induced lipid peroxidation in rat gastric mucosa.

  Journal of gastroenterology 20010401

• Effect of gamma-butyrobetaine on fatty liver in juvenile visceral steatosis mice.

  The Journal of pharmacy and pharmacology 20010401

• New treatment options in intermittent claudication: the US experience.

  International journal of clinical practice. Supplement 20010401

• Up-regulation of carnitine transporters helps maintain tissue carnitine levels in carnitine deficiency induced by pivalic acid.

  Pharmaceutical research 20010401

• Effect of L-carnitine supplementation on performance parameters in gilts and sows.

  Journal of animal physiology and animal nutrition 20010401

• Comparative effects of diet supplementation with l-carnitine and dl-carnitine on ammonia toxicity and hepatic metabolism in rats.

  Acta pharmacologica Sinica 20010401

• Molecular enzymology of carnitine transfer and transport.

  Biochimica et biophysica acta 20010309

• Different sensitivity of rabbit heart and skeletal muscle to endotoxin-induced impairment of mitochondrial function.

  European journal of biochemistry 20010301

• Development and characterization of an animal model of carnitine deficiency.

  European journal of biochemistry 20010301

• Protective efficacy of L-carnitine on acetylcholinesterase activity in aged rat brain.

  The journals of gerontology. Series A, Biological sciences and medical sciences 20010301

• Epigenetic regulation of carnitine metabolising enzymes in Proteus sp. under aerobic conditions.

  FEMS microbiology letters 20010301

• Erythropoietin-resistant refractory renal anemia: effects of oral L-carnitine supplementation.

  Clinical nephrology 20010301

• The effect of supplementary dietary L-carnitine on the growth performance, serum components, carcase traits and enzyme activities in relation to fatty acid beta-oxidation of broiler chickens.

  British poultry science 20010301

• Seminal plasma and IVF potential. Biochemical constituents of seminal plasma of males from in vitro fertilization couples.

  Journal of assisted reproduction and genetics 20010301

• [Antioxidant therapeutic efficiency after the use of carnitine in infertile patients with bacterial or non bacterial prostato-vesiculo-epididymitis].

  Archivio italiano di urologia, andrologia : organo ufficiale [di] Societa italiana di ecografia urologica e nefrologica 20010301

• Impaired fatty acid oxidation in propofol infusion syndrome.

  Lancet (London, England) 20010224

• Pig liver carnitine palmitoyltransferase I, with low Km for carnitine and high sensitivity to malonyl-CoA inhibition, is a natural chimera of rat liver and muscle enzymes.

  Biochemistry 20010220

• Involvement of 1,2-diacylglycerol in improvement of heart function by etomoxir in diabetic rats.

  Life sciences 20010216

• Are plasma concentrations of leptin and carnitine interrelated in haemodialysis patients?

  Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20010201

• Molecular and physiological evidence for multifunctionality of carnitine/organic cation transporter OCTN2.

  Molecular pharmacology 20010201

• Free carnitine concentrations in cord blood in preterm and full-term infants with intrauterine growth retardation.

  Pediatrics international : official journal of the Japan Pediatric Society 20010201

• Chip-based capillary electrophoresis/mass spectrometry determination of carnitines in human urine.

  Analytical chemistry 20010201

• Carnitine palmitoyltransferase I deficiency in neonate identified by dried blood spot free carnitine and acylcarnitine profile.

  Journal of inherited metabolic disease 20010201

• [Treatment of chronic arterial occlusive disease of the lower limbs with propionyl-1-carnitine in elderly patients].

  Minerva medica 20010201

• Effects of L-carnitine supplementation on renal anemia in poor responders to erythropoietin.

  Blood purification 20010101

• Postnatal changes in neonatal acylcarnitine profile.

  Pediatric research 20010101

• Effects of L-carnitine on nitrogen retention and blood metabolites of growing steers and performance of finishing steers.

  Journal of animal science 20010101

• Malnutrition in long-term haemodialysis survivors.

  Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20010101

• Effects of carnitine on cardiac function after cardioplegic ischemia in neonatal rabbit hearts.

  The Annals of thoracic surgery 20010101

• L-carnitine reduces malondialdehyde concentrations in isolated rat hearts in dependence on perfusion conditions.

  Molecular and cellular biochemistry 20010101

• Carnitine protects mitochondria and removes toxic acyls from xenobiotics.

  Drugs under experimental and clinical research 20010101

• Serum free carnitine and total triglycerid levels in children with iron deficiency anemia.

  International journal for vitamin and nutrition research. Internationale Zeitschrift fur Vitamin- und Ernahrungsforschung. Journal international de vitaminologie et de nutrition 20010101

• Evaluation of urinary carnitine and taurine excretion in 5 cystinuric dogs with carnitine and taurine deficiency.

  Journal of veterinary internal medicine 20010101

• Alternative strategies other than growth hormone for the treatment of immune diseases.

  Trends in immunology 20010101

• Oleate oxidation and mitochondrial substrate selection in vascular smooth muscle.

  Journal of vascular research 20010101

• L-carnitine in dialysis patients.

  Seminars in dialysis 20010101

• Electrospray tandem mass spectrometry for analysis of acylcarnitines in dried postmortem blood specimens collected at autopsy from infants with unexplained cause of death.

  Clinical chemistry 20010101

• Necessity of carnitine supplementation in semistarved rats fed a high-fat diet.

  Nutrition (Burbank, Los Angeles County, Calif.) 20010101

• Birth outcome and risk of neonatal hypoglycaemia following in utero exposure to pivmecillinam: a population-based cohort study with 414 exposed pregnancies.

  Scandinavian journal of infectious diseases 20010101

• [Carnitine transport defect].

  Ryoikibetsu shokogun shirizu 20010101

• Protective effect of L-carnitine on gastric mucosal barrier in rats exposed to cold-restraint stress.

  Indian journal of gastroenterology : official journal of the Indian Society of Gastroenterology 20010101

• Carnitine pretreatment can partially change the excitability of the immature nervous tissue.

  Physiological research 20010101

• Oral theophylline changes renal carnitine palmitoyltransferase activity in rats.

  Archives of medical research 20010101

• Emotional distress induced rhabdomyolysis in an individual with carnitine palmitoly-transferase deficiency.

  Clinical and experimental rheumatology 20010101

• [Variants of inborn errors of metabolism with late onset but nevertheless life threatening course].

  Klinische Padiatrie 20010101

• Assessment of dietary therapies in a canine model of Batten disease.

  European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology Society 20010101

• [Familial carnitine deficiency].

  Ryoikibetsu shokogun shirizu 20010101

• [Secondary carnitine deficiency].

  Ryoikibetsu shokogun shirizu 20010101

• Not so mighty mitochondria.

  Nutrition for healthy living 20010101

• Phenotype and genotype variation in primary carnitine deficiency.

  Genetics in medicine : official journal of the American College of Medical Genetics 20010101

• L-Carnitine in the treatment of HIV-associated lipodystrophy syndrome.

  HIV medicine 20010101

• Plasma carnitine levels in children with Down syndrome.

  American journal of human biology : the official journal of the Human Biology Council 20010101

• Alteration of body composition in rats: effect of organic chromium and L-carnitine.

  Acta veterinaria Hungarica 20010101

• Role of metabolically active drugs in the management of ischemic heart disease.

  American journal of cardiovascular drugs : drugs, devices, and other interventions 20010101

• Effects of dietary fat and carnitine on urine carnitine excretion in healthy dogs.

  Veterinary therapeutics : research in applied veterinary medicine 20010101

• Long-chain hydroxydicarboxylic aciduria, carnitine depletion and acetaminophen exposure.

  Journal of inherited metabolic disease 20000301

• beta-lactam antibiotics as substrates for OCTN2, an organic cation/carnitine transporter.

  The Journal of biological chemistry 20000121

• L-carnitine supplementation in patients with cystic acne on isotretinoin therapy.

  Journal of the European Academy of Dermatology and Venereology : JEADV 19991101

• [A case report of valproate encephalopathy].

  Rinsho shinkeigaku = Clinical neurology 19991001

• Reversal of doxorubicin-induced cardiac metabolic damage by L-carnitine.

  Pharmacological research 19990401

• L-carnitine esters as 'soft', broad-spectrum antimicrobial amphiphiles.

  Journal of medicinal chemistry 19980618

• Valproate-associated carnitine deficiency and malignant cerebral edema in the absence of hepatic failure.

  International journal of clinical pharmacology and therapeutics 19970901

• On the interrelationship between hepatic carnitine, fatty acid oxidation, and triglyceride biosynthesis in nephrosis.

  Lipids 19970801

• Effect of L-carnitine supplementation on acute valproate intoxication.

  Epilepsia 19960701

• Cardiac glucose and fatty acid oxidation in the streptozotocin-induced diabetic spontaneously hypertensive rat.

  Hypertension (Dallas, Tex. : 1979) 19950201

• Muscle carnitine deficiency associated with zidovudine-induced mitochondrial myopathy.

  Annals of neurology 19941001

• Valproate encephalopathy and hypocarnitinaemia in diabetic patients.

  Journal of neurology 19940801

• Effect of L-carnitine on the zidovudine-induced destruction of human myotubes. Part I: L-carnitine prevents the myotoxicity of AZT in vitro.

  Laboratory investigation; a journal of technical methods and pathology 19940701

• Cardiovascular and metabolic changes in spontaneously hypertensive rats following streptozotocin administration.

  The Canadian journal of cardiology 19940601

• Zidovudine-induced mitochondrial myopathy is associated with muscle carnitine deficiency and lipid storage.

  Annals of neurology 19940401

• Severe hepatotoxicity during valproate therapy: an update and report of eight new fatalities.

  Epilepsia 19940101

• Modulation of ethanol-mediated CYP2E1 induction by clofibrate and L-carnitine in rat liver.

  Biological & pharmaceutical bulletin 19931201

• Carnitine deficiency associated with long-term pivampicillin treatment: the effect of a replacement therapy regime.

  Postgraduate medical journal 19921101

• Valproate-induced coma with ketosis and carnitine insufficiency.

  Archives of neurology 19901001

• Oxfenicine-induced accumulation of lipid in the rat myocardium.

  Journal of molecular and cellular cardiology 19880301

• [Effect of DL-carnitine and gamma-butyrobetaine hydroxylase inhibitor 3-(2,2,2-trimethylhydrazinium) propionate on isoproterenol-induced changes in the metabolism of the rat myocardium].

  Voprosy meditsinskoi khimii 19880101

• Echocardiographic assessment of anthracycline cardiotoxicity during different therapeutic regimens.

  International journal of clinical pharmacology research 19870101

• Carnitine protection against adriamycin-induced cardiomyopathy in rats.

  Life sciences 19860210

• Effect of administration of carnitine on the severity of myocardial infarction induced by isoproterenol in rats.

  The Australian journal of experimental biology and medical science 19860201

• The biochemical functions of ascorbic acid.

  Annual review of nutrition 19860101

• Valproic acid associated abnormalities of carnitine metabolism.

  Lancet (London, England) 19850406

• Reduction of cardiac toxicity of anthracyclines by L-carnitine: preliminary overview of clinical data.

  International journal of clinical pharmacology research 19850101

• Decreased serum carnitine in valproate induced Reye syndrome.

  European journal of pediatrics 19821101

• Antagonism of doxorubicin cardiotoxicity by carnitine is specific of the L-diasteroisomer.

  Biomedicine / [publiee pour l'A.A.I.C.I.G.] 19810501

• Effect of clofibrate treatment on acylcarnitine oxidation in isolated rat liver mitochondria.

  Medical biology 19790201

• Myopathy with paroxysmal myoglobinuria and focal muscle necrosis following enfluorane anaesthesia.

  Journal of the neurological sciences 19781101

• Inducible gamma-butyrobetaine-degrading enzymes in Pseudomonas species AK 1.

  Journal of bacteriology 19700301

• Nephroprotective potential of carnitine against glycerol and contrast-induced kidney injury in rats through modulation of oxidative stress, proinflammatory cytokines, and apoptosis.

  The British journal of radiology